Ocular involvement in hemolytic uremic syndrome due to factor H deficiency - Are there therapeutic consequences?

Pediatric Nephrology

Volumn 22, Issue 11, 2007, Pages 1967-1970

  Larakeb, Anis ^a   Leroy, Sandrine ^a   Frémeaux Bacchi, Véronique ^b   Montchilova, Marta ^a   Pelosse, Béatrice ^a   Dunand, Olivier ^a   Deschênes, Georges ^c   Bensman, Albert ^a   Ulinski, Tim ^a  

^a ARMAND TROUSSEAU HOSPITAL   (France)

^b HÔPITAL EUROPÉEN GEORGES POMPIDOU   (France)

^c HÔPITAL ROBERT DEBRÉ   (France)

Author keywords

Complement system; Factor H; Fresh frozen plasma; Glaucoma; Hemolytic uremic syndrome; Ocular involvement; Plasma exchange; Thrombotic microangiopathy

Indexed keywords

ANTIHYPERTENSIVE AGENT; C REACTIVE PROTEIN; COMPLEMENT COMPONENT C3; COMPLEMENT FACTOR H; FRESH FROZEN PLASMA; HAPTOGLOBIN;

ARTICLE; BIOMICROSCOPY; BLURRED VISION; CASE REPORT; CHOROID HEMORRHAGE; CLINICAL FEATURE; COMPLEMENT BLOOD LEVEL; COMPLEMENT DEFICIENCY; COMPLEMENT FACTOR H DEFICIENCY; EYE DISEASE; EYE PAIN; FLUORESCENCE ANGIOGRAPHY; HEMODIALYSIS; HEMOLYTIC UREMIC SYNDROME; HUMAN; HYPERTENSION; INFANT; INTRAOCULAR HYPERTENSION; KIDNEY FAILURE; MALE; NEPHRECTOMY; OPHTHALMOSCOPY; PLASMAPHERESIS; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; RETINA ISCHEMIA; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; VITREOUS HEMORRHAGE;

CHOROID HEMORRHAGE; COMPLEMENT FACTOR H; COMPLEMENT PATHWAY, ALTERNATIVE; GLAUCOMA; HEMOLYTIC-UREMIC SYNDROME; HOMOZYGOTE; HUMANS; INFANT; MALE; THROMBOSIS;

EID: 34848903255     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-007-0540-0     Document Type: Article

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