-
1
-
-
32944456736
-
Current concepts in thrombotic thrombocytopenic purpura
-
Tsai HM. Current concepts in thrombotic thrombocytopenic purpura. Annu Rev Med 2006; 57: 419-436.
-
(2006)
Annu Rev Med
, vol.57
, pp. 419-436
-
-
Tsai, H.M.1
-
2
-
-
0036893186
-
ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions
-
Dong JF, Moake JL, Nolasco L et al. ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions. Blood 2002; 100: 4033-4039.
-
(2002)
Blood
, vol.100
, pp. 4033-4039
-
-
Dong, J.F.1
Moake, J.L.2
Nolasco, L.3
-
3
-
-
26444551183
-
Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice
-
Motto DG, Chauhan AK, Zhu G et al. Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice. J Clin Invest 2005; 115: 2752-2761.
-
(2005)
J Clin Invest
, vol.115
, pp. 2752-2761
-
-
Motto, D.G.1
Chauhan, A.K.2
Zhu, G.3
-
4
-
-
31544475409
-
Thrombospondin-1 controls vascular platelet recruitment and thrombus adherence in mice by protecting (sub)endothelial VWF from cleavage by ADAMTS-13
-
Bonnefoy A, Daenens K, Feys HB et al. Thrombospondin-1 controls vascular platelet recruitment and thrombus adherence in mice by protecting (sub)endothelial VWF from cleavage by ADAMTS-13. Blood 2006; 107: 955-964.
-
(2006)
Blood
, vol.107
, pp. 955-964
-
-
Bonnefoy, A.1
Daenens, K.2
Feys, H.B.3
-
5
-
-
28844502248
-
Enzymatically-active ADAMTS13 variants are not inhibited by anti-ADAMTS13 autoantibodies - A novel therapeutic strategy?
-
Zhou W, Dong L, Ginsburg D et al. Enzymatically-active ADAMTS13 variants are not inhibited by anti-ADAMTS13 autoantibodies - a novel therapeutic strategy? J Biol Chem 2005; 280: 39934-39941.
-
(2005)
J Biol Chem
, vol.280
, pp. 39934-39941
-
-
Zhou, W.1
Dong, L.2
Ginsburg, D.3
-
6
-
-
0012580388
-
ADAMTS13 gene mutation in congenital thrombotic thrombocytopenic purpura with previously reported normal VWF cleaving protease activity
-
Savasan S, Lee SK, Ginsburg D, Tsai HM. ADAMTS13 gene mutation in congenital thrombotic thrombocytopenic purpura with previously reported normal VWF cleaving protease activity. Blood 2003; 101: 4449-4451.
-
(2003)
Blood
, vol.101
, pp. 4449-4451
-
-
Savasan, S.1
Lee, S.K.2
Ginsburg, D.3
Tsai, H.M.4
-
7
-
-
10744223121
-
ADAMTS 13 genotype and vWF protease activity in an Italian family with TTP
-
Bestetti G, Stellari A, Lattuada A et al. ADAMTS 13 genotype and vWF protease activity in an Italian family with TTP. Thromb Haemost 2003; 90: 955-956.
-
(2003)
Thromb Haemost
, vol.90
, pp. 955-956
-
-
Bestetti, G.1
Stellari, A.2
Lattuada, A.3
-
8
-
-
30144440926
-
Modulation of ADAMTS13 secretion and specific activity by a combination of common amino-acid polymorphisms and a missense mutation
-
Plaimauer B, Fuhrmann J, Mohr G et al. Modulation of ADAMTS13 secretion and specific activity by a combination of common amino-acid polymorphisms and a missense mutation. Blood 2006; 107: 118-125.
-
(2006)
Blood
, vol.107
, pp. 118-125
-
-
Plaimauer, B.1
Fuhrmann, J.2
Mohr, G.3
-
9
-
-
23944468642
-
Complement factor H mutation in familial thrombotic thrombocytopenic purpura with ADAMTS13 deficiency and renal involvement
-
Noris M, Bucchioni S, Galbusera M et al. Complement factor H mutation in familial thrombotic thrombocytopenic purpura with ADAMTS13 deficiency and renal involvement. J Am Soc Nephrol 2005; 16: 1177-1183.
-
(2005)
J Am Soc Nephrol
, vol.16
, pp. 1177-1183
-
-
Noris, M.1
Bucchioni, S.2
Galbusera, M.3
-
10
-
-
23744486523
-
ADAMTS13 autoantibodies in patients with thrombotic microangiopathies and other immunomediated diseases
-
Rieger M, Mannucci PM, Kremer Hovinga JA et al. ADAMTS13 autoantibodies in patients with thrombotic microangiopathies and other immunomediated diseases. Blood 2005; 106: 1262-1267.
-
(2005)
Blood
, vol.106
, pp. 1262-1267
-
-
Rieger, M.1
Mannucci, P.M.2
Kremer Hovinga, J.A.3
-
11
-
-
33646459182
-
ADAMTS13-Binding IgG are present in patients with thrombotic thrombocytopenic purpura
-
in press
-
Tsai HM, Raoufi M, Zhou W et al. ADAMTS13-Binding IgG are present in patients with thrombotic thrombocytopenic purpura. Thromb Haemost 2006 (in press).
-
(2006)
Thromb Haemost
-
-
Tsai, H.M.1
Raoufi, M.2
Zhou, W.3
-
12
-
-
15244348050
-
Shiga-toxin-producing Escherichia coli and haemolytic uraemic syndrome
-
Tarr PI, Gordon CA, Chandler WL. Shiga-toxin-producing Escherichia coli and haemolytic uraemic syndrome. Lancet 2005; 365: 1073-1086.
-
(2005)
Lancet
, vol.365
, pp. 1073-1086
-
-
Tarr, P.I.1
Gordon, C.A.2
Chandler, W.L.3
-
13
-
-
0023801292
-
Direct cytotoxic action of Shiga toxin on human vascular endothelial cells
-
Obrig TG, Del Vecchio PJ, Brown JE et al. Direct cytotoxic action of Shiga toxin on human vascular endothelial cells. Infect Immun 1988; 56: 2373-2378.
-
(1988)
Infect Immun
, vol.56
, pp. 2373-2378
-
-
Obrig, T.G.1
Del Vecchio, P.J.2
Brown, J.E.3
-
14
-
-
0035035397
-
Willebrand factor and von Willebrand factor-cleaving metalloprotease activity in Escherichia coli O157:H7-associated hemolytic uremic syndrome
-
Tsai HM, Chandler WL, Sarode R et al. von Willebrand factor and von Willebrand factor-cleaving metalloprotease activity in Escherichia coli O157:H7-associated hemolytic uremic syndrome. Pediatr Res 2001; 49: 653-659.
-
(2001)
Pediatr Res
, vol.49
, pp. 653-659
-
-
Tsai, H.M.1
Chandler, W.L.2
Sarode, R.3
-
15
-
-
28844503491
-
Hemolytic uremic syndrome-associated Shiga toxins promote endothelial-cell secretion and impair ADAMTS13 cleavage of unusually large von Willebrand factor multimers
-
Nolasco LH, Turner NA, Bernardo A et al. Hemolytic uremic syndrome-associated Shiga toxins promote endothelial-cell secretion and impair ADAMTS13 cleavage of unusually large von Willebrand factor multimers. Blood 2005; 106: 4199-4209.
-
(2005)
Blood
, vol.106
, pp. 4199-4209
-
-
Nolasco, L.H.1
Turner, N.A.2
Bernardo, A.3
-
16
-
-
27844566613
-
Atypical haemolytic uraemic syndrome and mutations in complement regulator genes
-
Dragon-Durey MA, Fremeaux-Bacchi V. Atypical haemolytic uraemic syndrome and mutations in complement regulator genes. Springer Semin Immunopathol 2005; 27: 359-374.
-
(2005)
Springer Semin Immunopathol
, vol.27
, pp. 359-374
-
-
Dragon-Durey, M.A.1
Fremeaux-Bacchi, V.2
-
17
-
-
26944480588
-
The development of atypical haemolytic-uraemic syndrome is influenced by susceptibility factors in factor H and membrane cofactor protein: Evidence from two independent cohorts
-
Fremeaux-Bacchi V, Kemp EJ, Goodship JA et al. The development of atypical haemolytic-uraemic syndrome is influenced by susceptibility factors in factor H and membrane cofactor protein: evidence from two independent cohorts. J Med Genet 2005; 42: 852-856.
-
(2005)
J Med Genet
, vol.42
, pp. 852-856
-
-
Fremeaux-Bacchi, V.1
Kemp, E.J.2
Goodship, J.A.3
-
18
-
-
20544437666
-
Anti-factor H autoantibodies associated with atypical hemolytic uremic syndrome
-
Dragon-Durey MA, Loirat C, Cloarec S et al. Anti-factor H autoantibodies associated with atypical hemolytic uremic syndrome. J Am Soc Nephrol 2005; 16: 555-563.
-
(2005)
J Am Soc Nephrol
, vol.16
, pp. 555-563
-
-
Dragon-Durey, M.A.1
Loirat, C.2
Cloarec, S.3
-
19
-
-
0022904646
-
H deficiency in two brothers with atypical dense intramembranous deposit disease
-
Levy M, Halbwachs-Mecarelli L, Gubler MC et al. H deficiency in two brothers with atypical dense intramembranous deposit disease. Kidney Int 1986; 30: 949-956.
-
(1986)
Kidney Int
, vol.30
, pp. 949-956
-
-
Levy, M.1
Halbwachs-Mecarelli, L.2
Gubler, M.C.3
-
20
-
-
1542318912
-
Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: Report and genetic analysis of 16 cases
-
Dragon-Durey MA, Fremeaux-Bacchi V, Loirat C et al. Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases. J Am Soc Nephrol 2004; 15: 787-795.
-
(2004)
J Am Soc Nephrol
, vol.15
, pp. 787-795
-
-
Dragon-Durey, M.A.1
Fremeaux-Bacchi, V.2
Loirat, C.3
-
21
-
-
0028214132
-
Hereditary complement factor I deficiency
-
Vyse TJ, Spath PJ, Davies KA et al. Hereditary complement factor I deficiency. Q J Med 1994; 87: 385-401.
-
(1994)
Q J Med
, vol.87
, pp. 385-401
-
-
Vyse, T.J.1
Spath, P.J.2
Davies, K.A.3
|