Sickle-cell haemoglobin polymerization: Is it the primary pathogenic event of sickle-cell anaemia?

British Journal of Haematology

Volumn 139, Issue 2, 2007, Pages 173-184

  Vekilov, Peter G ^a,b  

^a University of Houston   (United States)

^b UNIVERSITY OF HOUSTON   (United States)

Author keywords

Aggregation; Haemoglobin disorders; Molecular haematology; Sickle cell anaemia

Indexed keywords

HEMOGLOBIN S; POLYMERIZED HEMOGLOBIN; WATER;

CELL GROWTH; CELL NUCLEUS; ENTROPY; FIBER; HUMAN; LIQUID; MOLECULAR SIZE; NONHUMAN; NUCLEAR DIVISION; PATHOGENESIS; POLYMERIZATION; PRIORITY JOURNAL; PROTEIN STRUCTURE; REVIEW; SENSITIVITY ANALYSIS; SHEAR FLOW; SICKLE CELL ANEMIA; SOLUTION AND SOLUBILITY; TEMPERATURE;

ANEMIA, SICKLE CELL; ANIMALS; BIOMECHANICS; BIOPOLYMERS; HEMOGLOBIN, SICKLE; HUMANS; MICE; MICROSCOPY, CONFOCAL; PROTEIN CONFORMATION;

EID: 34848813177     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/j.1365-2141.2007.06794.x     Document Type: Review

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