Severe deficiencies of IGF-I, IGF-II, IGFBP-3, ALS and paradoxically high-normal bone mass in a child with insulin-resistance syndrome (Rabson-Mendenhall type)

Growth Hormone and IGF Research

Volumn 17, Issue 5, 2007, Pages 399-407

  Fowlkes, J L ^a   Bunn, R C ^a   Coleman, H N ^a   Hall, B ^b   Reid, M C ^b   Thrailkill, K M ^a  

^a UNIVERSITY OF ARKANSAS FOR MEDICAL SCIENCES   (United States)

^b UNIVERSITY OF KENTUCKY   (United States)

Author keywords

Diabetes; Donahue's Syndrome; DXA; Growth; Growth hormone; Hyperinsulinism; Insulin receptor

Indexed keywords

ACID LABILE SUBUNIT; ARGININE; CLONIDINE; GENOMIC DNA; GLUCOSE; GROWTH HORMONE RELEASING FACTOR; HUMAN GROWTH HORMONE; ROSIGLITAZONE; SOMATOMEDIN B; SOMATOMEDIN BINDING PROTEIN 3; SOMATOMEDIN C; TROGLITAZONE; UNCLASSIFIED DRUG;

ARTICLE; BLOOD GLUCOSE MONITORING; BODY HEIGHT; BONE DENSITY; BONE DISEASE; CASE REPORT; CHILD; CLINICAL FEATURE; DIET RESTRICTION; DNA DETERMINATION; DRUG DOSE INCREASE; DRUG SUBSTITUTION; DRUG WITHDRAWAL; DUAL ENERGY X RAY ABSORPTIOMETRY; GLYCEMIC CONTROL; GROWTH HORMONE DEFICIENCY; GROWTH RETARDATION; HOMOZYGOSITY; HORMONAL REGULATION; HORMONE DETERMINATION; HORMONE SYNTHESIS; HUMAN; HYPERGLYCEMIA; HYPERINSULINEMIA; INSULIN RESISTANCE; LONG BONE; MALE; METABOLIC SYNDROME X; ORAL GLUCOSE TOLERANCE TEST; PRIORITY JOURNAL; RABSON MENDENHALL SYNDROME; SINGLE NUCLEOTIDE POLYMORPHISM;

BODY HEIGHT; BODY SIZE; BODY WEIGHT; BONE DENSITY; CHILD; CHILD, PRESCHOOL; DNA; FEMALE; HUMANS; HYPERINSULINISM; INFANT; INSULIN RESISTANCE; INSULIN-LIKE GROWTH FACTOR BINDING PROTEIN 3; INSULIN-LIKE GROWTH FACTOR I; INSULIN-LIKE GROWTH FACTOR II; MALE; PEDIGREE; PROTEIN SUBUNITS; SYNDROME;

EID: 34548273071     PISSN: 10966374     EISSN: 15322238     Source Type: Journal    
DOI: 10.1016/j.ghir.2007.04.007     Document Type: Article

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