The French registry of pulmonary arterial hypertension in children: Rationale and design

Current Medical Research and Opinion

Volumn 23, Issue SUPPL. 2, 2007, Pages

  Fraisse, Alain ^a   Godart, François ^b   Bonnet, Damien ^c   Gressin, Virginie ^d   Voisin, Michel ^e   Dauphin, Claire ^f   Schleich, Jean Marc ^g   Clerson, Pierre ^h   Beghetti, Maurice ^i,j   Simonneau, Gérald ^j  

^a TIMONE HOSPITAL   (France)

^b LILLE UNIVERSITY HOSPITAL   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

^d Actelion Pharmaceuticals France   (France)

^e HÔPITAL ARNAUD DE VILLENEUVE   (France)

^f SERVICE DE RHUMATOLOGIE   (France)

^g PONTCHAILLOU UNIVERSITY HOSPITAL   (France)

^h Orgametrie   (France)

ⁱ Department of Pediatrics   (Switzerland)

^j HÔPITAL ANTOINE BÉCLÈRE   (France)

more..

Author keywords

Children; French registry; Paediatric PAH; Pulmonary arterial hypertension

Indexed keywords

ADOLESCENT; CHILD; CLINICAL FEATURE; CONFERENCE PAPER; CONGENITAL HEART DISEASE; CONTROLLED STUDY; DEMOGRAPHY; DISEASE COURSE; DOPPLER ECHOCARDIOGRAPHY; FEMALE; FOLLOW UP; HEART CATHETERIZATION; HUMAN; INCIDENCE; MAJOR CLINICAL STUDY; MALE; MORBIDITY; PATHOGENESIS; PREVALENCE; PROSPECTIVE STUDY; PULMONARY HYPERTENSION; QUALITY OF LIFE; RISK FACTOR; SURVIVAL RATE;

EID: 34547447074     PISSN: 03007995     EISSN: None     Source Type: Journal    
DOI: 10.1185/030079907X199501     Document Type: Conference Paper

References (24)

1. Widliz A, Barst RJ. Pulmonary arterial hypertension in children. Eur Respir J 2003;21:155-76
2. Simonneau G, Galié N, Rubin LJ, et al. Clinical classification of pulmonary hypertension. J Am Coll Cardiol 2004;43:5S-12
3. D'Alonzo GE, Barst RJ, Ayres SM, et al. Survival in patients with primary pulmonary hypertension. Results from a national prospective registry. Ann Intern Med 1991;115:343-9
4. Galié N, Seeger W, Naeije R, et al. Comparative analysis of clinical trials and evidence-based treatment algorithm in pulmonary arterial hypertension. J Am Coll Cardiol 2004;43:81S-88
5. Humbert M, Sitbon O, Chaouat A, et al. Pulmonary arterial hypertension in France. Results from a national registry. Am J Respir Crit Care Med 2006;173:1023-30
6. Sandoval J, Bauerle O, Gomez A, et al. Primary pulmonary hypertension in children: clinical characterization and survival. J Am Coll Cardiol 1995;25:466-74
7. Rosenzweig EB, Ivy DD, Widlitz AC, at al. Effects of long term bosentan in children with pulmonary arterial hypertension. J Am Coll Cardiol 2005;46;697-704
8. Lang IM, Bonderman D, Kneussl M, et al. Paediatric pulmonary vascular disease. Paediatr Respir Rev 2004;5:238-48
9. Guidelines on diagnosis and treatment of pulmonary arterial hypertension. The Task Force on Diagnosis and Treatment of Pulmonary Arterial Hypertension of ffie European Society of Cardiology. Eur Heart J 2004;25:2243-78
10. Rosenzweig EB, Widlitz AC, Barst RJ. Pulmonary arterial hypertension in children. Pediatr Pulmonol 2004;38:2-22
11. Badesch DB, Abman SH, Ahearn GS, et al. Medical therapy for pulmonary arterial hypertension. ACCP evidence-based clinical practice guidelines. Chest 2004;126:35S-62
12. Barst RJ, Maislin G, Fishman AP. Vasodilator therapy for primary pulmonary hypertension in children. Circulation 1999;99:1197-208
13. Yung D, Widlitz AC, Rosenzweig EB, et al. Outcomes in children with idiopathic pulmonary hypertension. Circulation 2004;110:660-5
14. Brans LA, Chrisant MK, Lamour JM, et al. Carvedilol as therapy in pediatric heart failure: an initial multicenter experience. J Pediatr 2001;138:505-11
15. Manificat S, Dazord A, Langue J, et al. Evaluation of the quality of life of infants and very young children: validation of a questionnaire. Mutlicenter European Study. Arch Pediatr 2000;7:605-14
16. Manificat S, Dazord A. Child and adolescent quality of life: study analysis. Rech Soins Infirm 2002;70:13-22
17. Manificat S, Dazord A, Cochat P, et al. Evaluation of the quality of life in pediatrics: how to collect the point of view of children. Arch Pediatr 1997;4:1238-46
18. Landgraf JM, Maunsell E, Speechley KN, et al. Canadian-French, German and UK versions of the Child Health Questionnaire: methodology and preliminary item scaling results. Qual Life Res 1998;7:433-45
19. Rhodes J, Barst RJ, Garafono RP, et al. Hemodynamic correlates of exercise function in patients with primary pulmonary hypertension. J Am Coll Cardiol 1991;18:1738-44
20. Garofano RP, Barst RJ. Exercise testing in children with primary pulmonary hypertension. Pediatr Cardiol 1999;20:61-4
21. Oya H, Nagaya N, Uematsu M, et al. Poor prognosis and related factors in adults with Eisenmenger syndrome. Am Heart J 2002;143:739-44
22. Hopkins WE, Ochoa LL, Richardson GW, et al. Comparison of the hemodynamics and survival of adults with severe primary pulmonary hypertension or Eisenmenger syndrome. J Heart Lung Transplant 1996;15:100-5
23. Hopkins WE. The remarkable right ventricle of patients with Eisenmenger syndrome. Coron Artery Dis 2005;16:19-25
24. Hoeper MM, Oudiz RJ, Peacock A, et al. End points and clinical trial designs in pulmonary arterial hypertension. Clinical and regulatory perspectives. J Am Coll Cardiol 2004;43:48S-55