Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (Rendu-Osler disease)

Respiration

Volumn 74, Issue 4, 2007, Pages 361-378

  Cottin, Vincent ^a,b   Dupuis Girod, Sophie ^a   Lesca, Gaetan ^a   Cordier, Jean François ^a  

^a UNIVERSITÉ LYON 1   (France)

^b LOUIS PRADEL HOSPITAL   (France)

Author keywords

Cerebral abscess; Hereditary hemorrhagic telangiectasia; Pulmonary arteriovenous malformation; Pulmonary hypertension; Rendu Osler Weber disease; Right to left shunting

Indexed keywords

BOSENTAN; CONTRAST MEDIUM; IRON; NIFEDIPINE; PROSTACYCLIN; SILDENAFIL; TECHNETIUM 99M; UNIPROST;

ABSCESS; ARGON LASER; ARTERIOVENOUS MALFORMATION; ARTERIOVENOUS SHUNT; ARTIFICIAL EMBOLISM; AUTOSOMAL DOMINANT DISORDER; BALLOON EMBOLIZATION; BLEEDING; BRAIN CIRCULATION; CEREBROVASCULAR ACCIDENT; COIL EMBOLIZATION; COMPUTER ASSISTED TOMOGRAPHY; CONTRAST ECHOCARDIOGRAPHY; DYSPNEA; ECHOCARDIOGRAPHY; EPISTAXIS; GENE DELETION; GENE DUPLICATION; GENE INACTIVATION; GENE LOCATION; GENE LOCUS; GENE MUTATION; GENETIC DISORDER; GENETIC PREDISPOSITION; HEART CATHETERIZATION; HEART OUTPUT; HEART RIGHT LEFT SHUNT; HISTOLOGY; HUMAN; INNATE IMMUNITY; IRON THERAPY; LIVER TRANSPLANTATION; LOW LEVEL LASER THERAPY; LUNG ARTERIOVENOUS MALFORMATION; LUNG BLOOD VESSEL; LUNG SCINTISCANNING; MICROSURGERY; MISSENSE MUTATION; MULTIDETECTOR COMPUTED TOMOGRAPHY; NONHUMAN; PRIORITY JOURNAL; PULMONARY ARTERY; PULMONARY HYPERTENSION; PULMONARY VEIN; RECANALIZATION; RENDU OSLER WEBER DISEASE; REVIEW; RISK ASSESSMENT; SENSITIVITY AND SPECIFICITY; TELANGIECTASIA; THORAX RADIOGRAPHY; THREE DIMENSIONAL IMAGING; TRANSIENT ISCHEMIC ATTACK; TRICUSPID VALVE REGURGITATION; VASCULAR DISEASE;

ANGIOGRAPHY; HUMANS; HYPERTENSION, PULMONARY; PREVALENCE; PULMONARY ARTERY; PULMONARY VEINS; TELANGIECTASIA, HEREDITARY HEMORRHAGIC; TOMOGRAPHY, X-RAY COMPUTED; WORLD HEALTH;

EID: 34447633917     PISSN: 00257931     EISSN: None     Source Type: Journal    
DOI: 10.1159/000103205     Document Type: Review

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