Orthotopic liver transplantation in glucose-6-phosphatase deficiency - von Gierke disease - With Multiple hepatic adenomas and concomitant focal nodular hyperplasia

Journal of Pediatric Endocrinology and Metabolism

Volumn 20, Issue 4, 2007, Pages 545-549

  Carreiro, Gerson ^a   Villela Nogueira, Cristiane A ^a,b   Coelho, Henrique Sérgio M ^a   Basto, Samanta ^a   Pannain, Vera Lucia ^a   Caroli Bottino, Adriana ^a   Filho, Joaquim Ribeiro ^a  

^a FEDERAL UNIVERSITY OF RIO DE JANEIRO   (Brazil)

^b NONE   (Brazil)

Author keywords

Focal nodular hyperplasia; Glycogen storage disease type I; Liver cell adenoma; Liver transplantation; von Gierke disease

Indexed keywords

GLUCOSE 6 PHOSPHATASE; PREDNISONE; TACROLIMUS;

ADULT; ARTICLE; CADAVER DONOR; CASE REPORT; COMORBIDITY; COMPUTER ASSISTED TOMOGRAPHY; DIET THERAPY; ECHOGRAPHY; FEMALE; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HUMAN TISSUE; IMMUNOSUPPRESSIVE TREATMENT; LIVER ADENOMA; LIVER BIOPSY; LIVER HYPERPLASIA; LIVER TRANSPLANTATION; MALIGNANT TRANSFORMATION; METABOLIC REGULATION; PROGNOSIS; SYMPTOMATOLOGY; TREATMENT INDICATION; TREATMENT OUTCOME; TREATMENT PLANNING;

EID: 34249875958     PISSN: 0334018X     EISSN: None     Source Type: Journal    
DOI: 10.1515/JPEM.2007.20.4.545     Document Type: Article

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