Long-term outcome in susac syndrome

Medicine

Volumn 86, Issue 2, 2007, Pages 93-102

  Aubart Cohen, Fleur ^a   Klein, Isabelle ^a   Alexandra, Jean François ^a   Bodaghi, Bahram ^b   Doan, Serge ^a   Fardeau, Christine ^b   Lavallée, Philippa ^a   Piette, Jean Charles ^b   Hoang, Phuc Le ^b   Papo, Thomas ^a  

^a BICHAT HOSPITAL   (France)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYLSALICYLIC ACID; ANTICOAGULANT AGENT; ANTITHROMBOCYTIC AGENT; CORTICOSTEROID; CYCLOPHOSPHAMIDE; FLUINDIONE; FLUORESCEIN; METHYLPREDNISOLONE; NIMODIPINE; PREDNISONE; PROTEIN;

ADULT; ANTICOAGULANT THERAPY; ARTICLE; AUDIOGRAPHY; BRAIN ATROPHY; BRAIN DISEASE; CASE STUDY; CEREBROSPINAL FLUID CYTOLOGY; CLINICAL FEATURE; CORTICOSTEROID THERAPY; DISEASE EXACERBATION; DOSE RESPONSE; DRUG MEGADOSE; DRUG TREATMENT FAILURE; DRUG WITHDRAWAL; FEMALE; FLUORESCENCE ANGIOGRAPHY; FOLLOW UP; HEADACHE; HEARING LOSS; HUMAN; INDUCED ABORTION; INNER EAR DISEASE; LOW DRUG DOSE; MAJOR CLINICAL STUDY; MALE; MONOTHERAPY; NEUROIMAGING; NUCLEAR MAGNETIC RESONANCE IMAGING; ONSET AGE; OPHTHALMOSCOPY; OUTCOMES RESEARCH; PLEOCYTOSIS; PREGNANCY; PREGNANCY OUTCOME; PRIORITY JOURNAL; PROTEIN CEREBROSPINAL FLUID LEVEL; PUERPERIUM; QUANTITATIVE ANALYSIS; RELAPSE; RETINA ANGIOGRAPHY; RETINA ARTERY OCCLUSION; SUSAC SYNDROME;

ADRENAL CORTEX HORMONES; ADULT; ANTICOAGULANTS; ATAXIA; BRAIN; BRAIN DISEASES; CEREBROSPINAL FLUID PROTEINS; COGNITION DISORDERS; CONFUSION; FEMALE; FLUORESCEIN ANGIOGRAPHY; FOLLOW-UP STUDIES; HEADACHE; HEARING LOSS; HUMANS; IMMUNOSUPPRESSIVE AGENTS; LEUKOCYTOSIS; MAGNETIC RESONANCE IMAGING; MALE; PARESTHESIA; PERSONALITY DISORDERS; PLATELET AGGREGATION INHIBITORS; PREGNANCY; PREGNANCY OUTCOME; RETINAL ARTERY OCCLUSION; SYNDROME; TINNITUS; TREATMENT OUTCOME; VERTIGO; VISION DISORDERS;

EID: 34247643072     PISSN: 00257974     EISSN: None     Source Type: Journal    
DOI: 10.1097/MD.0b013e3180404c99     Document Type: Article

References (34)

1. Ayache D, Plouin-Gaudon I, Bakouche P, Elbaz P, Gout O. Microangiopathy of the inner ear, retina, and brain (Susac syndrome): report of a case. Arch Otolaryngol Head Neck Surg. 2000;126:82-84.
2. Bakri SJ, Kaiser PK. Ocular manifestations of West Nile virus. Curr Opin Ophthalmol. 2004;15:537-540.
3. Ballard E, Butzer JF, Donders J. Susac's syndrome: neuropsychological characteristics in a young man. Neurology. 1996;47:266-268.
4. Bogousslavsky J, Gaio JM, Caplan LR, Regli F, Hommel M, Hedges TR III, Ferrazzini M, Pollak P. Encephalopathy, deafness and blindness in young women: a distinct retinocochleocerebral arteriolopathy? J Neurol Neurosurg Psychiatry. 1989;52:43-46.
5. Bousser MG, Biousse V. Small vessel vasculopathies affecting the central nervous system. J Neuroophthalmol. 2004;24:56-61.
6. Coppeto JR, Currie JN, Monteiro ML, Lessell S. A syndrome of arterial-occlusive retinopathy and encephalopathy. Am J Ophthalmol. 1984;98:189-202.
7. Do TH, Fisch C, Evoy F. Susac syndrome: report of four cases and review of the literature. AJNR Am J Neuroradiol. 2004;25:382-388.
8. Donnan GA, Plummer C, Rattray K, Basilli S. An unusual disease presenting at an unusual age: Susac's syndrome. J Clin Neurosci. 2005;12:99.
9. Egan RA, Ha Nguyen T, Gass JD, Rizzo JF III, Tivnan J, Susac JO. Retinal arterial wall plaques in Susac syndrome. Am J Ophthalmol. 2003;135:483-486.
10. Gordon DL, Hayreh SS, Adams HP Jr. Microangiopathy of the brain, retina, and ear: improvement without immunosuppressive therapy. Stroke. 1991;22:933-937.
11. Gross M, Banin E, Eliashar R, Ben-Hur T. Susac syndrome. Otol Neurotol. 2004;25:470-473.
12. Johnson MW, Flynn HW Jr, Gass JD. Idiopathic recurrent branch retinal arterial occlusion. Arch Ophthalmol. 1989;107:757.
13. Lansberg MG, Thijs VN, O'Brien MW, Ali JO, de Crespigny AJ, Tong DC, Moseley ME, Albers GW. Evolution of apparent diffusion coefficient, diffusion-weighted, and T2-weighted signal intensity of acute stroke. AJNR Am J Neuroradiol. 2001;22:637-644.
14. Li HK, Dejean BJ, Tang RA. Reversal of visual loss with hyperbaric oxygen treatment in a patient with Susac syndrome. Ophthalmology. 1996;103:2091-2098.
15. MacFadyen DJ, Schneider RJ, Chisholm IA. A syndrome of brain, inner ear and retinal microangiopathy. Can J Neurol Sci. 1987;14:315-318.
16. Mala L, Bazard MC, Berrod JP, Wahl D, Raspiller A. [Small retinal, cochlear, and cerebral infarctions in the young patient, "SICRET" syndrome of Susac syndrome]. J Fr Ophtalmol. 1998;21:375-380.
17. Monteiro ML, Swanson RA, Coppeto JR, Cuneo RA, DeArmond SJ, Prusiner SB. A microangiopathic syndrome of encephalopathy, hearing loss, and retinal arteriolar occlusions. Neurology. 1985;35:1113-1121.
18. Murata Y, Inada K, Negi A. Susac syndrome. Am J Ophthalmol. 2000;129:682-684.
19. Nicolle MW, McLachlan RS. Microangiopathy with retinopathy, encephalopathy, and deafness (RED-M) and systemic features. Semin Arthritis Rheum. 1991;21:123-128.
20. Notis CM, Kitei RA, Cafferty MS, Odel JG, Mitchell JP. Microangiopathy of brain, retina, and inner ear. J Neuroophthalmol. 1995;15:1-8.
21. O'Halloran HS, Pearson PA, Lee WB, Susac JO, Berger JR. Microangiopathy of the brain, retina, and cochlea (Susac syndrome). A report of five cases and a review of the literature. Ophthalmology. 1998;105:1038-1044.
22. Papo T, Biousse V, Lehoang P, Fardeau C, N'Guyen N, Huong DL, Aumaitre O, Bousser MG, Godeau P, Piette JC. Susac syndrome. Medicine (Baltimore). 1998;77:3-11.
23. Petty GW, Engel AG, Younge BR, Duffy J, Yanagihara T, Lucchinetti CF, Bartleson JD, Parisi JE, Kasperbauer JL, Rodriguez M. Retinocochleocerebral vasculopathy. Medicine (Baltimore). 1998;77:12-40.
24. Petty GW, Matteson EL, Younge BR, McDonald TJ, Wood CP. Recurrence of Susac syndrome (retinocochleocerebral vasculopathy) after remission of 18 years. Mayo Clin Proc. 2001;76:958-960.
25. Recchia FM, Brown GC. Systemic disorders associated with retinal vascular occlusion. Curr Opin Ophthalmol. 2000;11:462-467.
26. Susac JO. Susac's syndrome. AJNR Am J Neuroradiol. 2004;25:351-352.
27. Susac JO. Susac's syndrome: the triad of microangiopathy of the brain and retina with hearing loss in young women. Neurology. 1994;44:591-593.
28. Susac JO, Hardman JM, Selhorst JB. Microangiopathy of the brain and retina. Neurology. 1979;29:313-316.
29. Susac JO, Murtagh FR, Egan RA, Berger JR, Bakshi R, Lincoff N, Gean AD, Galetta SL, Fox RJ, Costello FE, Lee AG, Clark J, Layzer RB, Daroff RB. MRI findings in Susac's syndrome. Neurology. 2003;61:1783-1787.
30. Tashima K, Uyama E, Hashimoto Y, Yonehara T, Uchino M. Susac's syndrome: beneficial effects of corticosteroid therapy in a Japanese case. Intern Med. 2001;40:135-139.
31. Vila N, Graus F, Blesa R, Santamaria J, Ribalta T, Tolosa E. Microangiopathy of the brain and retina (Susac's syndrome): two patients with atypical features. Neurology. 1995;45:1225-1226.
32. White ML, Zhang Y, Smoker WR. Evolution of lesions in Susac syndrome at serial MR imaging with diffusion-weighted imaging and apparent diffusion coefficient values. AJNR Am J Neuroradiol. 2004;25:706-713.
33. Xu MS, Tan CB, Umapathi T, Lim CC. Susac syndrome: serial diffusion-weighted MR imaging. Magn Reson Imaging. 2004;22:1295-1298.
34. Zeidman LA, Melen O, Gottardi-Littell N, Getch C, Alberts MJ, Goldstein L, Bernstein RA. Susac syndrome with transient inverted vision. Neurology. 2004;63:591.