Susac's syndrome: Beneficial effects of corticosteroid therapy in a Japanese case

Internal Medicine

Volumn 40, Issue 2, 2001, Pages 135-139

  Tashima, Kazuhiro ^a   Uyama, Eiichiro ^a   Hashimoto, Yoichiro ^b   Yonehara, Toshiro ^c   Uchino, Makoto ^a  

^a KUMAMOTO UNIV SCHOOL OF MEDICINE   (Japan)

^b KUMAMOTO CITY HOSPITAL   (Japan)

^c SAISEIKAI KUMAMOTO HOSPITAL   (Japan)

Author keywords

Microangiopathy; Retinal arterior occlusion; Sensorineural hearing loss; Subacute encephalopathy

Indexed keywords

METHYLPREDNISOLONE; PREDNISONE;

ADULT; ARTICLE; BRAIN DISEASE; CASE REPORT; CAUCASIAN; CORTICOSTEROID THERAPY; DRUG EFFECT; HEARING LOSS; HUMAN; MALE; MICROANGIOPATHY; NUCLEAR MAGNETIC RESONANCE IMAGING; PERCEPTION DEAFNESS; REMISSION; SUSAC SYNDROME; WHITE MATTER;

EID: 0035087507     PISSN: 09182918     EISSN: None     Source Type: Journal    
DOI: 10.2169/internalmedicine.40.135     Document Type: Article

References (20)

1. Susac JO, Hardman JM, Selhorst JB. Microangiopathy of the brain and retina. Neurology 29: 313-316, 1979.
2. Susac JO. Susac's syndrome: the triad of microangiopathy of the brain and retina with hearing loss in young women. Neurology 44: 591-593, 1994.
3. Monteiro MLR, Swanson RA, Coppeto JR, Cuneo RA, DeArmond SJ. Prusiner SB. A microangiopathic syndrome of encephalopathy, hearing loss, and retinal arteriolar occlusions. Neurology 35: 1113-1121, 1985.
4. MacFadyen DJ, Schneider RJ, Chisholm IA. A syndrome of brain, inner ear and retinal microangiopathy. Can J Neurol Sci 14: 315-318, 1987.
5. Heiskala H, Somer H, Kovanen J, Poutiainen E, Karli H, Haltia M. Microangiopathy with encephalopathy, hearing loss and retinal arteriolar occlusions: two new cases. J Neurol Sci 86: 239-250, 1988.
6. Bogousslavsky J, Gaio JM, Caplan LR, et al. Encephalopathy, deafness and blindness in young women: a distinct retinocochleocerebral arteriolopathy? J Neurol Neurosurg Psychiatry 52: 43-46, 1989 (see comments).
7. Kaminska EA, Sadler M, Sangalang V, Hoskinmott A, Silverberg D. Microangiopathic syndrome of encephalopathy, retinal vessel occlusion and hearing loss. Can J Neurol Sci 17: 241, 1990 (Abstract).
8. Gordon DL, Hayreh SS, Adams HP Jr. Microangiopathy of the brain, retina, and ear: improvement without immunosuppressive therapy. Stroke 22: 933-937, 1991.
9. Schwitter J, Agosti R, Ott P, Kalman A, Waespe W. Small infarctions of cochlear, retinal, and encephalic tissue in young women. Stroke 23: 903-907, 1992.
10. Vila N, Graus F, Blesa R, Santamaria J, Ribalta T, Tolosa E. Microangiopathy of the brain and retina (Susac's syndrome): two patients with atypical features. Neurology 45: 1225-1226, 1995.
11. Ballard E, Butzer JF, Donders J. Susac's syndrome: neuropsychological characteristics in a young man. Neurology 47: 266-268, 1996.
12. Li HK, Dejean BJ, Tang RA. Reversal of visual loss with hyperbaric oxygen treatment in a patient with Susac syndrome. Ophthalmology 103: 2091-2098, 1996.
13. Wildemann B, Schulin C, Storch-Hagenlocher B, et al. Susac's syndrome: improvement with combined antiplatelet and calcium antagonist therapy. Stroke 27: 149-151, 1996 (letter).
14. Bateman ND, Johnson IJ, Gibbin KP. Susac's syndrome: a rare cause of fluctuating sensorineural hearing loss. J Laryngol Otol 111: 1072-1074, 1997.
15. O'Halloran HS, Pearson PA, Lee WB, Susac JO, Berger JR. Microangiopathy of the brain, retina, and cochlea (Susac syndrome). Ophthalmology 105: 1038-1044, 1998.
16. Papo T, Biousse V, Lehoang P, et al. Susac syndrome. Medicine (Baltimore) 77: 3-11, 1998.
17. Barker RA, Anderson JR, Meyer P, Dick DJ, Scolding NJ. Microangiopathy of the brain and retina with hearing loss in a 50 year old woman: extending the spectrum of Susac's syndrome. J Neurol Neurosurg Psychiatry 66: 641-643, 1999.
18. Sahin O, Goldslein DA, Tessler HH. Findings typical of Susac's syndrome in a patient with scleroderma. Retina 19: 476-477, 1999.
19. Meca-Lallana JE, Martin JJ, Lucas C, et al. Susac syndrome: clinical and diagnostic approach: a new case report. Rev Neurol 29: 1027-1032, 1999 (In Spanish, Abstract in English).
20. Ehsan T, Hasan S, Powers JM, Heiserman JE. Serial magnetic resonance imaging in isolated angiitis of the central nervous system. Neurology 45: 1462-1465, 1995.