Simultaneous manifestation of fulminant infectious mononucleosis with haemophagocytic syndrome and B-cell lymphoma in X-linked lymphoproliferative disease

European Journal of Pediatrics

Volumn 166, Issue 6, 2007, Pages 589-593

  Hügle, Boris ^a   Astigarraga, Itziar ^b   Henter, Jan Inge ^c   Porwit Macdonald, Anna ^c   Meindl, Alfons ^d   Schuster, Volker ^a  

^a UNIVERSITY OF LEIPZIG   (Germany)

^b HOSPITAL DE CRUCES   (Spain)

^c KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^d TECHNICAL UNIVERSITY OF MUNICH   (Germany)

Author keywords

Lymphoma; Measles; SH2D1A; VAHS; X linked lymphoproliferative disease

Indexed keywords

CYCLOPHOSPHAMIDE; DEXAMETHASONE; ETOPOSIDE; MEASLES VACCINE; SIGNALING LYMPHOCYTE ACTIVATION MOLECULE ASSOCIATED PROTEIN;

ARTICLE; AUTOPSY; B CELL LYMPHOMA; BONE MARROW BIOPSY; CASE REPORT; DEATH; DISEASE ASSOCIATION; DISEASE COURSE; DISEASE SEVERITY; EPSTEIN BARR VIRUS; FAMILY HISTORY; FATALITY; GENE MUTATION; HEMOPHAGOCYTIC SYNDROME; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNE DEFICIENCY; INFECTIOUS MONONUCLEOSIS; LIVER FAILURE; LYMPHOPROLIFERATIVE DISEASE; MALE; MEASLES VACCINATION; MOLECULAR GENETICS; MUTATIONAL ANALYSIS; NEUROLOGIC DISEASE; PANCYTOPENIA; PRESCHOOL CHILD; PRIORITY JOURNAL; RELATIVE; VIRUS INFECTION; X CHROMOSOME LINKED DISORDER; X LINKED LYMPHOPROLIFERATIVE DISEASE;

CHILD, PRESCHOOL; FATAL OUTCOME; HUMANS; INFECTIOUS MONONUCLEOSIS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; LYMPHOMA, B-CELL; LYMPHOPROLIFERATIVE DISORDERS; MALE;

EID: 34247400182     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-006-0290-1     Document Type: Article

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