-
2
-
-
0025355607
-
Pulmonary function and clinical course in patients with CF after pulmonary colonization with Pseudomonas aeruginosa
-
Kerem E, Corey M, Gold R, Levison H. Pulmonary function and clinical course in patients with CF after pulmonary colonization with Pseudomonas aeruginosa. J Pediatr 1990;116:714-19.
-
(1990)
J Pediatr
, vol.116
, pp. 714-719
-
-
Kerem, E.1
Corey, M.2
Gold, R.3
Levison, H.4
-
3
-
-
0031471090
-
Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis
-
Corey M, Edwards L, Levison H, Knowles M. Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis. J Pediatr 1997;131:809-14.
-
(1997)
J Pediatr
, vol.131
, pp. 809-814
-
-
Corey, M.1
Edwards, L.2
Levison, H.3
Knowles, M.4
-
4
-
-
1542267792
-
Association between initial disease presentation, lung disease outcomes, and survival in patients with cystic fibrosis
-
Lai HJ, Cheng Y, Cho H, Kosorok MR, Farrell PM. Association between initial disease presentation, lung disease outcomes, and survival in patients with cystic fibrosis. Am J Epidemiol 2004;159:537-46.
-
(2004)
Am J Epidemiol
, vol.159
, pp. 537-546
-
-
Lai, H.J.1
Cheng, Y.2
Cho, H.3
Kosorok, M.R.4
Farrell, P.M.5
-
5
-
-
0034810513
-
Wasting as an independent predictor of mortality in patients with cystic fibrosis
-
Sharma R, Florea VG, Bolger AP, Doehner W, Florea ND, Coats AJ, Hodson ME, Anker SD, Henein MY. Wasting as an independent predictor of mortality in patients with cystic fibrosis. Thorax 2001;56:746-50.
-
(2001)
Thorax
, vol.56
, pp. 746-750
-
-
Sharma, R.1
Florea, V.G.2
Bolger, A.P.3
Doehner, W.4
Florea, N.D.5
Coats, A.J.6
Hodson, M.E.7
Anker, S.D.8
Henein, M.Y.9
-
6
-
-
0037390820
-
Median household income and mortality rate in cystic fibrosis
-
O'Connor GT, Quinton HB, Kneeland T, Kahn R, Lever T, Maddock J, Robichaud P, Detzer M, Swartz DR. Median household income and mortality rate in cystic fibrosis. Pediatrics 2003;111(4 Pt 1):e333-9.
-
(2003)
Pediatrics
, vol.111
, Issue.4 PART 1
-
-
O'Connor, G.T.1
Quinton, H.B.2
Kneeland, T.3
Kahn, R.4
Lever, T.5
Maddock, J.6
Robichaud, P.7
Detzer, M.8
Swartz, D.R.9
-
7
-
-
0038663174
-
Effect of genotype on phenotype and mortality in cystic fibrosis: A retrospective cohort study
-
McKone EF, Emerson SS, Edwards KL, Aitken ML. Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study. Lancet 2003;361:1671-6.
-
(2003)
Lancet
, vol.361
, pp. 1671-1676
-
-
McKone, E.F.1
Emerson, S.S.2
Edwards, K.L.3
Aitken, M.L.4
-
8
-
-
25844451159
-
Modifier genetics: Cystic fibrosis
-
Cutting GR. Modifier genetics: cystic fibrosis. Annu Rev Genomics Hum Genet 2005;6:237-60.
-
(2005)
Annu Rev Genomics Hum Genet
, vol.6
, pp. 237-260
-
-
Cutting, G.R.1
-
9
-
-
0032695668
-
Association of mannose-binding lectin gene heterogeneity with severity of lung disease and survival in cystic fibrosis
-
Garred P, Pressler T, Madsen HO, Frederiksen B, Svejgaard A, Hoiby N, Schwartz M, Koch C. Association of mannose-binding lectin gene heterogeneity with severity of lung disease and survival in cystic fibrosis. J Clin Invest 1999;104:431-7.
-
(1999)
J Clin Invest
, vol.104
, pp. 431-437
-
-
Garred, P.1
Pressler, T.2
Madsen, H.O.3
Frederiksen, B.4
Svejgaard, A.5
Hoiby, N.6
Schwartz, M.7
Koch, C.8
-
10
-
-
33644772194
-
Mannose-binding lectin and its genetic variants
-
Garred P, Larsen F, Seyfarth J, Fujita R, Madsen HO. Mannose-binding lectin and its genetic variants. Genes Immun 2006;7:85-94.
-
(2006)
Genes Immun
, vol.7
, pp. 85-94
-
-
Garred, P.1
Larsen, F.2
Seyfarth, J.3
Fujita, R.4
Madsen, H.O.5
-
11
-
-
0033619497
-
Association of variant alleles of mannose binding lectin with severity of pulmonary disease in cystic fibrosis: Cohort study
-
Gabolde M, Guilloud-Bataille M, Feingold J, Besmond C. Association of variant alleles of mannose binding lectin with severity of pulmonary disease in cystic fibrosis: cohort study. Br Med J 1999;319:1166-7.
-
(1999)
Br Med J
, vol.319
, pp. 1166-1167
-
-
Gabolde, M.1
Guilloud-Bataille, M.2
Feingold, J.3
Besmond, C.4
-
12
-
-
4043052927
-
Polymorphisms in the mannose binding lectin gene affect the cystic fibrosis pulmonary phenotype
-
Yarden J, Radojkovic D, De Boeck K, Macek M Jr, Zemkova D, Vavrova V, Vlietinck R, Cassiman JJ, Cuppens H. Polymorphisms in the mannose binding lectin gene affect the cystic fibrosis pulmonary phenotype. J Med Genet 2004;41:629-33.
-
(2004)
J Med Genet
, vol.41
, pp. 629-633
-
-
Yarden, J.1
Radojkovic, D.2
De Boeck, K.3
Macek Jr, M.4
Zemkova, D.5
Vavrova, V.6
Vlietinck, R.7
Cassiman, J.J.8
Cuppens, H.9
-
13
-
-
23944481077
-
MBL2 polymorphisms screening in a regional Italian CF Center
-
Trevisiol C, Boniotto M, Giglio L, Poli F, Morgutti M, Crovella S. MBL2 polymorphisms screening in a regional Italian CF Center. J Cyst Fibros 2005;4:189-91.
-
(2005)
J Cyst Fibros
, vol.4
, pp. 189-191
-
-
Trevisiol, C.1
Boniotto, M.2
Giglio, L.3
Poli, F.4
Morgutti, M.5
Crovella, S.6
-
14
-
-
33745953585
-
Association between mannan-binding lectin and impaired lung function in cystic fibrosis may be age-dependent
-
Muhlebach MS, MacDonald SL, Button B, Hubbard JJ, Turner ML, Boucher RC, Kilpatrick DC. Association between mannan-binding lectin and impaired lung function in cystic fibrosis may be age-dependent. Clin Exp Immunol 2006;145:302-7.
-
(2006)
Clin Exp Immunol
, vol.145
, pp. 302-307
-
-
Muhlebach, M.S.1
MacDonald, S.L.2
Button, B.3
Hubbard, J.J.4
Turner, M.L.5
Boucher, R.C.6
Kilpatrick, D.C.7
-
15
-
-
0031678410
-
Contribution of genetic factors other than CFTR to disease severity in cystic fibrosis
-
Hull J, Thomson AH. Contribution of genetic factors other than CFTR to disease severity in cystic fibrosis. Thorax 1998;53:1018- 21.
-
(1998)
Thorax
, vol.53
, pp. 1018-1021
-
-
Hull, J.1
Thomson, A.H.2
-
16
-
-
16844367922
-
Association of rumour necrosis factor alpha variants with the CF pulmonary phenotype
-
Yarden J, Radojkovic D, De Boeck K, Macek M Jr, Zemkova D, Vavrova V, Vlietinck R, Cassiman JJ, Cuppens H. Association of rumour necrosis factor alpha variants with the CF pulmonary phenotype. Thorax 2005;60:320-5.
-
(2005)
Thorax
, vol.60
, pp. 320-325
-
-
Yarden, J.1
Radojkovic, D.2
De Boeck, K.3
Macek Jr, M.4
Zemkova, D.5
Vavrova, V.6
Vlietinck, R.7
Cassiman, J.J.8
Cuppens, H.9
-
17
-
-
0034102868
-
TGF-beta(1) genotype and accelerated decline in lung function of patients with cystic fibrosis [see comments]
-
Arkwright PD, Laurie S, Super M, Pravica V, Schwarz MJ, Webb AK, Hutchinson IV. TGF-beta(1) genotype and accelerated decline in lung function of patients with cystic fibrosis [see comments]. Thorax 2000;55:459- 62.
-
(2000)
Thorax
, vol.55
, pp. 459-462
-
-
Arkwright, P.D.1
Laurie, S.2
Super, M.3
Pravica, V.4
Schwarz, M.J.5
Webb, A.K.6
Hutchinson, I.V.7
-
18
-
-
25844491194
-
Genetic modifiers of lung disease in cystic fibrosis
-
Drumm ML, Konstan MW, Schluchter MD, Handler A, Pace R, Zou F, Zariwala M, Fargo D, Xu A, Dunn JM, Darrah RJ, Dorfman R, Sandford AJ, Corey M, Zielenski J, Durie P, Goddard K, Yankaskas JR, Wright FA, Knowles MR. Genetic modifiers of lung disease in cystic fibrosis. N Engl J Med 2005;353:1443-53.
-
(2005)
N Engl J Med
, vol.353
, pp. 1443-1453
-
-
Drumm, M.L.1
Konstan, M.W.2
Schluchter, M.D.3
Handler, A.4
Pace, R.5
Zou, F.6
Zariwala, M.7
Fargo, D.8
Xu, A.9
Dunn, J.M.10
Darrah, R.J.11
Dorfman, R.12
Sandford, A.J.13
Corey, M.14
Zielenski, J.15
Durie, P.16
Goddard, K.17
Yankaskas, J.R.18
Wright, F.A.19
Knowles, M.R.20
more..
-
19
-
-
0034502495
-
Tumor necrosis factor alpha stimulation of human Clara cell secretory protein production by human airway epithelial cells
-
Cowan MJ, Huang X, Yao XL, Shelhamer JH. Tumor necrosis factor alpha stimulation of human Clara cell secretory protein production by human airway epithelial cells. Ann N Y Acad Sci 2000;923:193-201
-
(2000)
Ann N Y Acad Sci
, vol.923
, pp. 193-201
-
-
Cowan, M.J.1
Huang, X.2
Yao, X.L.3
Shelhamer, J.H.4
-
20
-
-
27744548897
-
TNF-alpha triggers mucus production in airway epithelium through an IKKbeta dependent mechanism
-
Lora JM, Zhang DM, Liao SM, Burwell T, King AM, Barker PA, Singh L, Keaveney M, Morgenstern J, Gutierrez-Ramos JC, Coyle AJ, Fraser CC. TNF-alpha triggers mucus production in airway epithelium through an IKKbeta dependent mechanism. J Biol Chem 2005;280(43):36510-17.
-
(2005)
J Biol Chem
, vol.280
, Issue.43
, pp. 36510-36517
-
-
Lora, J.M.1
Zhang, D.M.2
Liao, S.M.3
Burwell, T.4
King, A.M.5
Barker, P.A.6
Singh, L.7
Keaveney, M.8
Morgenstern, J.9
Gutierrez-Ramos, J.C.10
Coyle, A.J.11
Fraser, C.C.12
-
21
-
-
0035991525
-
The role of inflammation in the pathophysiology of CF lung disease
-
Chmiel JF, Berger M, Konstan MW. The role of inflammation in the pathophysiology of CF lung disease. Clin Rev Allergy Immunol 2002;23:5-27.
-
(2002)
Clin Rev Allergy Immunol
, vol.23
, pp. 5-27
-
-
Chmiel, J.F.1
Berger, M.2
Konstan, M.W.3
-
22
-
-
0035655177
-
Recurrent miscarriage and variant alleles of mannose binding lectin, tumour necrosis factor and lymphotoxin alpha genes
-
Baxter N, Sumiya M, Cheng S, Erlich H, Regan L, Simons A, Summerfield JA. Recurrent miscarriage and variant alleles of mannose binding lectin, tumour necrosis factor and lymphotoxin alpha genes. Clin Exp Immunol 2001;126:529-34.
-
(2001)
Clin Exp Immunol
, vol.126
, pp. 529-534
-
-
Baxter, N.1
Sumiya, M.2
Cheng, S.3
Erlich, H.4
Regan, L.5
Simons, A.6
Summerfield, J.A.7
-
23
-
-
0036092502
-
Development and evaluation of a PCR-based, line probe assay for the detection of 58 alleles in the cystic fibrosis transmembrane conductance regulator (CFTR) Gene
-
Wang X, Myers A, Saiki RK, Cutting GR. Development and evaluation of a PCR-based, line probe assay for the detection of 58 alleles in the cystic fibrosis transmembrane conductance regulator (CFTR) Gene. Clin Chem 2002;48:1121-3.
-
(2002)
Clin Chem
, vol.48
, pp. 1121-1123
-
-
Wang, X.1
Myers, A.2
Saiki, R.K.3
Cutting, G.R.4
-
25
-
-
8644255090
-
Impaired pulmonary status in cystic fibrosis adults with two mutated MBL-2 alleles
-
Davies JC, Turner MW, Klein N. Impaired pulmonary status in cystic fibrosis adults with two mutated MBL-2 alleles. Eur Respir J 2004;24:798-804.
-
(2004)
Eur Respir J
, vol.24
, pp. 798-804
-
-
Davies, J.C.1
Turner, M.W.2
Klein, N.3
-
26
-
-
0037115262
-
Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality
-
Mayer-Hamblett N, Rosenfeld M, Emerson J, Goss CH, Aitken ML. Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality. Am J Respir Crit Care Med 2002;166(12 Pt 1):1550-5.
-
(2002)
Am J Respir Crit Care Med
, vol.166
, Issue.12 PART 1
, pp. 1550-1555
-
-
Mayer-Hamblett, N.1
Rosenfeld, M.2
Emerson, J.3
Goss, C.H.4
Aitken, M.L.5
-
27
-
-
0034099699
-
Different transcriptional activity and in vitro TNF-alpha production in psoriasis patients carrying the TNF-alpha 238A promoter polymorphism
-
Kaluza W, Reuss E, Grossmann S, Hug R, Schopf RE, Galle PR, Maerker-Hermann E, Hoehler T. Different transcriptional activity and in vitro TNF-alpha production in psoriasis patients carrying the TNF-alpha 238A promoter polymorphism. J Invest Dermatol 2000;114:1180-3.
-
(2000)
J Invest Dermatol
, vol.114
, pp. 1180-1183
-
-
Kaluza, W.1
Reuss, E.2
Grossmann, S.3
Hug, R.4
Schopf, R.E.5
Galle, P.R.6
Maerker-Hermann, E.7
Hoehler, T.8
-
28
-
-
0028318464
-
Identification and characterization of a novel repressor site in the human tumor necrosis factor alpha gene
-
Fong CL, Siddiqui AH, Mark DF. Identification and characterization of a novel repressor site in the human tumor necrosis factor alpha gene. Nucleic Acids Res 1994;22:1108-14.
-
(1994)
Nucleic Acids Res
, vol.22
, pp. 1108-1114
-
-
Fong, C.L.1
Siddiqui, A.H.2
Mark, D.F.3
-
29
-
-
0032993434
-
A polymorphism that affects OCT-1 binding to the TNF promoter region is associated with severe malaria
-
Knight JC, Udalova I, Hill AV, Greenwood BM, Peshu N, Marsh K, Kwiatkowski D. A polymorphism that affects OCT-1 binding to the TNF promoter region is associated with severe malaria. Nat Genet 1999;22:145- 50.
-
(1999)
Nat Genet
, vol.22
, pp. 145-150
-
-
Knight, J.C.1
Udalova, I.2
Hill, A.V.3
Greenwood, B.M.4
Peshu, N.5
Marsh, K.6
Kwiatkowski, D.7
-
30
-
-
4944260975
-
Lung inflammation as a therapeutic target in cystic fibrosis
-
Koehler DR, Downey GP, Sweezey NB, Tanswell AK, Hu J. Lung inflammation as a therapeutic target in cystic fibrosis. Am J Respir Cell Mol Biol 2004;31:377-81.
-
(2004)
Am J Respir Cell Mol Biol
, vol.31
, pp. 377-381
-
-
Koehler, D.R.1
Downey, G.P.2
Sweezey, N.B.3
Tanswell, A.K.4
Hu, J.5
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