Over-expression of Microspan, a novel component of the sarcoplasmic reticulum, causes severe muscle pathology with triad abnormalities

Journal of Muscle Research and Cell Motility

Volumn 27, Issue 8, 2006, Pages 545-558

  Miller, Gaynor ^a   Peter, Angela K ^a   Espinoza, Erica ^a   Heighway, Jim ^b   Crosbie, Rachelle H ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF LIVERPOOL   (United Kingdom)

Author keywords

Dihydropyridine receptor; Dystrophin; Excitation contraction coupling; Microspan; Muscular dystrophy; Ryanodine receptor; Sarcoplasmic reticulum; Sarcospan; Tetraspanin; Transverse tubule; Triad

Indexed keywords

DYSTROPHIN; GLYCOPROTEIN; MEMBRANE PROTEIN; MUSCLE PROTEIN; PROTEIN MICROSPAN; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; HUMAN; HUMAN TISSUE; IMMUNOELECTRON MICROSCOPY; IMMUNOFLUORESCENCE; MOUSE; MUSCLE DISEASE; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DOMAIN; PROTEIN EXPRESSION; RNA SPLICING; RNA TRANSCRIPTION; SARCOPLASMIC RETICULUM; SKELETAL MUSCLE; TRANSVERSE TUBULAR SYSTEM;

3' UNTRANSLATED REGIONS; ALTERNATIVE SPLICING; AMINO ACID SEQUENCE; ANIMALS; CALCIUM CHANNELS, L-TYPE; CARRIER PROTEINS; CHROMOSOMES, HUMAN, PAIR 12; DYSTROPHIN; EXONS; FLUORESCENT ANTIBODY TECHNIQUE; GLYCOPROTEINS; HUMANS; INTRONS; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MODELS, BIOLOGICAL; MOLECULAR SEQUENCE DATA; MOLECULAR WEIGHT; MUSCLE CONTRACTION; MUSCLE, SKELETAL; NEOPLASM PROTEINS; PROTEIN ISOFORMS; PROTEIN STRUCTURE, SECONDARY; PROTEIN STRUCTURE, TERTIARY; RABBITS; RNA, MESSENGER; RYANODINE RECEPTOR CALCIUM RELEASE CHANNEL; SARCOPLASMIC RETICULUM; SARCOPLASMIC RETICULUM CALCIUM-TRANSPORTING ATPASES;

EID: 33750603606     PISSN: 01424319     EISSN: 15732657     Source Type: Journal    
DOI: 10.1007/s10974-006-9069-2     Document Type: Article

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