Impaired portal circulation resulting from L-arginine deficiency in patients with lysinuric protein intolerance [8]

Gut

Volumn 55, Issue 10, 2006, Pages 1526-1527

  Takeda, T ^a   Watanabe, H ^a   Saito, T ^a   Saito, K ^a   Takeda, H ^a   Togashi, H ^a   Fujii, J ^a   Takasago, Y ^b   Kawata, S ^a  

^a YAMAGATA UNIVERSITY   (Japan)

^b Morioka Red Cross Hospital   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ARGININE; LYSINE; NITRIC OXIDE;

ADOLESCENT; ADULT; AMINO ACID BLOOD LEVEL; AMINO ACID DEFICIENCY; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; GENE MUTATION; HUMAN; LETTER; MALE; PORTAL VEIN; PORTAL VEIN BLOOD FLOW; PRIORITY JOURNAL; PROTEIN INTOLERANCE; VEIN DIAMETER;

ADOLESCENT; ADULT; AGED; ARGININE; CHILD; FEMALE; HUMANS; LIVER CIRCULATION; MALE; MIDDLE AGED; MUCOPROTEINS; RENAL AMINOACIDURIAS;

EID: 33749187488     PISSN: 00175749     EISSN: None     Source Type: Journal    
DOI: 10.1136/gut.2005.086603     Document Type: Letter

References (10)

1. Simell O. Lysinuric protein intolerance and other aminocidurias. In: Scriver CR, Beaudet AL, Sly WS, et al, eds. The metabolic and molecular bases of inherited disease, vol 3, 7th edn. New York: McGraw-Hill, 1995:3603-27.
2. Sakuma I, Stuehr DJ, Gross SS, et al. Identification of arginine as a precursor of endothelium-derived relaxing factor. Proc Natl Acad Sci U S A 1988;85:8664-7.
3. Kilbourn RG, Belloni P. Endothelial cell production of nitrogen oxides in response to interferon γ in combination with tumor necrosis factor, inteleukin-1, and endotoxin. J Natl Cancer Inst 1990;82:772-6.
4. Palmer RMJ, Ferrige AG, Moncada S. Nitric oxide release accounts for the biological activity of endothelium-derived relaxing factor. Nature 1987;327:524-6.
5. Rubanyi GM, Romero JC, Vanhoutte PM. Flow-induced release of endothelium-derived relaxing factor. Am J Physiol 1986;250:H1145-9.
6. Kamada Y, Nogaretani H, Tamura S, et al. Vascular endothelial dysfunction resulting from L-arginine deficiency in a patients with lysinuric protein intolerance. J Clin Invest 2001;108:717-24.
7. Noguchi A, Shoji Y, Koizumi A, et al. SLC7A7 genomic structure and novel variants in three Japanese lysinuric protein intolerance families. Human Mutat 2000;15:357-72.
8. Koizumi A, Shoji Y, Nozaki J, et al. A cluster of lysinuric protein intolerance (LPI) patients in a northern part of Iwate, Japan due to a founder effect. Human Mutat 2000;16:270-1.
9. Taourel P, Blanc P, Dauzat M, et al. Doppler study of mesenteric, hepatic, and portal measurements and the severity of portal hypertension and hepatic failure. Hepatology 1998;28:932-6.
10. Piscaglia F, Zironi G, Gaiani S, et al. Systemic and splanchnic hemodynamic changes after liver transplantation for cirrhosis: A long-term prospective study. Hepatology 1999;30:58-64.