MM2-thalamic-type sporadic Creutzfeldt-Jakob disease with widespread neocortical pathology

Acta Neuropathologica

Volumn 112, Issue 4, 2006, Pages 503-511

  Hirose, Kazunori ^a   Iwasaki, Yasushi ^b   Izumi, Masayuki ^a   Yoshida, Mari ^c   Hashizume, Yoshio ^c   Kitamoto, Tetsuyuki ^d   Sahashi, Ko ^a  

^a AICHI MEDICAL UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^c AICHI MEDICAL UNIVERSITY   (Japan)

^d TOHOKU UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Cerebral neocortical pathology; MM2 thalamic type; Prion protein deposition; Sporadic Creutzfeldt Jakob disease; Sporadic fatal insomnia

Indexed keywords

ANTIBIOTIC AGENT; ANTIDEPRESSANT AGENT; METHIONINE; NEURON SPECIFIC ENOLASE; PRION PROTEIN; PROTEIN S100B; TAU PROTEIN;

ABNORMAL BEHAVIOR; ADULT; ANOREXIA; ARTICLE; ASTROCYTOSIS; AUTOPSY; BASAL GANGLION; BRADYKINESIA; BRAIN ATROPHY; BRAIN CORTEX; BRAIN STEM; BRONCHOPNEUMONIA; CASE REPORT; CEREBELLUM CORTEX; CREUTZFELDT JAKOB DISEASE; DEPRESSION; DIFFERENTIAL DIAGNOSIS; DIFFUSION WEIGHTED IMAGING; DISEASE COURSE; DISEASE DURATION; DISEASE SEVERITY; DYSAUTONOMIA; FATALITY; GAZE PARALYSIS; GENETIC ANALYSIS; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; HYPERHIDROSIS; IMMUNOHISTOCHEMISTRY; INFERIOR OLIVE; INSOMNIA; JAPAN; LIPODYSTROPHY; MALE; MENTAL DETERIORATION; NERVE DEGENERATION; NEUROLOGIC EXAMINATION; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PONS ANGLE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN CEREBROSPINAL FLUID LEVEL; PSEUDOBULBAR PALSY; PURKINJE CELL; RESTLESSNESS; SPINAL CORD; SUBSTANTIA NIGRA; SYMPTOMATOLOGY; TEGMENTUM; THALAMUS NUCLEUS; VISUAL HALLUCINATION; WESTERN BLOTTING;

ADULT; BLOTTING, WESTERN; CREUTZFELDT-JAKOB SYNDROME; GLIOSIS; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; NEOCORTEX; NEUROLOGIC EXAMINATION; PRPSC PROTEINS; THALAMUS;

EID: 33749133871     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-006-0131-3     Document Type: Article

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