Sporadic fatal insomnia with spongiform degeneration in the thalamus and widespread PrPSc deposits in the brain

Neuropathology

Volumn 25, Issue 2, 2005, Pages 144-149

  Piao, Yue Shan ^a,d   Kakita, Akiyoshi ^a   Watanabe, Hiroyuki ^b   Kitamoto, Tetsuyuki ^c   Takahashi, Hitoshi ^a  

^a NIIGATA UNIVERSITY   (Japan)

^b Tachikawa General Hospital   (Japan)

^c TOHOKU UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^d CAPITAL MEDICAL UNIVERSITY   (China)

Author keywords

Creutzfeldt Jakob disease; Fatal insomnia; PRNP; PRPsc; Thalamic degeneration

Indexed keywords

AMYLOID; METHIONINE; PRION PROTEIN;

AGED; ARTICLE; BASAL GANGLION; BRAIN ATROPHY; BRAIN CORTEX; BRAIN REGION; BRAIN SPONGIOSIS; BRAIN STEM; CASE REPORT; CELL ULTRASTRUCTURE; CEREBELLUM CORTEX; CLINICAL FEATURE; CODON; CORPUS STRIATUM; DEMENTIA; DISEASE COURSE; GENE MUTATION; GENETIC ANALYSIS; GLIOSIS; HISTOPATHOLOGY; HOMOZYGOSITY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; INFERIOR OLIVE; INSOMNIA; MALE; NERVE CELL LESION; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PRION DISEASE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PURKINJE CELL; SOMNOLENCE; SPORADIC FATAL INSOMNIA; THALAMUS;

AGED; BRAIN; CREUTZFELDT-JAKOB SYNDROME; DIAGNOSIS, DIFFERENTIAL; HUMANS; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; INSOMNIA, FATAL FAMILIAL; MAGNETIC RESONANCE IMAGING; MALE; PRPSC PROTEINS; THALAMUS;

EID: 17644403505     PISSN: 09196544     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1440-1789.2005.00608.x     Document Type: Article

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