Cortical visual function in the rd12 mouse model of Leber Congenital Amarousis (LCA) after gene replacement therapy to restore retinal function

Vision Research

Volumn 46, Issue 22, 2006, Pages 3926-3934

  Nusinowitz, S ^a   Ridder III, W H ^b   Pang, J J ^c   Chang, B ^d   Noorwez, S M ^c   Kaushal, S ^c   Hauswirth, W W ^c   Heckenlively, J R ^e  

^a JULES STEIN EYE INSTITUTE   (United States)

^b SOUTHERN CALIFORNIA COLLEGE OF OPTOMETRY   (United States)

^c UNIVERSITY OF FLORIDA   (United States)

^d JACKSON LABORATORY   (United States)

^e UNIVERSITY OF MICHIGAN   (United States)

Author keywords

Cortical visual function; Electroretinography; Gene replacement therapy; LCA; Leber's Congenital Amarousis; Mouse; Temporal frequency; Visual evoked potential

Indexed keywords

COMPLEMENTARY DNA; PARVOVIRUS VECTOR;

AGE; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; ELECTRORETINOGRAPHY; EVOKED VISUAL RESPONSE; EXPERIMENTAL MOUSE; FREQUENCY MODULATION; GENE; GENE REPLACEMENT THERAPY; HUMAN; LEBER CONGENITAL AMAUROSIS; LUMINANCE; MOUSE; NONHUMAN; PERINATAL PERIOD; PRIORITY JOURNAL; RD12 MOUSE; RETINA; RPE65 GENE; VIRAL GENE THERAPY; VISION; VISUAL CORTEX; VISUAL STIMULATION;

ANIMALS; BLINDNESS; DARK ADAPTATION; DISEASE MODELS, ANIMAL; ELECTRORETINOGRAPHY; EVOKED POTENTIALS, VISUAL; GENE THERAPY; MICE; MICE, MUTANT STRAINS; RETINA; RHODOPSIN; TIME FACTORS; VISION TESTS; VISUAL ACUITY; VISUAL CORTEX;

EID: 33748537392     PISSN: 00426989     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.visres.2006.05.010     Document Type: Article

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