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Volumn 155, Issue 2, 2006, Pages 224-230

A chemically-induced acute model of maple syrup urine disease in rats for neurochemical studies

Author keywords

Acute animal model; Branched chain amino acids; Maple syrup urine disease; Rats

Indexed keywords

ALANINE; BRANCHED CHAIN AMINO ACID; HISTIDINE; ISOLEUCINE; LEUCINE; LYSINE; METHIONINE; ORNITHINE; PHENYLALANINE; TYROSINE; VALINE;

EID: 33747204835     PISSN: 01650270     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jneumeth.2006.01.005     Document Type: Article
Times cited : (28)

References (26)
  • 2
    • 0042122354 scopus 로고    scopus 로고
    • Induction of oxidative stress in rat brain by the metabolite accumulating in maple syrup urine disease
    • Bridi R., Araldi J., Sgarbi M.B., Testa C.G., Durigon K., Wajner M., et al. Induction of oxidative stress in rat brain by the metabolite accumulating in maple syrup urine disease. Int J Dev Neurosci 21 (2003) 327-332
    • (2003) Int J Dev Neurosci , vol.21 , pp. 327-332
    • Bridi, R.1    Araldi, J.2    Sgarbi, M.B.3    Testa, C.G.4    Durigon, K.5    Wajner, M.6
  • 3
    • 14644442394 scopus 로고    scopus 로고
    • Evaluation of the mechanisms involved in leucine-induced oxidative damage in cerebral cortex of young rats
    • Bridi R., Latini A., Braum C.A., Zorzi G.K., Wajner M., Lissi E., et al. Evaluation of the mechanisms involved in leucine-induced oxidative damage in cerebral cortex of young rats. Free Radic Res 31 9 (2005) 71-79
    • (2005) Free Radic Res , vol.31 , Issue.9 , pp. 71-79
    • Bridi, R.1    Latini, A.2    Braum, C.A.3    Zorzi, G.K.4    Wajner, M.5    Lissi, E.6
  • 4
    • 0002977005 scopus 로고    scopus 로고
    • Maple syrup urine disease (branched-chain ketoaciduria)
    • Scriver C.R., Beaudet A.L., Sly W.S., and Valle D. (Eds), McGraw-Hill, New York
    • Chuang D.T., and Shih V.E. Maple syrup urine disease (branched-chain ketoaciduria). In: Scriver C.R., Beaudet A.L., Sly W.S., and Valle D. (Eds). The metabolic and molecular bases of inherited disease (2001), McGraw-Hill, New York 1971-2005
    • (2001) The metabolic and molecular bases of inherited disease , pp. 1971-2005
    • Chuang, D.T.1    Shih, V.E.2
  • 5
    • 0000299656 scopus 로고
    • Disorders of branched chain amino acid and keto acid metabolism
    • Scriver C.R., Beaudet A.L., Sly W.L., and Valle D. (Eds), McGraw-Hill, New York
    • Danner D.J., and Elsas II L.J. Disorders of branched chain amino acid and keto acid metabolism. In: Scriver C.R., Beaudet A.L., Sly W.L., and Valle D. (Eds). The metabolic basis of inherited disease (1989), McGraw-Hill, New York 671-692
    • (1989) The metabolic basis of inherited disease , pp. 671-692
    • Danner, D.J.1    Elsas II, L.J.2
  • 6
    • 0026660006 scopus 로고
    • Glutamate and γ-aminobutyric acid neurotransmitter systems in the acute phase of maple syrup urine disease and citrullinemia encephalopathies in newborn calves
    • Dodd P.R., Wiliams A.L., Gundlach A.L., Harper P.A.W., Healy P.J., Dennis J.A., et al. Glutamate and γ-aminobutyric acid neurotransmitter systems in the acute phase of maple syrup urine disease and citrullinemia encephalopathies in newborn calves. J Neurochem 59 (1992) 582-590
    • (1992) J Neurochem , vol.59 , pp. 582-590
    • Dodd, P.R.1    Wiliams, A.L.2    Gundlach, A.L.3    Harper, P.A.W.4    Healy, P.J.5    Dennis, J.A.6
  • 7
    • 20344386484 scopus 로고    scopus 로고
    • Branched-chain amino acids and brain function
    • Fernstron J.D. Branched-chain amino acids and brain function. J Nutr 135 (2005) 1539S-1546S
    • (2005) J Nutr , vol.135
    • Fernstron, J.D.1
  • 8
    • 0036186148 scopus 로고    scopus 로고
    • Stimulation of lipid peroxidation in vitro in rat brain by metabolites accumulating in maple syrup urine disease
    • Fontella F.U., Gassen E., Pulrolnik V., Wannmacher C.M.D., Klein A.B., Wajner M., et al. Stimulation of lipid peroxidation in vitro in rat brain by metabolites accumulating in maple syrup urine disease. Metab Brain Dis 17 (2002) 47-54
    • (2002) Metab Brain Dis , vol.17 , pp. 47-54
    • Fontella, F.U.1    Gassen, E.2    Pulrolnik, V.3    Wannmacher, C.M.D.4    Klein, A.B.5    Wajner, M.6
  • 9
    • 0016259467 scopus 로고
    • Inhibition of mitochondrial pyruvate transport by phenylpyruvate and α-ketoisocaproate
    • Halestrap A.P., Brand M.D., and Denton R.M. Inhibition of mitochondrial pyruvate transport by phenylpyruvate and α-ketoisocaproate. Biochem Biophys Acta 367 (1974) 102-108
    • (1974) Biochem Biophys Acta , vol.367 , pp. 102-108
    • Halestrap, A.P.1    Brand, M.D.2    Denton, R.M.3
  • 10
    • 0023052779 scopus 로고
    • Maple syrup urine disease as a cause of spongiform encephalopathy in calves
    • Harper P.A., Healy P.J., and Dennis J.A. Maple syrup urine disease as a cause of spongiform encephalopathy in calves. Vet Rec 119 (1986) 62-65
    • (1986) Vet Rec , vol.119 , pp. 62-65
    • Harper, P.A.1    Healy, P.J.2    Dennis, J.A.3
  • 11
    • 0002762662 scopus 로고
    • Amino acids and small peptides
    • Lim C.K. (Ed), IRL Press, Oxford
    • Joseph M.H., and Marsden C.A. Amino acids and small peptides. In: Lim C.K. (Ed). HPLC of small peptides (1986), IRL Press, Oxford 13-27
    • (1986) HPLC of small peptides , pp. 13-27
    • Joseph, M.H.1    Marsden, C.A.2
  • 12
    • 0034108632 scopus 로고    scopus 로고
    • Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane despolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease
    • Jouvet P., Rustin P., Taylor D.L., Pocock J.M., Felderhoff-Mueser U., Mazarakis N.D.C., et al. Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane despolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease. Mol Biol Cell 11 (2000) 1919-1932
    • (2000) Mol Biol Cell , vol.11 , pp. 1919-1932
    • Jouvet, P.1    Rustin, P.2    Taylor, D.L.3    Pocock, J.M.4    Felderhoff-Mueser, U.5    Mazarakis, N.D.C.6
  • 13
    • 0017258183 scopus 로고
    • Control of pyruvate and β-hydroxybutyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease
    • Land J.M., Mowbray J., and Clark J.B. Control of pyruvate and β-hydroxybutyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease. J Neurochem 26 (1976) 823-830
    • (1976) J Neurochem , vol.26 , pp. 823-830
    • Land, J.M.1    Mowbray, J.2    Clark, J.B.3
  • 16
    • 14644402200 scopus 로고
    • Maple syrup urine disease: branched-chain ketoaciduria
    • Nyhan W.L. (Ed), Appleton-Century-Crofts, Norwalk
    • Nyhan W.L. Maple syrup urine disease: branched-chain ketoaciduria. In: Nyhan W.L. (Ed). Abnormalities in amino acid metabolism in clinical medicine (1984), Appleton-Century-Crofts, Norwalk 21-35
    • (1984) Abnormalities in amino acid metabolism in clinical medicine , pp. 21-35
    • Nyhan, W.L.1
  • 17
    • 0037403984 scopus 로고    scopus 로고
    • Kinetic studies on the inhibition of creatine kinase activity by branched-chain alpha-amino acids in the brain cortex of rats
    • Pilla C., Cardozo R.F., Dornelles P.K., Dutra-Filho C.S., Wyse A.T., Wajner M., et al. Kinetic studies on the inhibition of creatine kinase activity by branched-chain alpha-amino acids in the brain cortex of rats. Int J Dev Neurosci 21 (2003) 145-151
    • (2003) Int J Dev Neurosci , vol.21 , pp. 145-151
    • Pilla, C.1    Cardozo, R.F.2    Dornelles, P.K.3    Dutra-Filho, C.S.4    Wyse, A.T.5    Wajner, M.6
  • 19
    • 0014039598 scopus 로고
    • Changes in the amino acid composition of proteolipids of white matter during maturation of the human nervous system
    • Prensky A.L., and Moser H.W. Changes in the amino acid composition of proteolipids of white matter during maturation of the human nervous system. J Neurochem 14 (1967) 117-121
    • (1967) J Neurochem , vol.14 , pp. 117-121
    • Prensky, A.L.1    Moser, H.W.2
  • 20
    • 0001760204 scopus 로고
    • Maple syrup urine disease with particular reference to diet therapy
    • Snyderman S.E., Norton P.M., and Roitman E. Maple syrup urine disease with particular reference to diet therapy. Pediatrics 34 (1964) 454-472
    • (1964) Pediatrics , vol.34 , pp. 454-472
    • Snyderman, S.E.1    Norton, P.M.2    Roitman, E.3
  • 21
    • 0034547976 scopus 로고    scopus 로고
    • Inhibition of glutamate uptake into synaptic vesicles of rat brain by the metabolites accumulating in maple syrup urine disease
    • Tavares R.G., Santos C.E.S., Tasca C., Wajner M., Souza D.O., and Dutra-Filho C.S. Inhibition of glutamate uptake into synaptic vesicles of rat brain by the metabolites accumulating in maple syrup urine disease. J Neurol Sci 181 (2000) 44-49
    • (2000) J Neurol Sci , vol.181 , pp. 44-49
    • Tavares, R.G.1    Santos, C.E.S.2    Tasca, C.3    Wajner, M.4    Souza, D.O.5    Dutra-Filho, C.S.6
  • 22
    • 0033913801 scopus 로고    scopus 로고
    • Reduction of large neutral amino acid concentrations in plasma and CSF of patients with maple syrup urine disease during crises
    • Wajner M., Coelho D.M., Barschak A.G., Araujo P.R., Pires R.F., Lulhier F.L., et al. Reduction of large neutral amino acid concentrations in plasma and CSF of patients with maple syrup urine disease during crises. J Inherit Metab Dis 23 (2000) 505-512
    • (2000) J Inherit Metab Dis , vol.23 , pp. 505-512
    • Wajner, M.1    Coelho, D.M.2    Barschak, A.G.3    Araujo, P.R.4    Pires, R.F.5    Lulhier, F.L.6
  • 23
    • 0032989964 scopus 로고    scopus 로고
    • Reduction of plasma concentrations of large neutral amino acids in patients with maple syrup urine disease during crises
    • Wajner M., and Vargas C.R. Reduction of plasma concentrations of large neutral amino acids in patients with maple syrup urine disease during crises. Arch Dis Child 80 (1999) 579
    • (1999) Arch Dis Child , vol.80 , pp. 579
    • Wajner, M.1    Vargas, C.R.2
  • 24
    • 85047690932 scopus 로고    scopus 로고
    • ENU mutagenesis identifies mice with mitochondrial branched-chain aminotransferase deficiency resembling human maple syrup urine disease
    • Wu J.Y., Kao H.J., Li S.C., Stevens R., Hillman S., Millington D., et al. ENU mutagenesis identifies mice with mitochondrial branched-chain aminotransferase deficiency resembling human maple syrup urine disease. J Clin Invest 113 (2004) 434-440
    • (2004) J Clin Invest , vol.113 , pp. 434-440
    • Wu, J.Y.1    Kao, H.J.2    Li, S.C.3    Stevens, R.4    Hillman, S.5    Millington, D.6
  • 25
    • 0028006431 scopus 로고
    • Interrelationships of leucine and glutamate metabolism in cultured astrocyts
    • Yudkoff M., Daikhin Y., Lin Z.P., Nissim I., Stern J., Pleasure D., et al. Interrelationships of leucine and glutamate metabolism in cultured astrocyts. J Neurochem 62 (1994) 1192-1202
    • (1994) J Neurochem , vol.62 , pp. 1192-1202
    • Yudkoff, M.1    Daikhin, Y.2    Lin, Z.P.3    Nissim, I.4    Stern, J.5    Pleasure, D.6
  • 26
    • 0036160407 scopus 로고    scopus 로고
    • Large neutral amino acids auto exchange when infused by microdialysis into the rat brain: implications for maple syrup urine disease and phenylketonuria
    • Zielke H.R., Zielke C.L., Baab P.J., and Collins R.M. Large neutral amino acids auto exchange when infused by microdialysis into the rat brain: implications for maple syrup urine disease and phenylketonuria. Neurochem Int 40 (2002) 347-354
    • (2002) Neurochem Int , vol.40 , pp. 347-354
    • Zielke, H.R.1    Zielke, C.L.2    Baab, P.J.3    Collins, R.M.4


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.