Human protoporphyria: Reduced cutaneous photosensitivity and lower erythrocyte porphyrin levels during pregnancy

Journal of the American Academy of Dermatology

Volumn 36, Issue 1, 1997, Pages 40-43

  Poh Fitzpatrick, M B ^a  

^a ST LUKE S ROOSEVELT HOSPITAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BETA CAROTENE; PORPHYRIN;

ARTICLE; CLINICAL ARTICLE; ERYTHROCYTE LEVEL; ERYTHROPOIETIC PROTOPORPHYRIA; FEMALE; HUMAN; HUMAN CELL; HUMAN TISSUE; LIGHT EXPOSURE; PHOTOSENSITIVITY DISORDER; PORPHYRIN METABOLISM; PREGNANCY COMPLICATION; PRIORITY JOURNAL; SEASONAL VARIATION;

EID: 0031029499     PISSN: 01909622     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0190-9622(97)70323-2     Document Type: Article

References (12)

1. S Piomelli AA Lamola MB Poh-Fitzpatrick Erythropoietic protoporphyria and Pb intoxication: the molecular basis for difference in cutaneous photosensitivity. I. Different rates of diffusion from the erythrocytes, both in vivo and in vitro J Clin Invest 56 1975 1519 1527
2. H Schmidt G Snitker K Thomsen Erythropoietic protoporphyria: a clinical study based on 29 cases in 14 families Arch Dermatol 110 1974 58 64
3. LN Went EC Klasen Genetic aspects of erythropoietic protoporphyria Ann Hum Genet 48 1984 105 117
4. S Piomelli A micromethod for free erythrocyte porphyrins: the FEP test J Lab Clin Med 81 1973 932 940
5. LL Maio MM Mathews-Roth MB Poh-Fitzpatrick Beta-carotene treatment and erythrocyte protoporphyrin levels [letter] Arch Dermatol 115 1979 818
6. BA Brown Hematology principles and procedures 6th ed 1993 Lea & Febiger Philadelphia 108
7. RC Haining ML Cowger RF Labbe Erythropoietic porphyria II. The effects of induced polycythemia Blood 36 1970 297 309
8. A Dobozy M Csato C Siklosi Transfusion therapy for erythropoietic protoporphyria Br J Dermatol 109 1983 571 576
9. S Piomelli MB Poh-Fitzpatrick C Seaman Complete suppression of the symptoms of congenital erythropoietic porphyria by long-term treatment with high-level transfusions N Engl J Med 314 1986 1029 1031
10. L Guarini MB Poh-Fitzpatrick D Carriero Congenital erythropoietic porphyria (CEP): suppression of erythropoiesis by treatment with hydroxyurea (HU) Blood 80 suppl 1 1992 285a
11. R Huch A Huch Erythropoietin in obstetrics Hematol Oncol Clin North Am 8 1994 1021 1040
12. E Letsky The haematological system F Hytten G Chamberlain Clinical physiology in obstetrics 1980 Blackwell Scientific Publications Oxford 44 78