Inborn errors of metabolism with a protein-restricted diet: Effect on polyunsaturated fatty acids

Journal of Inherited Metabolic Disease

Volumn 20, Issue 6, 1997, Pages 783-789

  Sanjurjo, P ^a,b   Ruiz, J I ^a   Montejo, M ^a  

^a UNIVERSITY OF THE BASQUE COUNTRY UPV EHU   (Spain)

^b HOSPITAL DE CRUCES   (Spain)

Author keywords

[No Author keywords available]

Indexed keywords

ARACHIDONIC ACID; DOCOSAHEXAENOIC ACID; FATTY ACID; PHOSPHOLIPID; POLYUNSATURATED FATTY ACID;

ADOLESCENT; ARTICLE; CHILD; CLINICAL ARTICLE; DIET SUPPLEMENTATION; DIET THERAPY; ERYTHROCYTE LEVEL; FATTY ACID BLOOD LEVEL; HUMAN; INBORN ERROR OF METABOLISM; INFANT; LIPID COMPOSITION; NUTRITION; PHENYLKETONURIA; PROTEIN RESTRICTION; PSYCHOMOTOR DEVELOPMENT; UREA CYCLE;

ALPHA-LINOLENIC ACID; AMINO ACID METABOLISM, INBORN ERRORS; ARACHIDONIC ACID; CHILD; CHILD, PRESCHOOL; CITRULLINE; DIET, PROTEIN-RESTRICTED; DOCOSAHEXAENOIC ACIDS; FATTY ACIDS, MONOUNSATURATED; FATTY ACIDS, UNSATURATED; HUMANS; INFANT; INFANT, NEWBORN; LINOLEIC ACID; METABOLISM, INBORN ERRORS; METHYLMALONIC ACID; MYRISTIC ACID; ORNITHINE CARBAMOYLTRANSFERASE; PHOSPHOLIPIDS;

EID: 0030727790     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005367701176     Document Type: Article

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