Measurement of the energy-generating capacity of human muscle mitochondria: Diagnostic procedure and application to human pathology

Clinical Chemistry

Volumn 52, Issue 5, 2006, Pages 860-871

  Janssen, Antoon J M ^a   Trijbels, Frans J M ^a   Sengers, Rob C A ^a   Wintjes, Liesbeth T M ^a   Ruitenbeek, Wim ^a   Smeitink, Jan A M ^a   Morava, Eva ^a   Van Engelen, Baziel G M ^a   Van Den Heuvel, Lambert P ^a   Rodenburg, Richard J T ^a  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYL COENZYME A; ADENINE NUCLEOTIDE TRANSLOCASE; ADENOSINE TRIPHOSPHATE; CARBONYL CYANIDE CHLOROPHENYLHYDRAZONE; CARNITINE; MALIC ACID; PYRUVATE DEHYDROGENASE COMPLEX; PYRUVIC ACID; SUCCINIC ACID;

ADOLESCENT; ADULT; ANALYTIC METHOD; ARTICLE; CHILD; CITRIC ACID CYCLE; CLINICAL ARTICLE; COMPLEX FORMATION; CONTROLLED STUDY; DIAGNOSTIC TEST; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENERGY METABOLISM; ENZYME DEFICIENCY; ENZYME SPECIFICITY; FEMALE; HIGH RISK PATIENT; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INFANT; MALE; MEASUREMENT; MUSCLE BIOPSY; MUSCLE MITOCHONDRION; OXIDATIVE PHOSPHORYLATION; SAMPLING;

ADENOSINE TRIPHOSPHATE; ADOLESCENT; ADULT; BIOPSY; CARBON RADIOISOTOPES; CARNITINE; CHILD; CHILD, PRESCHOOL; ENERGY METABOLISM; FEMALE; HUMANS; MALATES; MALE; MALONATES; MITOCHONDRIA; MITOCHONDRIAL ADP, ATP TRANSLOCASES; MITOCHONDRIAL DISEASES; MUSCLE, SKELETAL; OXIDATION-REDUCTION; OXIDATIVE PHOSPHORYLATION; PYRUVATE DEHYDROGENASE COMPLEX; PYRUVIC ACID; SUCCINIC ACID;

EID: 33646347898     PISSN: 00099147     EISSN: None     Source Type: Journal    
DOI: 10.1373/clinchem.2005.062414     Document Type: Article

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