CSPα-deficiency causes massive and rapid photoreceptor degeneration

Proceedings of the National Academy of Sciences of the United States of America

Volumn 103, Issue 8, 2006, Pages 2926-2931

  Schmitz, Frank ^a,b   Tabares, Lucia ^c   Khimich, Darina ^d   Strenzke, Nicola ^d   De La Villa Polo, Pedro ^e   Castellano Muñoz, Manuel ^c   Bulankina, Anna ^d   Moser, Tobias ^d   Fernández Chacón, Rafael ^c   Südhof, Thomas C ^b  

^a SAARLAND UNIVERSITY   (Germany)

^b UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^c UNIVERSITY OF SEVILLE   (Spain)

^d UNIVERSITY OF GÖTTINGEN   (Germany)

^e UNIVERSITY OF ALCALÁ   (Spain)

Author keywords

Blindness; Chaperone; Electroretinogram; Hair cell; Ribbon synapse

Indexed keywords

CHAPERONE; CYSTEINE STRING PROTEIN; CYSTEINE STRING PROTEIN ALPHA; DNA; DNA J PROTEIN; HEAT SHOCK PROTEIN 40; UNCLASSIFIED DRUG; CARRIER PROTEIN; MEMBRANE PROTEIN; NERVE PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BLINDNESS; CELL SUBPOPULATION; CONTROLLED STUDY; GENE DELETION; HAIR CELL; MOUSE; NERVE DEGENERATION; NEUROPROTECTION; NONHUMAN; PHENOTYPE; PHOTORECEPTOR; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN DEGRADATION; PROTEIN DOMAIN; RETINA CELL; SYNAPSE VESICLE; ANIMAL; CYTOLOGY; DEGENERATIVE DISEASE; GENETICS; METABOLISM; MOUSE MUTANT; PATHOLOGY; PHYSIOLOGY; RETINA; SYNAPSE; ULTRASTRUCTURE;

ANIMALIA;

ANIMALS; BLINDNESS; CARRIER PROTEINS; HAIR CELLS, INNER; HSP40 HEAT-SHOCK PROTEINS; MEMBRANE PROTEINS; MICE; MICE, KNOCKOUT; NERVE TISSUE PROTEINS; NEURODEGENERATIVE DISEASES; PHOTORECEPTORS, VERTEBRATE; RETINA; SYNAPSES;

EID: 33644552728     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0510060103     Document Type: Article

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