Use of an arginine-restricted diet to slow progression of visual loss in patients with gyrate atrophy

Archives of Ophthalmology

Volumn 122, Issue 7, 2004, Pages 982-984

  Kaiser Kupfer, Muriel I ^a,c   Caruso, Rafael C ^a   Valle, David ^b   Reed, George F ^a  

^a NATIONAL EYE INSTITUTE   (United States)

^b JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c NONE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ARGININE; ORNITHINE;

ADULT; AGED; ARTICLE; CHOROID; CLINICAL ARTICLE; CLINICAL OBSERVATION; DIET RESTRICTION; ELECTRORETINOGRAPHY; FEMALE; FOLLOW UP; FUNCTIONAL ASSESSMENT; HUMAN; LONG TERM CARE; MALE; OUTCOMES RESEARCH; PERIMETRY; PRIORITY JOURNAL; QUANTITATIVE DIAGNOSIS; RETINA GYRATE ATROPHY; STATISTICAL SIGNIFICANCE; VISION; VISUAL FIELD; VISUAL IMPAIRMENT; ADOLESCENT; BLOOD; CHILD; DIET THERAPY; DISEASE COURSE; MIDDLE AGED; PATHOPHYSIOLOGY; PATIENT COMPLIANCE; PHYSIOLOGY; PROTEIN RESTRICTION; RETINA; VISUAL DISORDER;

ADOLESCENT; ADULT; AGED; ARGININE; CHILD; DIET, PROTEIN-RESTRICTED; DISEASE PROGRESSION; ELECTRORETINOGRAPHY; FEMALE; FOLLOW-UP STUDIES; GYRATE ATROPHY; HUMANS; MALE; MIDDLE AGED; ORNITHINE; PATIENT COMPLIANCE; PERIMETRY; RETINA; VISION DISORDERS; VISUAL FIELDS;

EID: 3342990125     PISSN: 00039950     EISSN: None     Source Type: Journal    
DOI: 10.1001/archopht.122.7.982     Document Type: Article

References (4)

1. Kaiser-Kupfer MI, Caruso RC, Valle D. Gyrate atrophy of the choroid and retina: long-term reduction of ornithine slows retinal degeneration. Arch Ophthalmol. 1991;109:1539-1548.
2. Kaiser-Kupfer MI, Caruso RC, Valle D. Gyrate atrophy of the choroid and retina: further experience with long-term reduction of ornithine levels in children. Arch Ophthalmol. 2002:120:146-153.
3. Caruso RC, Nussenblatt RB, Csaky KG, Valle D, Kaiser-Kupfer MI. Assessment of visual function in patients with gyrate atrophy who are considered candidates for gene replacement. Arch Ophthalmol. 2001;119:667-669.
4. Wang T, Steel G, Milam AH, Valle D. Correction of ornithine accumulation prevents retinal degeneration in a mouse model of gyrate atrophy of the choroid and retina. Proc Natl Acad Sci U S A. 2000;97:1224-1229.