Correction of ornithine accumulation prevents retinal degeneration in a mouse model of gyrate atrophy of the choroid and retina

Proceedings of the National Academy of Sciences of the United States of America

Volumn 97, Issue 3, 2000, Pages 1224-1229

  Wang, Tao ^a   Steel, Gary ^a   Milam, Ann H ^b   Valle, David ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; ARGININE; ORNITHINE; ORNITHINE OXOACID AMINOTRANSFERASE;

AMINO ACID BLOOD LEVEL; ANIMAL MODEL; ARTICLE; CHOROID GYRATE ATROPHY; CONTROLLED STUDY; DIET RESTRICTION; ELECTRORETINOGRAM; ENZYME DEFICIENCY; GENE TARGETING; MALE; MOUSE; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RETINA DEGENERATION; RETINA GYRATE ATROPHY;

AMINO ACIDS; ANIMALS; ARGININE; CHOROID; DISEASE MODELS, ANIMAL; ELECTRORETINOGRAPHY; GYRATE ATROPHY; MICE; MICE, KNOCKOUT; ORNITHINE; ORNITHINE-OXO-ACID TRANSAMINASE; RETINA; RETINAL DEGENERATION;

ANIMALIA;

EID: 0033950654     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.97.3.1224     Document Type: Article

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