Structure, stability and interactions of type I collagen with GLY349-CYS substitution in α1(I) chain in a murine Osteogenesis Imperfecta model

Matrix Biology

Volumn 23, Issue 2, 2004, Pages 101-112

  Kuznetsova, Natalia V ^a   Forlino, Antonella ^a,b   Cabral, Wayne A ^a   Marini, Joan C ^a   Leikin, Sergey ^a  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

^b UNIVERSITY OF PAVIA   (Italy)

Author keywords

Collagen collagen interactions; Osteogenesis Imperfecta; Thermal stability

Indexed keywords

COLLAGEN TYPE 1;

AMINO ACID SUBSTITUTION; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CELL FUNCTION; CROSS LINKING; MOLECULAR RECOGNITION; MOUSE; NONHUMAN; OSTEOBLAST; OSTEOGENESIS IMPERFECTA; PHENOTYPIC VARIATION; PRIORITY JOURNAL; PROTEIN DENATURATION; PROTEIN INTERACTION; PROTEIN STABILITY; PROTEIN STRUCTURE; THERMOSTABILITY;

AMINO ACID SUBSTITUTION; ANIMALS; COLLAGEN TYPE I; CYSTEINE; DISEASE MODELS, ANIMAL; ENZYME STABILITY; EXTRACELLULAR MATRIX; FIBROBLASTS; GLYCINE; MICE; OSTEOGENESIS IMPERFECTA; PROTEIN BINDING; PROTEIN CONFORMATION; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN STRUCTURE, QUATERNARY; TAIL; TENDONS; THERMODYNAMICS;

ANIMALIA; MURINAE;

EID: 3042797594     PISSN: 0945053X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.matbio.2004.03.002     Document Type: Article

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