Pulmonary hypertension developing after alglucerase therapy in two patients with type 1 gaucher disease complicated by the hepatopulmonary syndrome

Annals of Internal Medicine

Volumn 125, Issue 11, 1996, Pages 901-904

  Dawson, Arthur ^a   Elias, Darlene J ^a   Rubenson, David ^a   Bartz, Stephen H ^a   Garver, Paul R ^a   Kay, Andrea C ^a   Bloor, Colin M ^a   Beutler, Ernest ^a  

^a NONE

Author keywords

[No Author keywords available]

Indexed keywords

ALGLUCERASE;

ADULT; ARTICLE; CASE REPORT; CLINICAL FEATURE; CYANOSIS; DYSPNEA; ECHOCARDIOGRAPHY; GAUCHER DISEASE; HEPATOPULMONARY SYNDROME; HUMAN; LUNG BIOPSY; LUNG LAVAGE; MALE; PRIORITY JOURNAL; PULMONARY HYPERTENSION; THORAX RADIOGRAPHY;

ADULT; ANOXEMIA; DILATATION, PATHOLOGIC; FEMALE; GAUCHER DISEASE; GLUCOSYLCERAMIDASE; HEPATOMEGALY; HUMANS; HYPERTENSION, PULMONARY; MALE; PULMONARY ARTERY; SYNDROME;

EID: 0030317958     PISSN: 00034819     EISSN: None     Source Type: Journal    
DOI: 10.7326/0003-4819-125-11-199612010-00005     Document Type: Article

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