Developmental paradigm for early features of cystic fibrosis

Pediatric Pulmonology

Volumn 40, Issue 5, 2005, Pages 371-377

  Larson, Janet E ^a,b   Cohen, J Craig ^a,c  

^a Joint Laboratory of Molecular Therapeutics   (United States)

^b OCHSNER CLINIC FOUNDATION   (United States)

^c LOUISIANA STATE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Cystic fibrosis; Cystic fibrosis transmembrane regulator; Epithelial differentiation; Lung development

Indexed keywords

ADENOVIRUS VECTOR; CHLORIDE CHANNEL; DNA; GLYCOGEN; MESSENGER RNA; SODIUM CHANNEL; TRANSMEMBRANE CONDUCTANCE REGULATOR;

CELL DIFFERENTIATION; CELL PROLIFERATION; CELL ULTRASTRUCTURE; CHANNEL GATING; CLINICAL FEATURE; CYSTIC FIBROSIS; EPITHELIUM CELL; FETUS DEVELOPMENT; GENE CONTROL; GENE EXPRESSION; GENE MUTATION; GENE OVEREXPRESSION; HUMAN; LUNG DEVELOPMENT; LUNG FUNCTION TEST; LUNG INFECTION; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PLEIOTROPY; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; REGULATORY MECHANISM; REVIEW; VIRAL GENE THERAPY;

CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GENE THERAPY; HUMANS; INTERLEUKIN-8; LUNG; MUTATION; PHENOTYPE; RESPIRATORY FUNCTION TESTS; RESPIRATORY TRACT INFECTIONS; RNA, MESSENGER;

EID: 27544434744     PISSN: 87556863     EISSN: None     Source Type: Journal    
DOI: 10.1002/ppul.20169     Document Type: Review

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