Hyperammonaemic encephalopathy after initiation of valproate therapy in unrecognised ornithine transcarbamylase deficiency

Journal of Neurology Neurosurgery and Psychiatry

Volumn 64, Issue 5, 1998, Pages 680-682

  Oechsner, M ^a,b   Steen, C ^b   Sturenburg H J ^a   Kohlschutter A ^b  

^a Department of Neurology ^*

^b UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

Author keywords

Ammonia in blood; Ornithine transcarbamylase deficiency; Valproic acid therapy

Indexed keywords

AMMONIA; GLUTAMINE; ORNITHINE CARBAMOYLTRANSFERASE; VALPROIC ACID;

ADOLESCENT; AMINO ACID BLOOD LEVEL; AMMONIA BLOOD LEVEL; ARTICLE; BRAIN DISEASE; CASE REPORT; COMPLEX PARTIAL SEIZURE; DIALYSIS; ENZYME DEFICIENCY; FEMALE; HUMAN; HYPERAMMONEMIA; MENTAL DEFICIENCY; PRIORITY JOURNAL; PROTEIN INTOLERANCE; UREA CYCLE; VOMITING;

EID: 0031924543     PISSN: 00223050     EISSN: None     Source Type: Journal    
DOI: 10.1136/jnnp.64.5.680     Document Type: Article

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