Emergencies in patients with inherited hemoglobin disorders - An emergency department perspective

Clinical Pediatric Emergency Medicine

Volumn 6, Issue 3, 2005, Pages 138-148

  Hampton, Rebecca R ^a,b   Balasa, Vinod ^a,b   Allen Bracey, Sheryl E ^a,b  

^a CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^b UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

Hemoglobin disorders; Methemoglobinemia; Sickle cell disease; Thalassemias

Indexed keywords

ANTIPYRETIC AGENT; CEFOTAXIME; HEMOGLOBIN; OXYGEN; PENICILLIN G;

ADOLESCENT; ANAMNESIS; ARTICLE; BLOOD GAS ANALYSIS; CASE REPORT; CHILD; CLINICAL PROTOCOL; DISEASE EXACERBATION; EMERGENCY TREATMENT; EMERGENCY WARD; ERYTHROCYTE TRANSFUSION; FEMALE; FEVER; HOSPITAL DISCHARGE; HOSPITALIZATION; HUMAN; LABORATORY TEST; LONG TERM CARE; MALE; OXYGEN SATURATION; PHYSICAL EXAMINATION; SICKLE CELL ANEMIA; THORAX RADIOGRAPHY;

EID: 25144518594     PISSN: 15228401     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cpem.2005.06.002     Document Type: Article

References (29)

1. D.J. Weatherall J.B. Clegg Inherited haemoglobin disorders: An increasing global health problem Bull World Health Organ 79 2001 704-712
2. H.M. Ranney Hemoglobin: A historical perspective In: M.H. Steinberg B.G. Forget D.R. Higgs editors. Disorders of hemoglobin: Genetics, pathophysiology, and clinical management 2001 Cambridge University Press New York 1-25
3. E. Uthman Hemoglobinathies and thalassemias In: http://we2.airmail.net/uthman/hemoglobinathy/hemoglobinpathy.html
4. D. Bachman R. Barkin S. Breenan Hematologic and oncologic disorders In: R.M. Barkin G. Caputo editors. Pediatric emergency medicine: Concepts and clinical practice 2nd ed. 1997 Mosby St Louis 897-912
5. G. Clarke T. Higgins Laboratory investigation of hemoglobinopathies and thalassemias: Review and update Clin Chem 46 2000 1284-1290
6. K. Quirolo E. Vinchinsky Hemoglobin disorders In: R.E. Behrman R.M. Kliegman H.B. Jenson editors. Nelson textbook of pediatrics 17th ed. 2004 WB Saunders Philadelphia 1624-1634
7. AAP Section on Hematology/Oncology Committee on Genetics Health supervision for children with sickle cell disease Pediatrics 109 2002 526-535
8. P.D. Sadowitz S. Amanullah A.K. Souid Hematologic emergencies in the pediatric emergency room Emerg Med Clin North Am 20 2002 177-198
9. M. Steinberg Management of sickle cell disease N Engl J Med 340 1999 1021-1030
10. A.R. Cohen Hematologic emergencies In: G.R. Fleisher S. Ludwig editors. Synopsis of pediatric emergency medicine 4th ed. 2002 Lippincott, Williams and Wilkins Philadelphia 351-355
11. New England Journal of Medicine electronic images: www.nejm.org
12. L. Neumayr E. Lennette D. Kelly et al. Mycoplasma disease and acute chest syndrome in sickle cell disease Pediatrics 112 2003 87-95
13. Wadiology cases in pediatric emergency medicine: http://www.hawaii.edu/medicine/pediatrics/pemxray/pemxray.html.
14. E. Vinchinsky L. Neuymayr A.N. Earles et al. Causes and outcomes of the acute chest syndrome in sickle cell disease N Engl J Med 342 2000 1855-1865
15. D.L. Wethers Sickle cell disease in childhood: Part II. Diagnosis and treatment of major complications and recent advances in treatment Am Fam Physician 62 2000 1309-1314
16. P.S. Bellet K.A. Kalinyak R. Shukla et al. Incentive spirometry to prevent acute pulmonary complications in sickle cell diseases N Engl J Med 333 1995 699-703
17. J. Wilimas P. Flynn S. Harris S. Day R. Smith P.J. Chesney et al. Randomized study of outpatient treatment with ceftriaxone for selected febrile children with sickle cell disease N Engl J Med 329 1993 472-476
18. A.R. Cohen Hematologic emergencies In: G.R. Fleisher S. Ludwig editors. Textbook of pediatric emergency medicine 4th ed. 2000 Lippincott, Williams and Wilkins Philadelphia 865-873
19. K. Ohene-Frempong S.J. Weiner L.A. Sleeper et al. Cerebrovascular accidents in sickle cell disease: Rates and risk factors Blood 91 1998 288-294
20. K. Ohene-Frempong Stroke in sickle cell disease: Demographic, clinical and therapeutic considerations Semin Hematol 28 1991 213-219
21. R.J. Adams V.C. McKie L. Hsu et al. Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography N Engl J Med 339 1998 5-11
22. O. Platt D.J. Brambilla W.F. Rosse et al. Mortality in sickle cell disease - life expectancy and risk factors for early death N Engl J Med 330 1994 1639-1644
23. G.R. Serjeant B.E. Serjeant P.W. Thomas et al. Human parvovirus infection in homozygous sickle cell disease Lancet 341 1993 237-240
24. K. Sackey Hemolytic anemia: Part I Pediatr Rev 20 1999 152-158
25. N.F. Olivieri The β thalassemias N Engl J Med 341 1999 99-109
26. D.L. Wethers Sickle cell disease in childhood: Part I. Laboratory diagnosis, pathophysiology and health maintenance Am Fam Physician 62 2000 1013-1020
27. D.R. Higgs Alpha thalassemia In: M.H. Steinberg B.G. Forget D.R. Higgs editors. Disorders of hemoglobin: Genetics, pathophysiology, and clinical management 2001 Cambridge University Press New York 389-390
28. J.L. Kwiatkowski A.R. Cohen Iron chelation therapy in sickle cell disease and other transfusion dependent anemias Hematol Oncol Clin North Am 18 2004 1355-1377
29. H. Rehman Methemoglobinemia West J Med 75 2001 193-198