Vascular wall remodeling in patients with supravalvular aortic stenosis and Williams Beuren syndrome

Journal of Vascular Research

Volumn 42, Issue 3, 2005, Pages 190-201

  Dridi, S M ^a   Foucault Bertaud, A ^a   Igondjo Tchen, S ^a   Senni, K ^a   Ejeil, A L ^a   Pellat, B ^a   Lyonnet, S ^b   Bonnet, D ^c   Charpiot, P ^d   Godeau, G ^a  

^a UNIVERSITÉ PARIS DESCARTES   (France)

^b INSERM   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

^d AIX MARSEILLE UNIVERSITY   (France)

Author keywords

Arteries; Elastic fibers; Supravalvular aortic stenosis; Williams Beuren syndrome

Indexed keywords

ENZYME; GELATINASE A; GELATINASE B; MATRILYSIN; TISSUE INHIBITOR OF METALLOPROTEINASE 2; METALLOPROTEINASE; TISSUE INHIBITOR OF METALLOPROTEINASE 1;

ADULT; AORTA SUPRAVALVULAR STENOSIS; ARTICLE; BLOOD VESSEL WALL; CASE REPORT; CELL MIGRATION; CELL SECRETION; CHILD; CONTROLLED STUDY; ELASTIC FIBER; ENZYME RELEASE; EPITHELIUM HYPERPLASIA; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; MORPHOLOGY; MORPHOMETRICS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; SKIN MANIFESTATION; SMOOTH MUSCLE FIBER; TISSUE REPAIR; VASCULAR SMOOTH MUSCLE; WILLIAMS BEUREN SYNDROME; AORTA; CASE CONTROL STUDY; IMAGE PROCESSING; IMMUNOLOGICAL PROCEDURES; METABOLISM; PATHOLOGY; PRESCHOOL CHILD; TISSUE DISTRIBUTION;

ADULT; AORTA; AORTIC STENOSIS, SUPRAVALVULAR; CASE-CONTROL STUDIES; CHILD; CHILD, PRESCHOOL; HUMANS; IMAGE PROCESSING, COMPUTER-ASSISTED; IMMUNOLOGIC TECHNIQUES; METALLOPROTEASES; TISSUE DISTRIBUTION; TISSUE INHIBITOR OF METALLOPROTEINASE-1; TISSUE INHIBITOR OF METALLOPROTEINASE-2; WILLIAMS SYNDROME;

EID: 20644433965     PISSN: 10181172     EISSN: None     Source Type: Journal    
DOI: 10.1159/000085141     Document Type: Article

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