L-Carnitine and exercise tolerance in medium-chain acyl-coenzyme A dehydrogenase (MCAD) deficiency: A pilot study

Journal of Inherited Metabolic Disease

Volumn 28, Issue 2, 2005, Pages 141-152

  Lee, Philip J ^a,c   Harrison, E L ^a   Jones, M G ^a   Jones, S ^a   Leonard, J V ^b   Chalmers, R A ^a,d  

^a ST GEORGE'S UNIVERSITY OF LONDON   (United Kingdom)

^b UNIVERSITY COLLEGE LONDON   (United Kingdom)

^c NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

^d ROYAL VETERINARY COLLEGE   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYLCARNITINE; ACYLCARNITINE; CARNITINE; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE;

ADOLESCENT; ADULT; AMINO ACID BLOOD LEVEL; AMINO ACID URINE LEVEL; ANAEROBIC THRESHOLD; ARTICLE; CASE REPORT; DIET SUPPLEMENTATION; DRUG MECHANISM; ENZYME DEFICIENCY; EXERCISE TEST; EXERCISE TOLERANCE; FEMALE; HEART RATE; HUMAN; MALE; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE DEFICIENCY; MITOCHONDRIAL RESPIRATION; OXYGEN CONSUMPTION; SCHOOL CHILD; SHORT COURSE THERAPY;

3-HYDROXYBUTYRIC ACID; ACIDS; ACYL-COA DEHYDROGENASE; ADOLESCENT; ADULT; ANAEROBIC THRESHOLD; BLOOD GLUCOSE; CARNITINE; CHILD; EXERCISE; EXERCISE TEST; FATTY ACIDS, NONESTERIFIED; FEMALE; HUMANS; LACTIC ACID; LIFE STYLE; MALE; METABOLISM, INBORN ERRORS; PILOT PROJECTS;

EID: 19444384285     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10545-005-5262-5     Document Type: Article

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