Identification of the RAG-1 as a suitable mouse model for mitochondrial DNA disease

Neuromuscular Disorders

Volumn 14, Issue 5, 2004, Pages 329-336

  Pye, Deborah ^a   Watt, Diana J ^b   Walker, Chris ^c   Lightowlers, Robert N ^a   Turnbull, Douglass M ^a  

^a NEWCASTLE UNIVERSITY   (United Kingdom)

^b BRIGHTON AND SUSSEX MEDICAL SCHOOL   (United Kingdom)

^c NEWCASTLE GENERAL HOSPITAL   (United Kingdom)

Author keywords

Muscle fibres; Recombinase activating gene 1; Severe combined immunodeficient mouse

Indexed keywords

BARIUM CHLORIDE; MITOCHONDRIAL DNA; RAG1 PROTEIN; RECOMBINASE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL TRANSFER; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; EXPERIMENTAL MODEL; EXPERIMENTAL MOUSE; IMMUNE DEFICIENCY; IRRADIATION; MITOCHONDRIAL MYOPATHY; MOUSE; MOUSE STRAIN; MUSCLE; MUSCLE ATROPHY; MUSCLE CELL; MUSCULAR DYSTROPHY; MYOBLAST; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DETERMINATION; STATISTICAL SIGNIFICANCE; TIBIALIS ANTERIOR MUSCLE;

ANALYSIS OF VARIANCE; ANIMALS; BARIUM COMPOUNDS; CELL TRANSPLANTATION; CELLS, CULTURED; CHLORIDES; DESMIN; DISEASE MODELS, ANIMAL; ELECTRON TRANSPORT COMPLEX IV; GENES, RAG-1; HUMANS; IMMUNOHISTOCHEMISTRY; MICE; MICE, INBRED BALB C; MICE, SCID; MITOCHONDRIAL MYOPATHIES; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, ANIMAL; MYOBLASTS; RADIATION; REGENERATION; SPECTRIN; STAINING AND LABELING;

EID: 1942521752     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nmd.2004.02.010     Document Type: Article

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