Mitochondrial localization of human PANK2 and hypotheses of secondary iron accumulation in pantothenate kinase-associated neurodegeneration

Annals of the New York Academy of Sciences

Volumn 1012, Issue , 2004, Pages 282-298

  Johnson, Monique A ^a   Kuo, Yien Ming ^b   Westaway, Shawn K ^a   Parker, Susan M ^a   Ching, Katherine H L ^a   Gitschier, Jane ^b   Hayflick, Susan J ^a  

^a OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^b HOWARD HUGHES MEDICAL INSTITUTE   (United States)

Author keywords

Brain iron; CoA; Hallervorden Spatz syndrome; Mitochondrial localization; Pantothenate kinase; PKAN

Indexed keywords

COENZYME A; IRON; PANTOTHENATE KINASE; PANTOTHENIC ACID;

ANIMAL CELL; ARTICLE; BASAL GANGLION; BRAIN MITOCHONDRION; CELL STRAIN COS1; CONTROLLED STUDY; DEGENERATIVE DISEASE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GENE; GENE FREQUENCY; GENE MUTATION; GENETIC SUSCEPTIBILITY; HALLERVORDEN SPATZ DISEASE; HELA CELL; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE MICROSCOPY; IMMUNOHISTOCHEMISTRY; IRON OVERLOAD; IRON STORAGE; MITOCHONDRIAL DNA DISORDER; NERVE DEGENERATION; NONHUMAN; NUCLEOTIDE SEQUENCE; OXIDATIVE STRESS; PANK2 GENE; PANTHOTENATE KINASE GENE; PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION; PARKINSON DISEASE; PROTEIN LOCALIZATION; SIGNAL TRANSDUCTION; START CODON; SYNDROME DELINEATION; TRANSLATION INITIATION;

ANIMALIA;

EID: 1842504252     PISSN: 00778923     EISSN: None     Source Type: Book Series    
DOI: 10.1196/annals.1306.023     Document Type: Article

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