-
1
-
-
0028946717
-
Intracellular folding of tissue-type plasminogen activator. Effects of disulfide bond formation on N-linked glycosylation and secretion
-
S. Allen, H.Y. Naim and N.J. Bulleid, Intracellular folding of tissue-type plasminogen activator. Effects of disulfide bond formation on N-linked glycosylation and secretion, J. Biol. Chem. 270 (1995), 4797-4804.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 4797-4804
-
-
Allen, S.1
Naim, H.Y.2
Bulleid, N.J.3
-
2
-
-
2342432162
-
The effect of disease-associated mutations on the folding pathway of human prion protein
-
A.C. Apetri, K. Surewicz and W. K. Surewicz, The effect of disease-associated mutations on the folding pathway of human prion protein, J. Biol. Chem. 279 (2004), 18008-18014.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 18008-18014
-
-
Apetri, A.C.1
Surewicz, K.2
Surewicz, W.K.3
-
3
-
-
0037934610
-
The interplay of glycosylation and disulfide formation influences fibrillization in a prion protein fragment
-
C.J. Bosques and B. Imperiali, The interplay of glycosylation and disulfide formation influences fibrillization in a prion protein fragment, Proc. Natl. Acad. Sci. USA 100 (2003), 7593-7598.
-
(2003)
Proc. Natl. Acad. Sci. USA
, vol.100
, pp. 7593-7598
-
-
Bosques, C.J.1
Imperiali, B.2
-
4
-
-
0033873642
-
Effect of the E200K mutation on prion protein metabolism. Comparative study of a cell model and human brain
-
S. Capellari, P. Parchi, C.M. Russo, J. Sanford, M.S. Sy, P. Gambetti and R.B. Petersen, Effect of the E200K mutation on prion protein metabolism. Comparative study of a cell model and human brain, Am. J. Pathol. 157 (2000), 613-622.
-
(2000)
Am. J. Pathol.
, vol.157
, pp. 613-622
-
-
Capellari, S.1
Parchi, P.2
Russo, C.M.3
Sanford, J.4
Sy, M.S.5
Gambetti, P.6
Petersen, R.B.7
-
5
-
-
0034045157
-
The Thr183Ala Mutation, Not the Loss of the First Glycosylation Site, Alters the Physical Properties of the Prion Protein
-
S. Capellari, S.I. Zaidi, A.C. Long, E.E. Kwon and R.B. Petersen, The Thr183Ala Mutation, Not the Loss of the First Glycosylation Site, Alters the Physical Properties of the Prion Protein, J. Alzheimers Dis. 2 (2000), 27-35.
-
(2000)
J. Alzheimers Dis.
, vol.2
, pp. 27-35
-
-
Capellari, S.1
Zaidi, S.I.2
Long, A.C.3
Kwon, E.E.4
Petersen, R.B.5
-
6
-
-
0033521131
-
Prion protein glycosylation is sensitive to redox change
-
S. Capellari, S.I. Zaidi, C.B. Urig, G. Perry, M.A. Smith and R.B. Petersen, Prion protein glycosylation is sensitive to redox change, J. Biol. Chem. 274 (1999), 34846-34850.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 34846-34850
-
-
Capellari, S.1
Zaidi, S.I.2
Urig, C.B.3
Perry, G.4
Smith, M.A.5
Petersen, R.B.6
-
7
-
-
0029027854
-
Truncated forms of the human prion protein in normal brain and in prion diseases
-
S.G. Chen, D.B. Teplow, P. Parchi, J.K. Teller, P. Gambetti and L. Autilio-Gambetti, Truncated forms of the human prion protein in normal brain and in prion diseases, J. Biol. Chem. 270(1995), 19173-19180.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 19173-19180
-
-
Chen, S.G.1
Teplow, D.B.2
Parchi, P.3
Teller, J.K.4
Gambetti, P.5
Autilio-Gambetti, L.6
-
8
-
-
0026849545
-
Linkage of the Indiana kindred of Gerstmann-Straussler-Scheinker disease to the prion protein gene
-
S.R. Dlouhy, K. Hsiao, M.R. Farlow, T. Foroud, P.M. Conneally, P. Johnson, S.B. Prusiner, M.E. Hodes and B. Ghetti, Linkage of the Indiana kindred of Gerstmann-Straussler-Scheinker disease to the prion protein gene,Nat. Genet. 1 (1992), 64-67.
-
(1992)
Nat. Genet.
, vol.1
, pp. 64-67
-
-
Dlouhy, S.R.1
Hsiao, K.2
Farlow, M.R.3
Foroud, T.4
Conneally, P.M.5
Johnson, P.6
Prusiner, S.B.7
Hodes, M.E.8
Ghetti, B.9
-
9
-
-
0023161237
-
Glycosylation inhibitors for N-linked glycoproteins
-
A.D. Elbein, Glycosylation inhibitors for N-linked glycoproteins, Methods Enzymol 138 (1987), 661-709.
-
(1987)
Methods Enzymol.
, vol.138
, pp. 661-709
-
-
Elbein, A.D.1
-
10
-
-
0038175192
-
Evolving views in prion glycosylation: Functional and pathological implications
-
M. Ermonval, S. Mouillet-Richard, P. Codogno, O. Kellermann and J. Botti, Evolving views in prion glycosylation: functional and pathological implications, Biochimie 85 (2003), 33-45.
-
(2003)
Biochimie
, vol.85
, pp. 33-45
-
-
Ermonval, M.1
Mouillet-Richard, S.2
Codogno, P.3
Kellermann, O.4
Botti, J.5
-
11
-
-
0017643758
-
Unconventional viruses and the origin and disappearance of kuru
-
D.C. Gajdusek, Unconventional viruses and the origin and disappearance of kuru, Science 197 (1977), 943-960.
-
(1977)
Science
, vol.197
, pp. 943-960
-
-
Gajdusek, D.C.1
-
12
-
-
0028198111
-
How N-linked oligosaccharides affect glycoprotein folding in the endoplasmic reticulum
-
A. Helenius, How N-linked oligosaccharides affect glycoprotein folding in the endoplasmic reticulum, Mol. Biol. Cell 5 (1994), 253-265.
-
(1994)
Mol. Biol. Cell
, vol.5
, pp. 253-265
-
-
Helenius, A.1
-
13
-
-
0023512804
-
Conserved arrangement of nested genes at the Drosophila Gart locus
-
S. Henikoff and M.K. Eghtedarzadeh, Conserved arrangement of nested genes at the Drosophila Gart locus. Genetics 117 (1987), 711-725.
-
(1987)
Genetics
, vol.117
, pp. 711-725
-
-
Henikoff, S.1
Eghtedarzadeh, M.K.2
-
14
-
-
0026849947
-
Mutant prion proteins in Gerstmann-Straussler-Scheinker disease with neurofibrillary tangles
-
K. Hsiao, S.R. Dlouhy, M.R. Farlow, C. Cass, M. Da Costa, P.M. Conneally, M.E. Hodes, B. Ghetti and S.B. Prusiner, Mutant prion proteins in Gerstmann-Straussler-Scheinker disease with neurofibrillary tangles, Nat. Genet. 1 (1992), 68-71.
-
(1992)
Nat. Genet.
, vol.1
, pp. 68-71
-
-
Hsiao, K.1
Dlouhy, S.R.2
Farlow, M.R.3
Cass, C.4
Da Costa, M.5
Conneally, P.M.6
Hodes, M.E.7
Ghetti, B.8
Prusiner, S.B.9
-
15
-
-
0026561901
-
Brefeldin A: Insights into the control of membrane traffic and organelle structure
-
R.D. Klausner, J.G. Donaldson and J. Lippincott-Schwartz, Brefeldin A: insights into the control of membrane traffic and organelle structure, J. Cell Biol. 116 (1992), 1071-1080.
-
(1992)
J. Cell Biol.
, vol.116
, pp. 1071-1080
-
-
Klausner, R.D.1
Donaldson, J.G.2
Lippincott-Schwartz, J.3
-
16
-
-
1842644947
-
Inherited prion diseases
-
S.B. Prusiner, ed., Cold Spring Harbor Laboratory Press, New York
-
Q. Kong, W.K. Surewicz, R.B. Petersen, W.Zou, S.G. Chen, P. Gambetti, P. Parchi, S. Capellari, L. Goldfarb, P. Montagna, E. Lugaresi, P. Piccardo and B. Ghetti, Inherited prion diseases, in: Prion Biology and Disease, S.B. Prusiner, ed., Cold Spring Harbor Laboratory Press, New York, 2004, pp. 673-776.
-
(2004)
Prion Biology and Disease
, pp. 673-776
-
-
Kong, Q.1
Surewicz, W.K.2
Petersen, R.B.3
Zou, W.4
Chen, S.G.5
Gambetti, P.6
Parchi, P.7
Capellari, S.8
Goldfarb, L.9
Montagna, P.10
Lugaresi, E.11
Piccardo, P.12
Ghetti, B.13
-
17
-
-
0022477981
-
Molecular cloning of a human prion protein cDNA
-
H.A. Kretzschmar, L.E. Stowring, D. Westaway, W.H. Stubblebine, S.B. Prusiner and S.J. Dearmond, Molecular cloning of a human prion protein cDNA, DNA 5 (1986), 315-324.
-
(1986)
DNA
, vol.5
, pp. 315-324
-
-
Kretzschmar, H.A.1
Stowring, L.E.2
Westaway, D.3
Stubblebine, W.H.4
Prusiner, S.B.5
Dearmond, S.J.6
-
18
-
-
0030799062
-
Blockade of glycosylation promotes acquisition of scrapie-like properties by the prion protein in cultured cells
-
S. Lehmann and D.A. Harris, Blockade of glycosylation promotes acquisition of scrapie-like properties by the prion protein in cultured cells, J. Biol. Chem. 272 ( 1997), 21479-21487.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 21479-21487
-
-
Lehmann, S.1
Harris, D.A.2
-
19
-
-
0034682866
-
Identification of an epitope in the C terminus of normal prion protein whose expression is modulated by binding events in the N terminus
-
R. Li, T. Liu, B.S. Wong, T. Pan, M. Morillas, W. Swietnicki, K. O'Rourke, P. Gambetti, W.K. Surewicz and M.S. Sy, Identification of an epitope in the C terminus of normal prion protein whose expression is modulated by binding events in the N terminus, J. Mol Biol 301 (2000), 567-573.
-
(2000)
J. Mol. Biol.
, vol.301
, pp. 567-573
-
-
Li, R.1
Liu, T.2
Wong, B.S.3
Pan, T.4
Morillas, M.5
Swietnicki, W.6
O'Rourke, K.7
Gambetti, P.8
Surewicz, W.K.9
Sy, M.S.10
-
20
-
-
0033574161
-
Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein
-
S. Liemann and R. Glockshuber, Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein, Biochemistry 38 (1999), 3258-3267.
-
(1999)
Biochemistry
, vol.38
, pp. 3258-3267
-
-
Liemann, S.1
Glockshuber, R.2
-
21
-
-
0037025370
-
Cell surface accumulation of a truncated transmembrane prion protein in Gerstmann-Straussler-Scheinker disease P102L
-
R.S. Mishra, Y. Gu, S. Bose, S. Verghese, S. Kalepu and N. Singh, Cell surface accumulation of a truncated transmembrane prion protein in Gerstmann-Straussler-Scheinker disease P102L, J. Biol. Chem. 277 (2002), 24554-24561.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 24554-24561
-
-
Mishra, R.S.1
Gu, Y.2
Bose, S.3
Verghese, S.4
Kalepu, S.5
Singh, N.6
-
23
-
-
17544366508
-
Effect of the D178N mutation and the codon 129 polymorphism on the metabolism of the prion protein
-
R.B. Petersen, P. Parchi, S.L. Richardson, C.B. Urig and P. Gambetti, Effect of the D178N mutation and the codon 129 polymorphism on the metabolism of the prion protein, J. Biol. Chem. 271 (1996), 12661-12668.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 12661-12668
-
-
Petersen, R.B.1
Parchi, P.2
Richardson, S.L.3
Urig, C.B.4
Gambetti, P.5
-
24
-
-
10344259077
-
Protease K resistant prion protein isoforms in Gerstmann-Straussler- Scheinker Disease (Indiana Kindred)
-
P. Piccardo, C. Seiler, S.R. Dlouhy, K. Young, M.R. Farlow, F. Prelli, B. Frangione, O. Bugiani, F. Tagliavini and B. Ghetti, Protease K resistant prion protein isoforms in Gerstmann-Straussler-Scheinker Disease (Indiana Kindred), J. Neuropath and Exp Neur 55 (1996), 1157-1163.
-
(1996)
J Neuropath. and Exp. Neur.
, vol.55
, pp. 1157-1163
-
-
Piccardo, P.1
Seiler, C.2
Dlouhy, S.R.3
Young, K.4
Farlow, M.R.5
Prelli, F.6
Frangione, B.7
Bugiani, O.8
Tagliavini, F.9
Ghetti, B.10
-
27
-
-
0026323642
-
Genomic structure of the human prion protein gene
-
C. Puckett, P. Concannon, C. Casey and L. Hood, Genomic structure of the human prion protein gene, Am. J. Hum. Genet. 49(1991), 320-329.
-
(1991)
Am. J. Hum. Genet.
, vol.49
, pp. 320-329
-
-
Puckett, C.1
Concannon, P.2
Casey, C.3
Hood, L.4
-
30
-
-
0029916898
-
The amino acid at the X position of an Asn-X-Ser sequon is an important determinant of N-linked core-glycosylation efficiency
-
S.H. Shakin-Eshleman, S.L. Spitalnik and L. Kasturi, The amino acid at the X position of an Asn-X-Ser sequon is an important determinant of N-linked core-glycosylation efficiency, J. Biol. Chem. 271 (1996), 6363-6366.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 6363-6366
-
-
Shakin-Eshleman, S.H.1
Spitalnik, S.L.2
Kasturi, L.3
-
31
-
-
0030658027
-
Prion protein aggregation reverted by low temperature in transfected cells carrying a prion protein gene mutation
-
N. Singh, G. Zanusso, S.G. Chen, H. Fujioka, S. Richardson, P. Gambetti and R.B. Petersen, Prion protein aggregation reverted by low temperature in transfected cells carrying a prion protein gene mutation, J. Biol. Chem. 272 (1997), 28461-28470.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 28461-28470
-
-
Singh, N.1
Zanusso, G.2
Chen, S.G.3
Fujioka, H.4
Richardson, S.5
Gambetti, P.6
Petersen, R.B.7
-
32
-
-
0023663071
-
Scrapie prion protein contains a phosphatidylinositol glycolipid
-
N. Stahl, D.R. Borchelt, K. Hsiao and S.B. Prusiner, Scrapie prion protein contains a phosphatidylinositol glycolipid, Cell 51 (1987), 229-240.
-
(1987)
Cell
, vol.51
, pp. 229-240
-
-
Stahl, N.1
Borchelt, D.R.2
Hsiao, K.3
Prusiner, S.B.4
-
33
-
-
0026033998
-
Amyloid protein of Gerstmann-Straussler-Scheinker disease (Indiana kindred) is an 11 kd fragment of prion protein with an N-terminal glycine at codon 58
-
F. Tagliavini, F. Prelli, J. Ghiso, O. Bugiani, D. Serban, S.B. Prusiner, M.R. Farlow, B. Ghetti and B. Frangione, Amyloid protein of Gerstmann-Straussler-Scheinker disease (Indiana kindred) is an 11 kd fragment of prion protein with an N-terminal glycine at codon 58, EMBO J. 10 (1991), 513-519.
-
(1991)
EMBO J.
, vol.10
, pp. 513-519
-
-
Tagliavini, F.1
Prelli, F.2
Ghiso, J.3
Bugiani, O.4
Serban, D.5
Prusiner, S.B.6
Farlow, M.R.7
Ghetti, B.8
Frangione, B.9
-
34
-
-
0025087141
-
Acquisition of protease resistance by prion proteins in scrapie-infected cells does not require asparagine-linked glycosylation
-
A. Taraboulos, M. Rogers, D.R. Borchelt, M.P. McKinley, M. Scott, D. Serban and S.B. Prusiner, Acquisition of protease resistance by prion proteins in scrapie-infected cells does not require asparagine-linked glycosylation, Proc. Natl. Acad. Sci. USA 87 (1990), 8262-8266.
-
(1990)
Proc. Natl. Acad. Sci. USA
, vol.87
, pp. 8262-8266
-
-
Taraboulos, A.1
Rogers, M.2
Borchelt, D.R.3
McKinley, M.P.4
Scott, M.5
Serban, D.6
Prusiner, S.B.7
-
35
-
-
0037073678
-
Disease-associated F198S mutation increases the propensity of the recombinant prion protein for conformational conversion to scrapie-like form
-
D.L. Vanik and W.K. Surewicz, Disease-associated F198S mutation increases the propensity of the recombinant prion protein for conformational conversion to scrapie-like form, J. Biol Chem. 277 (2002), 49065-49070.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 49065-49070
-
-
Vanik, D.L.1
Surewicz, W.K.2
-
36
-
-
13144256747
-
Prion protein expression in different species: Analysis with a panel of new mAbs
-
G. Zanusso, D. Liu, S. Ferrari, I. Hegyi, X. Yin, A. Aguzzi, S. Hornemann, S. Liemann, R. Glockshuber, J.C. Manson, P. Brown, R.B. Petersen, P. Gambetti and M.S. Sy, Prion protein expression in different species: analysis with a panel of new mAbs, Proc. Natl. Acad. Sci. USA 95 (1998), 8812-8816.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 8812-8816
-
-
Zanusso, G.1
Liu, D.2
Ferrari, S.3
Hegyi, I.4
Yin, X.5
Aguzzi, A.6
Hornemann, S.7
Liemann, S.8
Glockshuber, R.9
Manson, J.C.10
Brown, P.11
Petersen, R.B.12
Gambetti, P.13
Sy, M.S.14
-
37
-
-
0033551776
-
Proteasomal degradation and N-terminal protease resistance of the codon 145 mutant prion protein
-
G. Zanusso, R.B. Petersen, T. Jin, Y. Jing, R. Kanoush, S. Ferrari, P. Gambetti and N. Singh, Proteasomal degradation and N-terminal protease resistance of the codon 145 mutant prion protein, J. Biol. Chem. 274 (1999), 23396-23404.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 23396-23404
-
-
Zanusso, G.1
Petersen, R.B.2
Jin, T.3
Jing, Y.4
Kanoush, R.5
Ferrari, S.6
Gambetti, P.7
Singh, N.8
-
38
-
-
0033789318
-
Molecular dynamics simulation of human prion protein including both N-linked oligosaccharides and the GPI anchor
-
J. Zuegg and J.E. Gready, Molecular dynamics simulation of human prion protein including both N-linked oligosaccharides and the GPI anchor, Glycobiology 10 (2000), 959-974.
-
(2000)
Glycobiology
, vol.10
, pp. 959-974
-
-
Zuegg, J.1
Gready, J.E.2
|