A domain-specific usherin/collagen IV interaction may be required for stable integration into the basement membrane superstructure

Journal of Cell Science

Volumn 117, Issue 2, 2004, Pages 233-242

  Bhattacharya, Gautam ^a   Kalluri, Raghu ^b   Orten, Dana J ^a   Kimberling, William J ^a   Cosgrove, Dominic ^a  

^a BOYS TOWN NATIONAL RESEARCH HOSPITAL   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

Author keywords

Basement membrane; Collagen (IV); Protein interaction; Usher syndrome; Usherin

Indexed keywords

COLLAGEN TYPE 4; MEMBRANE PROTEIN; PEPTIDE; RECOMBINANT PROTEIN;

ALPORT SYNDROME; AMINO ACID SUBSTITUTION; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BASEMENT MEMBRANE; BINDING AFFINITY; BLINDNESS; CONTROLLED STUDY; HEARING IMPAIRMENT; IMMUNOPRECIPITATION; IN VIVO STUDY; MALE; MEMBRANE STRUCTURE; MISSENSE MUTATION; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; STOICHIOMETRY; TESTIS; WESTERN BLOTTING;

ANIMALS; BASEMENT MEMBRANE; CELLS, CULTURED; COLLAGEN TYPE IV; EXTRACELLULAR MATRIX PROTEINS; HUMANS; MICE; MICROSCOPY, IMMUNOELECTRON; MODELS, STRUCTURAL; MUTATION; PEPTIDE FRAGMENTS; PROTEIN BINDING; PROTEIN STRUCTURE, TERTIARY; SURFACE PLASMON RESONANCE;

ANIMALIA;

EID: 1642462397     PISSN: 00219533     EISSN: None     Source Type: Journal    
DOI: 10.1242/jcs.00850     Document Type: Article

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