Mental retardation and hypotonia seen in the knock out mouse for Canavan disease is not due to succinate semialdehyde dehydrogenase deficiency

Neuroscience Letters

Volumn 358, Issue 1, 2004, Pages 29-32

  Surendran, S ^a   Ezell, E L ^a   Quast, M J ^a   Wei, J ^a   Tyring, S K ^a   Michals Matalon, K ^a   Matalon, R ^a  

^a University of Texas Medical Branch School of Medicine   (United States)

Author keywords

Ketoglutarate dehydrogenase complex; Alanine aminotransferase; Canavan disease; Glutamate dehydrogenase; Succinate; Succinate semialdehyde dehydrogenase

Indexed keywords

4 AMINOBUTYRIC ACID; ALANINE AMINOTRANSFERASE; GLUTAMATE DEHYDROGENASE; GLUTAMIC ACID; OXOGLUTARATE DEHYDROGENASE; SUCCINATE SEMIALDEHYDE DEHYDROGENASE; SUCCINIC ACID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASSOCIATION; BRAIN STEM; CANAVAN DISEASE; CEREBELLUM; CLINICAL FEATURE; COMPLEX FORMATION; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME SYNTHESIS; KNOCKOUT MOUSE; MENTAL DEFICIENCY; MOUSE; MUSCLE HYPOTONIA; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION; PROTEIN SECRETION; SUCCINATE SEMIALDEHYDE DEHYDROGENASE DEFICIENCY;

ALDEHYDE OXIDOREDUCTASES; ANIMALS; CANAVAN DISEASE; MENTAL RETARDATION; MICE; MICE, KNOCKOUT; MUSCLE HYPOTONIA; SUCCINATE-SEMIALDEHYDE DEHYDROGENASE;

EID: 1542375297     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neulet.2003.12.105     Document Type: Article

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