Glutathione deficiency in patients with mitochondrial disease: Implications for pathogenesis and treatment

Journal of Inherited Metabolic Disease

Volumn 28, Issue 1, 2005, Pages 81-88

  Hargreaves, I P ^a   Sheena, Y ^a   Land, J M ^a   Heales, S J R ^a  

^a NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; CYTOCHROME C OXIDASE; GLUTATHIONE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE;

ARTICLE; CHILD; CLINICAL ARTICLE; COMPLEX I DEFICIENCY; COMPLEX II DEFICIENCY; COMPLEX III DEFICIENCY; CONTROLLED STUDY; CYTOCHROME C OXIDASE DEFICIENCY; DATA ANALYSIS; DISEASE COURSE; ELECTROCHEMICAL ANALYSIS; ENZYME ACTIVITY; FEMALE; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; HUMAN TISSUE; INFANT; MALE; MITOCHONDRIAL MYOPATHY; MUSCLE BIOPSY; OXIDATIVE STRESS; PATHOGENESIS; RESPIRATORY CHAIN; SKELETAL MUSCLE;

ADENOSINE TRIPHOSPHATE; AGE FACTORS; ANTIOXIDANTS; CHILD; CHILD, PRESCHOOL; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; FEMALE; GLUTATHIONE; HUMANS; INFANT; MALE; MITOCHONDRIAL DISEASES; MUSCLE, SKELETAL; OXIDATIVE STRESS; SEX FACTORS; TIME FACTORS;

EID: 13844276595     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10545-005-4160-1     Document Type: Article

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