A dominantly inherited progressive deafness affecting distal auditory nerve and hair cells

JARO - Journal of the Association for Research in Otolaryngology

Volumn 5, Issue 4, 2004, Pages 411-426

  Starr, Arnold ^a   Isaacson, Brandon ^b   Michalewski, Henry J ^a   Zeng, Fan Gang ^a   Kong, Ying Yee ^a   Beale, Paula ^c   Paulson, George W ^d   Keats, Bronya J B ^e   Lesperance, Marci M ^b  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF MICHIGAN HOSPITALS   (United States)

^c Ohio ENT Surgeons Inc   (United States)

^d OHIO STATE UNIVERSITY   (United States)

^e LOUISIANA STATE UNIVERSITY HEALTH SCIENCES CENTER   (United States)

Author keywords

Auditory neuropathy; Cochlear implant; Hereditary deafness; Sensorineural

Indexed keywords

ACOUSTIC NERVE FIBER; ADOLESCENT; ADULT; AGED; AMPLITUDE MODULATION; ARTICLE; AUDIOLOGY; AUDITORY SYSTEM; AUTOSOMAL DOMINANT INHERITANCE; BRAIN STEM RESPONSE; CELL FUNCTION; COCHLEA POTENTIAL; CONTROLLED STUDY; CRANIAL NEUROPATHY; DENDRITE; DISEASE COURSE; EVOKED BRAIN STEM AUDITORY RESPONSE; FAMILY; HAIR CELL; HEARING; HEARING IMPAIRMENT; HUMAN; IMPLANTATION; MAJOR CLINICAL STUDY; MALE; NERVE CELL; NERVE FIBER; NEUROPATHY; OTOACOUSTIC EMISSION; PERCEPTION DEAFNESS; PERIPHERAL NEUROPATHY; PHENOTYPE; PHYSIOLOGY; PRIORITY JOURNAL; PSYCHOANALYSIS; PSYCHOPHYSICS; SENSORY DYSFUNCTION; SOUND DETECTION; SPEECH DISCRIMINATION; SYNAPSE;

ACOUSTIC IMPEDANCE TESTS; AUDIOLOGY; COCHLEAR IMPLANTS; COCHLEAR NERVE; EVOKED POTENTIALS, AUDITORY; FEMALE; GENES, DOMINANT; HAIR CELLS; HEARING LOSS, SENSORINEURAL; HUMANS; MALE; NEURAL CONDUCTION; NEUROLOGIC EXAMINATION; PEDIGREE; PHENOTYPE; PSYCHOPHYSICS; REACTION TIME; SPEECH PERCEPTION;

EID: 13844264405     PISSN: 15253961     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10162-004-5014-5     Document Type: Article

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