-
1
-
-
0032539874
-
10 deficiency
-
10 deficiency, J. Neurol. Sci. 156 (1998), 41-46.
-
(1998)
J. Neurol. Sci.
, vol.156
, pp. 41-46
-
-
Boitier, E.1
Degoul, F.2
Desguerre, I.3
Charpentier, C.4
Francois, D.5
Ponsot, G.6
Diry, M.7
Rustin, P.8
Marsac, C.9
-
3
-
-
0035859689
-
10 deficiency
-
10 deficiency, Neurology 57 (2001), 515-518.
-
(2001)
Neurology
, vol.57
, pp. 515-518
-
-
Di Giovanni, S.1
Mirabella, M.2
Spinazzola, A.3
Crociani, P.4
Silvestri, G.5
Broccolini, A.6
Tonali, P.7
DiMauro, S.8
Servidei, S.9
-
4
-
-
0034735799
-
Coenzyme Q is an obligatory cofactor for uncoupling protein function
-
K.S. Echtay, E. Winkler and M. Klingenberg, Coenzyme Q is an obligatory cofactor for uncoupling protein function, Nature 408 (2000), 609-613.
-
(2000)
Nature
, vol.408
, pp. 609-613
-
-
Echtay, K.S.1
Winkler, E.2
Klingenberg, M.3
-
5
-
-
0035852755
-
Uncoupling proteins 2 and 3 are highly active H+ transporters and highly nucleotide sensitive when activated by coenzyme Q(ubiquinone)
-
K.S. Echtay, E. Winkler and M. Klingenberg, Uncoupling proteins 2 and 3 are highly active H+ transporters and highly nucleotide sensitive when activated by coenzyme Q(ubiquinone), Pro. Natl. Acad. Sci. 98 (2001), 1416-1421.
-
(2001)
Pro. Natl. Acad. Sci.
, vol.98
, pp. 1416-1421
-
-
Echtay, K.S.1
Winkler, E.2
Klingenberg, M.3
-
6
-
-
0025369150
-
Antioxidant effects of ubiquinone in microsome and mitochondria are mediated by tocopherol recycling
-
V. Kagan, E. Serbinova and L. Packer, Antioxidant effects of ubiquinone in microsome and mitochondria are mediated by tocopherol recycling, Biochem. Biophys. Res. Comm. 169 (1990), 851-857.
-
(1990)
Biochem. Biophys. Res. Comm.
, vol.169
, pp. 851-857
-
-
Kagan, V.1
Serbinova, E.2
Packer, L.3
-
7
-
-
0036710515
-
10 administration on its tissue concentrations, mitochondrial oxidant generation, and oxidative stress in the rat
-
10 administration on its tissue concentrations, mitochondrial oxidant generation, and oxidative stress in the rat, Free Rad, Biol and Med. 33 (2002), 627-638.
-
(2002)
Free Rad, Biol. and Med.
, vol.33
, pp. 627-638
-
-
Kwang, L.K.1
Kamzalov, S.2
Rebrin, I.3
Byne, A.V.4
Jana, C.K.5
Morris, P.6
Foster, M.J.7
Sohal, R.S.8
-
8
-
-
0037426430
-
10 deficiency
-
10 deficiency, Neurology 60 (2003), 1206-1208.
-
(2003)
Neurology
, vol.60
, pp. 1206-1208
-
-
Lamperti, C.1
Naini, A.2
Hirano, M.3
De Vivo, D.4
Bertini, E.5
Servidei6
Valeriani, M.7
Lynch, D.8
Banwell, B.9
Berg, M.10
Dubrovsky, T.11
Chiriboga, C.12
Angelini, C.13
Pegoraro, E.14
DiMauro, S.15
-
9
-
-
0030748375
-
Mitochondrial ubiquinone homologues, superoxide radical generation, and longevity in different mammalian species
-
A. Lass, S. Agarwal and R.S. Sohal, Mitochondrial ubiquinone homologues, superoxide radical generation, and longevity in different mammalian species, J. Biol. Chem. 272 (1997), 9199-19204.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 9199-19204
-
-
Lass, A.1
Agarwal, S.2
Sohal, R.S.3
-
10
-
-
0032522304
-
Electron transport-linked ubiquinone-dependent recycling of a-tocopherol inhibits autoxidation of mitochondrial membranes
-
A. Lass and R.S. Sohal, Electron transport-linked ubiquinone-dependent recycling of a-tocopherol inhibits autoxidation of mitochondrial membranes, Arch. Biochem, Biophys. 352 (1998), 229-236.
-
(1998)
Arch. Biochem, Biophys.
, vol.352
, pp. 229-236
-
-
Lass, A.1
Sohal, R.S.2
-
11
-
-
0023680684
-
The role of mobility of redox components in the inner mitochondrial membrane
-
G. Lenaz, The role of mobility of redox components in the inner mitochondrial membrane, J. Membr. Biol. 104 (1988), 193-209.
-
(1988)
J. Membr. Biol.
, vol.104
, pp. 193-209
-
-
Lenaz, G.1
-
14
-
-
0035836740
-
10 deficiency
-
10 deficiency, Neurology 56 (2001), 849-855.
-
(2001)
Neurology
, vol.56
, pp. 849-855
-
-
Musumeci, O.1
Naini, A.2
Slonim, A.E.3
Skavin, N.4
Hadjigeorgiou, G.L.5
Krawiecki, N.6
Weissman, B.M.7
Tsao, C.Y.8
Mandell, J.R.9
Shanske, S.10
De Vivo, D.C.11
Hirano, M.12
DeMauro, S.13
-
15
-
-
0141610413
-
Muscle coenzyme Q deficiency in familial mitochondrial encephalomyopathy
-
S. Ogasahara, A.G. Engel, D. Frens and D. Mack, Muscle coenzyme Q deficiency in familial mitochondrial encephalomyopathy, Pro. Natl. Acad. Sci. 86 (1989), 2379-2382.
-
(1989)
Pro. Natl. Acad. Sci.
, vol.86
, pp. 2379-2382
-
-
Ogasahara, S.1
Engel, A.G.2
Frens, D.3
Mack, D.4
-
16
-
-
0026666969
-
10 in the rat following its oral and intraperitoneal administration
-
10 in the rat following its oral and intraperitoneal administration, Drug. Met. Disp. 20 (1992), 423-427.
-
(1992)
Drug. Met. Disp.
, vol.20
, pp. 423-427
-
-
Reahal, S.1
Wrigglesworth, J.2
-
17
-
-
0034730011
-
10 deficiency
-
10 deficiency, Lancet 356 (2000), 391-395.
-
(2000)
Lancet
, vol.356
, pp. 391-395
-
-
Rötig, A.1
Appelkvist, E.L.2
Geromel, V.3
Chretien, D.4
Kadhom, N.5
Edery, P.6
Lebideau, M.7
Dallner, G.8
Munnich, A.9
Ernster, L.10
Rustin, P.11
-
18
-
-
0030975555
-
10 deficiency
-
10 deficiency, Neurology 48 (1997), 1238-1243.
-
(1997)
Neurology
, vol.48
, pp. 1238-1243
-
-
Sobreira, C.1
Hirano, M.2
Shanske, S.3
Keller, R.K.4
Heller, R.G.5
Davidson, E.6
Santorelli, F.M.7
Miranda, A.F.8
Bonilla, E.9
Mojon, D.S.10
Barreira, A.A.11
King, M.P.12
Dimauro, S.13
-
19
-
-
0036895391
-
Coenzyme Q-responsive Leigh's encephalopathy in two sisters
-
L. Van Maldergem, F. Trijbels, S. DiMauro, P. Sindler, O. Musumeci, A. Janssen, X. Delberghe, J. Martin and Y. Gillerot, Coenzyme Q-responsive Leigh's encephalopathy in two sisters, Ann. Neurol. 52 (2002), 750-754.
-
(2002)
Ann. Neurol.
, vol.52
, pp. 750-754
-
-
Van Maldergem, L.1
Trijbels, F.2
DiMauro, S.3
Sindler, P.4
Musumeci, O.5
Janssen, A.6
Delberghe, X.7
Martin, J.8
Gillerot, Y.9
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