Lipid malabsorption in cystic fibrosis

Pediatric Pulmonology

Volumn 30, Issue SUPPL. 20, 2000, Pages 156-158

  Feranchak, Andrew P ^a  

^a CHILDREN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

EID: 0345852299     PISSN: 87556863     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Conference Paper

References (12)

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2. Feranchak AP, Sontag MK, Wagener JS, Hammond KB, Accurso FJ, Sokol RJ. Prospective, long-term study of fat-soluble vitamin status in children with cystic fibrosis identified by newborn screen. J Pediatr 135:601-10, 1999.
3. Holman RT, Johnson SB, Hatch F. A case of human linolenic acid deficiency involving neurologic abnormalities. Am J Clin Nutr 35:617-623, 1982.
4. Hansen AE, Haggard ME, Boelsche AN, et al. Essential fatty acids in infant nutrition. III. Clinical manifestations of linolenic acid deficiency. J Nutr 60:565-576, 1958.
5. Holman RT, et al. Essential fatty acid deficiency in malnourished children. Am J Clin Nutr 34:1534, 1981.
6. Durie PR, Pencharz PB. A rational approach to the nutritional care of patients with cystic fibrosis. J Roy Soc Med 82:516:11-20, 1989.
7. Rogiers V, Dab I, Brokaert R, Vis HL. Long-chain nonesterified fatty acid patterns in plasma of cystic fibrosis patients and their parents. Pediatr Res 14: 1088-1091, 1980.
8. Christophe AB, Warwick WJ, Holman RT. Serum fatty acid profiles in cystic fibrosis patients and their parents. Lipids 29:569-75, 1994.
9. Roulet M, Frascarolo P, Rappaz I, Pilet M. Essential fatty acid deficiency in well nourished young cystic fibrosis patients. Eur J Pediatr 156:952-956, 1997.
10. Gilljam H, Strandvik B, Ellin A, Wiman LG. Scand J Clin Lab Invest 46:511-518, 1986.
11. Anderson MP, Welsh MJ. Fatty acids inhibit apical membrane chloride channels in airway epithelial. Proc Natl Acad Sci USA 87:7334-8, 1990.
12. Freedman SD, Katz MH, Parker EM, Laposata M, Urman MY, Alvarez JG. A membrane lipid imbalance plays a role in the phenotypic expression of cystic fibrosis in CFTR -/- mice. Proc Natl Acad Sci USA 96:13995-14000, 1999.