Differential utilization of systemic and enteral ammonia for urea synthesis in control subjects and ornithine transcarbamylase deficiency carriers

American Journal of Clinical Nutrition

Volumn 78, Issue 4, 2003, Pages 749-755

  Scaglia, Fernando ^a   Marini, Juan ^b   Rosenberger, Judy ^a   Henry, Joseph ^a   Garlick, Peter ^c   Lee, Brendan ^a   Reeds, Peter ^b  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF ILLINOIS AT URBANA CHAMPAIGN   (United States)

^c STONY BROOK UNIVERSITY   (United States)

Author keywords

Ammonia flux; Humans; Ornithine transcarbamylase deficiency; Stable isotopes; Urea synthesis

Indexed keywords

AMMONIA; AMMONIA N 15; ORNITHINE CARBAMOYLTRANSFERASE; TRACER; UNCLASSIFIED DRUG; UREA C 14; UREA O 18; UREA;

ARTICLE; CALORIC INTAKE; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; FEMALE; GENOTYPE; HUMAN; ISOTOPE LABELING; PROTEIN INTAKE; SYMPTOMATOLOGY; UREA CYCLE; ADULT; CASE CONTROL STUDY; HETEROZYGOTE; INTRAVENOUS DRUG ADMINISTRATION; LIVER; MALE; METABOLISM; MIDDLE AGED; ORAL DRUG ADMINISTRATION;

ADMINISTRATION, ORAL; ADULT; AMMONIA; CARRIER STATE; CASE-CONTROL STUDIES; FEMALE; HUMANS; INJECTIONS, INTRAVENOUS; LIVER; MALE; MIDDLE AGED; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; UREA;

EID: 0142024838     PISSN: 00029165     EISSN: None     Source Type: Journal    
DOI: 10.1093/ajcn/78.4.749     Document Type: Article

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