Analysis of intracellular storage and regulated secretion of 3 von Willebrand disease-causing variants of von Willebrand factor

Blood

Volumn 102, Issue 7, 2003, Pages 2452-2458

  Michaux, Grégoire ^b   Hewlett, Lindsay J ^b   Messenger, Sarah L ^b   Goodeve, Anne C ^b   Peake, Ian R ^b   Daly, Martina E ^b   Cutler, Daniel F ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

CD63 ANTIGEN; COMPLEMENTARY DNA; MEMBRANE PROTEIN; PADGEM PROTEIN; PHORBOL ESTER; POLYMER; RECOMBINANT PROTEIN; VON WILLEBRAND FACTOR;

ANALYTIC METHOD; ARTICLE; CELL COMPARTMENTALIZATION; CELL FUNCTION; CELL ORGANELLE; CELL STRUCTURE; CONTROLLED STUDY; DISEASE SEVERITY; ENDOTHELIUM CELL; EXOCYTOSIS; GENE MUTATION; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; INTRACELLULAR TRANSPORT; NONHUMAN; POLYMERIZATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SECRETION; PROTEIN STRUCTURE; PROTEIN TRANSPORT; PROTEIN VARIANT; REGULATORY MECHANISM; STRUCTURE ACTIVITY RELATION; VON WILLEBRAND DISEASE; WEIBEL PALADE BODY; WILD TYPE;

EID: 0141705326     PISSN: 00064971     EISSN: None     Source Type: Journal    
DOI: 10.1182/blood-2003-02-0599     Document Type: Article

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