Endoplasmic reticulum retention and prolonged association of a von Willebrand's disease-causing von Willebrand factor variant with ERp57 and calnexin

Biochemical and Biophysical Research Communications

Volumn 280, Issue 2, 2001, Pages 448-453

  Allen, Simon ^a   Goodeve, Anne C ^a   Peake, Ian R ^a   Daly, Martina E ^a  

^a UNIVERSITY OF SHEFFIELD   (United Kingdom)

Author keywords

Calnexin; Calreticulin; Endoplasmic reticulum; ERp57; Molecular chaperones; Von Willebrand factor; Von Willebrand's disease

Indexed keywords

CALNEXIN; CALRETICULIN; ENDOGLYCOSIDASE H; GLYCOSIDASE; OXIDOREDUCTASE; PROTEIN; PROTEIN ERP57; UNCLASSIFIED DRUG; VON WILLEBRAND FACTOR;

ANIMAL CELL; ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; IMMUNOPRECIPITATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN PROTEIN INTERACTION; PROTEIN VARIANT; VON WILLEBRAND DISEASE;

EID: 0034810825     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1006/bbrc.2000.4139     Document Type: Article

References (21)

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14. ERp57 functions as a subunit of specific complexes formed with the ER lectins calreticulin and calnexin
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