-
1
-
-
0026297937
-
Antineutrophil elastase activity in cystic fibrosis serum
-
Cantin, A. M., S. Lafrenaye, and R. O. Begin. 1991. Antineutrophil elastase activity in cystic fibrosis serum. Pediatr. Pulmonol. 11:249-253.
-
(1991)
Pediatr. Pulmonol.
, vol.11
, pp. 249-253
-
-
Cantin, A.M.1
Lafrenaye, S.2
Begin, R.O.3
-
2
-
-
0028240276
-
Protease-antiprotease imbalance in the lungs of children with cystic fibrosis
-
Birrer, P., N. G. McElvaney, A. Rudeberg, C. W. Sommer, S. Liechti-Gallati, R. Kraemer, R. Hubbard, and R. G. Crystal. 1994. Protease-antiprotease imbalance in the lungs of children with cystic fibrosis. Am. J. Respir. Crit. Care Med. 150:207-213.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.150
, pp. 207-213
-
-
Birrer, P.1
McElvaney, N.G.2
Rudeberg, A.3
Sommer, C.W.4
Liechti-Gallati, S.5
Kraemer, R.6
Hubbard, R.7
Crystal, R.G.8
-
3
-
-
0027131471
-
alpha 1-Proteinase inhibitor, elastase activity, and lung disease severity in cystic fibrosis
-
O'Connor, C. M., K. Gaffney, J. Keane, A. Southey, N. Byrne, S. O'Mahoney, and M. X. Fitzgerald. 1993. alpha 1-Proteinase inhibitor, elastase activity, and lung disease severity in cystic fibrosis. Am. Rev. Respir. Dis. 148:1665-1670.
-
(1993)
Am. Rev. Respir. Dis.
, vol.148
, pp. 1665-1670
-
-
O'Connor, C.M.1
Gaffney, K.2
Keane, J.3
Southey, A.4
Byrne, N.5
O'Mahoney, S.6
Fitzgerald, M.X.7
-
4
-
-
0022485439
-
Lysosomal enzymes from polymorphonuclear leukocytes and proteinase inhibitors in patients with cystic fibrosis
-
Goldstein, W., and G. Doring. 1986. Lysosomal enzymes from polymorphonuclear leukocytes and proteinase inhibitors in patients with cystic fibrosis. Am. Rev. Respir. Dis. 134:49-56.
-
(1986)
Am. Rev. Respir. Dis.
, vol.134
, pp. 49-56
-
-
Goldstein, W.1
Doring, G.2
-
5
-
-
0024822502
-
Adherence of Pseudomonas aeruginosa to respiratory epithelium and the effect of leucocyte elastase
-
Plotkowski, M. C., G. Beck. J. M. Tournier, M. Bernardo-Filho, E. A. Marques, and E. Puchelle. 1989. Adherence of Pseudomonas aeruginosa to respiratory epithelium and the effect of leucocyte elastase. J. Med. Microbiol. 30:285-293.
-
(1989)
J. Med. Microbiol.
, vol.30
, pp. 285-293
-
-
Plotkowski, M.C.1
Beck, G.2
Tournier, J.M.3
Bernardo-Filho, M.4
Marques, E.A.5
Puchelle, E.6
-
6
-
-
0027986436
-
Pseudomonas aeruginosa selective adherence to and entry into human endothelial cells
-
Plotkowski, M. C., A. M. Saliba, S. H. Pereira, M. P. Cervante, and O. Bajolet-Laudinat. 1994. Pseudomonas aeruginosa selective adherence to and entry into human endothelial cells. Infect. Immun. 62:5456-5463.
-
(1994)
Infect. Immun.
, vol.62
, pp. 5456-5463
-
-
Plotkowski, M.C.1
Saliba, A.M.2
Pereira, S.H.3
Cervante, M.P.4
Bajolet-Laudinat, O.5
-
7
-
-
0030780774
-
Genetic and immunologic aspects of cystic fibrosis
-
Hilman, B. C. 1997. Genetic and immunologic aspects of cystic fibrosis. Ann. Allergy Asthma Immunol. 79:379-390.
-
(1997)
Ann. Allergy Asthma Immunol.
, vol.79
, pp. 379-390
-
-
Hilman, B.C.1
-
8
-
-
0026036665
-
Circulating levels of tumor necrosis factor and interleukin-1 in cystic fibrosis
-
Brown, M. A., W. J. Morgan, P. R. Finley, and P. Scuderi. 1991. Circulating levels of tumor necrosis factor and interleukin-1 in cystic fibrosis. Pediatr. Pulmonol. 10:86-91.
-
(1991)
Pediatr. Pulmonol.
, vol.10
, pp. 86-91
-
-
Brown, M.A.1
Morgan, W.J.2
Finley, P.R.3
Scuderi, P.4
-
9
-
-
0022496447
-
Imbalance between polymorphonuclear leukocyte proteases and antiproteases in chronic pyogenic infections and its relation to the proteolysis of complement component C3
-
Suter, S. 1986. Imbalance between polymorphonuclear leukocyte proteases and antiproteases in chronic pyogenic infections and its relation to the proteolysis of complement component C3. Complement 3:1-24.
-
(1986)
Complement
, vol.3
, pp. 1-24
-
-
Suter, S.1
-
10
-
-
0025136920
-
Genetic influences on pulmonary severity in cystic fibrosis
-
Santis, G., L. Osborne, R. Knight, M. E. Hodson, and M. Ramsay. 1990. Genetic influences on pulmonary severity in cystic fibrosis. Lancet 335:294.
-
(1990)
Lancet
, vol.335
, pp. 294
-
-
Santis, G.1
Osborne, L.2
Knight, R.3
Hodson, M.E.4
Ramsay, M.5
-
11
-
-
0025011469
-
Cystic fibrosis haplotype association and the delta F508 mutation in adult British CF patients
-
Santis, G., L. Osborne, R. Knight, M. Ramsay, R. Williamson, and M. Hodson. 1990. Cystic fibrosis haplotype association and the delta F508 mutation in adult British CF patients. Hum. Genet. 85:424-425.
-
(1990)
Hum. Genet.
, vol.85
, pp. 424-425
-
-
Santis, G.1
Osborne, L.2
Knight, R.3
Ramsay, M.4
Williamson, R.5
Hodson, M.6
-
12
-
-
0031589641
-
Mutation in an alpha1-antitrypsin enhancer results in an interleukin-6 deficient acute-phase response due to loss of cooperativity between transcription factors
-
Morgan, K., G. Scobie, P. Marsters, and N. A. Kalsheker. 1997. Mutation in an alpha1-antitrypsin enhancer results in an interleukin-6 deficient acute-phase response due to loss of cooperativity between transcription factors. Biochim. Biophys. Acta 1362:67-76.
-
(1997)
Biochim. Biophys. Acta
, vol.1362
, pp. 67-76
-
-
Morgan, K.1
Scobie, G.2
Marsters, P.3
Kalsheker, N.A.4
-
13
-
-
0028473632
-
Allotypes of alpha 1-antitrypsin in patients with cystic fibrosis, homozygous and heterozygous for deltaF508
-
Doring, G., H. Krogh-Johansen, S. Weidinger, and N. Hoiby. 1994. Allotypes of alpha 1-antitrypsin in patients with cystic fibrosis, homozygous and heterozygous for deltaF508. Pediatr. Pulmonol. 18:3-7.
-
(1994)
Pediatr. Pulmonol.
, vol.18
, pp. 3-7
-
-
Doring, G.1
Krogh-Johansen, H.2
Weidinger, S.3
Hoiby, N.4
-
14
-
-
0031704170
-
Alpha-1 anti-trypsin deficiency alleles and severe cystic fibrosis lung disease
-
Mahadeva, R., S. Stewart, D. Bilton, and D. A. Lomas. 1998. Alpha-1 anti-trypsin deficiency alleles and severe cystic fibrosis lung disease. Thorax 53:1022-1024.
-
(1998)
Thorax
, vol.53
, pp. 1022-1024
-
-
Mahadeva, R.1
Stewart, S.2
Bilton, D.3
Lomas, D.A.4
-
15
-
-
0031596312
-
Alpha-1 antitrypsin deficiency alleles and the Taq-I G→A allele in cystic fibrosis lung disease
-
Mahadeva, R., R. C. Westerbeek, D. J. Perry, J. U. Lovegrove, D. B. Whitehouse, N. R. Carroll, R. I. Ross-Russell, A. K. Webb, D. Bilton, and D. A. Lomas. 1998. Alpha-1 antitrypsin deficiency alleles and the Taq-I G→A allele in cystic fibrosis lung disease. Eur. Respir. J. 11:873-879.
-
(1998)
Eur. Respir. J.
, vol.11
, pp. 873-879
-
-
Mahadeva, R.1
Westerbeek, R.C.2
Perry, D.J.3
Lovegrove, J.U.4
Whitehouse, D.B.5
Carroll, N.R.6
Ross-Russell, R.I.7
Webb, A.K.8
Bilton, D.9
Lomas, D.A.10
-
16
-
-
0034744674
-
An alpha(1)-antitrypsin enhancer polymorphism is a genetic modifier of pulmonary outcome in cystic fibrosis
-
Henry, M. T., S. Cave, J. Rendall, C. M. O'Connor, K. Morgan, M. X. FitzGerald, and N. Kalsheker. 2001. An alpha(1)-antitrypsin enhancer polymorphism is a genetic modifier of pulmonary outcome in cystic fibrosis. Eur. J. Hum. Genet. 9:273-278.
-
(2001)
Eur. J. Hum. Genet.
, vol.9
, pp. 273-278
-
-
Henry, M.T.1
Cave, S.2
Rendall, J.3
O'Connor, C.M.4
Morgan, K.5
FitzGerald, M.X.6
Kalsheker, N.7
-
17
-
-
0033124185
-
alphaI-antitrypsin genotypes and the acute-phase response to open heart surgery
-
Sandford, A. J., T. Chagani, J. J. Spinelli, and P. D. Pare. 1999. alphaI-antitrypsin genotypes and the acute-phase response to open heart surgery. Am. J. Respir. Crit. Care Med. 159:1624-1628.
-
(1999)
Am. J. Respir. Crit. Care Med.
, vol.159
, pp. 1624-1628
-
-
Sandford, A.J.1
Chagani, T.2
Spinelli, J.J.3
Pare, P.D.4
-
18
-
-
0029090616
-
Standardization of Spirometry, 1994 update
-
American Thoracic Society
-
Anonymous. 1995. Standardization of Spirometry, 1994 update. American Thoracic Society. Am. J. Respir. Crit. Care Med. 152:1107-11136.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.152
, pp. 1107-11136
-
-
-
19
-
-
0019457107
-
Reference spirometric values using techniques and equipment that meet ATS recommendations
-
Crapo, R. O., A. H. Morris, and R. M. Gardner. 1981. Reference spirometric values using techniques and equipment that meet ATS recommendations. Am. Rev. Respir. Dis. 123:659-4564.
-
(1981)
Am. Rev. Respir. Dis.
, vol.123
, pp. 659-4564
-
-
Crapo, R.O.1
Morris, A.H.2
Gardner, R.M.3
-
20
-
-
0024372516
-
Lung function values from a longitudinal study of healthy children and adolescents
-
Hibbert, M. E., A. Lannigan, L. I. Landau, and P. D. Phelan. 1989. Lung function values from a longitudinal study of healthy children and adolescents. Pediatr. Pulmonol. 7:101-109.
-
(1989)
Pediatr. Pulmonol.
, vol.7
, pp. 101-109
-
-
Hibbert, M.E.1
Lannigan, A.2
Landau, L.I.3
Phelan, P.D.4
-
21
-
-
0042283246
-
Long-term study of one hundred five patients with cystic fibrosis
-
Shwachman, H., and L. Kulczycki. 1958. Long-term study of one hundred five patients with cystic fibrosis. Am. J. Dis. Child. 96:6-15.
-
(1958)
Am. J. Dis. Child.
, vol.96
, pp. 6-15
-
-
Shwachman, H.1
Kulczycki, L.2
-
22
-
-
0018377101
-
The chest roentgenogram in cystic fibrosis: A new scoring system
-
Brasfield, D., G. Hicks, S. Soong, and R. E. Tiller. 1979. The chest roentgenogram in cystic fibrosis: a new scoring system. Pediatrics 63:24-29.
-
(1979)
Pediatrics
, vol.63
, pp. 24-29
-
-
Brasfield, D.1
Hicks, G.2
Soong, S.3
Tiller, R.E.4
-
23
-
-
0025167094
-
Independent mutations in the flanking sequence of the alpha-1-antitrypsin gene are associated with chronic obstructive airways disease
-
Kalsheker, N. A., G. L. Watkins, S. Hill, K. Morgan, R. A. Stockley, and R. B. Fick. 1990. Independent mutations in the flanking sequence of the alpha-1-antitrypsin gene are associated with chronic obstructive airways disease. Dis. Markers 8:151-157.
-
(1990)
Dis. Markers
, vol.8
, pp. 151-157
-
-
Kalsheker, N.A.1
Watkins, G.L.2
Hill, S.3
Morgan, K.4
Stockley, R.A.5
Fick, R.B.6
-
24
-
-
0033979879
-
Risk of hospital admission for obstructive pulmonary disease in alpha(1)-antitrypsin heterozygotes of phenotype PiMZ
-
Seersholm, N., J. T. Wilcke, A. Kok-Jensen, and A. Dirksen. 2000. Risk of hospital admission for obstructive pulmonary disease in alpha(1)-antitrypsin heterozygotes of phenotype PiMZ. Am. J. Respir. Crit. Care Med. 161:81-84.
-
(2000)
Am. J. Respir. Crit. Care Med.
, vol.161
, pp. 81-84
-
-
Seersholm, N.1
Wilcke, J.T.2
Kok-Jensen, A.3
Dirksen, A.4
-
25
-
-
0025966879
-
Aerosol alpha 1-antitrypsin treatment for cystic fibrosis
-
McElvaney, N. G., R. C. Hubbard, P. Birrer, M. S. Chernick, D. B. Caplan. M. M. Frank, and R. G. Crystal. 1991. Aerosol alpha 1-antitrypsin treatment for cystic fibrosis. Lancet 337:392-394.
-
(1991)
Lancet
, vol.337
, pp. 392-394
-
-
McElvaney, N.G.1
Hubbard, R.C.2
Birrer, P.3
Chernick, M.S.4
Caplan, D.B.5
Frank, M.M.6
Crystal, R.G.7
-
26
-
-
0019984864
-
Serum levels of acute phase and cardiac proteins after myocardial infarction, surgery, and infection
-
Voulgari, F., P. Cummins, T. I. Gardecki, N. J. Beeching, P. C. Stone, and J. Stuart. 1982. Serum levels of acute phase and cardiac proteins after myocardial infarction, surgery, and infection. Br. Heart J. 48:352-356.
-
(1982)
Br. Heart J.
, vol.48
, pp. 352-356
-
-
Voulgari, F.1
Cummins, P.2
Gardecki, T.I.3
Beeching, N.J.4
Stone, P.C.5
Stuart, J.6
-
27
-
-
0014386781
-
Genetically determined differences in the response of alpha-antitrypsin levels in human serum to typhoid vaccine
-
Kueppers, F. 1968. Genetically determined differences in the response of alpha-antitrypsin levels in human serum to typhoid vaccine. Humangenetik 6:207-214.
-
(1968)
Humangenetik
, vol.6
, pp. 207-214
-
-
Kueppers, F.1
-
28
-
-
0031831817
-
Acute-phase protein response to infection in severe malnutrition
-
Morlese, J. F., T. Forrester, and F. Jahoor. 1998. Acute-phase protein response to infection in severe malnutrition. Am. J. Physiol. 275:E112-E117.
-
(1998)
Am. J. Physiol.
, vol.275
-
-
Morlese, J.F.1
Forrester, T.2
Jahoor, F.3
-
30
-
-
0035113140
-
Predictability of oxygen desaturation during sleep in patients with cystic fibrosis: Clinical, spirometric, and exercise parameters
-
Frangolias, D. D., and P. G. Wilcox. 2001. Predictability of oxygen desaturation during sleep in patients with cystic fibrosis: clinical, spirometric, and exercise parameters. Chest 119:434-441.
-
(2001)
Chest
, vol.119
, pp. 434-441
-
-
Frangolias, D.D.1
Wilcox, P.G.2
-
31
-
-
0036204597
-
Effects of tobramycin solution for inhalation on global ratings of quality of life in patients with cystic fibrosis and Pseudomonas aeruginosa infection
-
Quittner, A. L., and A. Buu. 2002. Effects of tobramycin solution for inhalation on global ratings of quality of life in patients with cystic fibrosis and Pseudomonas aeruginosa infection. Pediatr. Pulmonol. 33:269-276.
-
(2002)
Pediatr. Pulmonol.
, vol.33
, pp. 269-276
-
-
Quittner, A.L.1
Buu, A.2
-
32
-
-
0034915189
-
Comparison of three generic questionnaires measuring quality of life in adolescents and adults with cystic fibrosis: The 36-item short form health survey, the quality of life profile for chronic diseases, and the questions on life satisfaction
-
Goldbeck, L., and T. G. Schmitz. 2001. Comparison of three generic questionnaires measuring quality of life in adolescents and adults with cystic fibrosis: the 36-item short form health survey, the quality of life profile for chronic diseases, and the questions on life satisfaction. Qual. Life Res. 10:23-36.
-
(2001)
Qual. Life Res.
, vol.10
, pp. 23-36
-
-
Goldbeck, L.1
Schmitz, T.G.2
-
33
-
-
0035000956
-
Pulmonary function, inflammation, exercise capacity and quality of life in cystic fibrosis
-
Bradley, J., O. McAlister, and S. Elborn. 2001. Pulmonary function, inflammation, exercise capacity and quality of life in cystic fibrosis. Eur. Respir. J. 17:712-715.
-
(2001)
Eur. Respir. J.
, vol.17
, pp. 712-715
-
-
Bradley, J.1
McAlister, O.2
Elborn, S.3
|