-
1
-
-
0028220333
-
Heterogeneity in the severity of cystic fibrosis and the role of CFTR gene mutations
-
Dean M, Santis G. Heterogeneity in the severity of cystic fibrosis and the role of CFTR gene mutations. Hum Genet 1994;93:364-8.
-
(1994)
Hum Genet
, vol.93
, pp. 364-368
-
-
Dean, M.1
Santis, G.2
-
2
-
-
0022350960
-
Cystic fibrosis locus defined by a genetically linked polymorphic DNA marker
-
Tsui LC, Buchwald M, Barker D, et al. Cystic fibrosis locus defined by a genetically linked polymorphic DNA marker, Science 1985;230:1054-7.
-
(1985)
Science
, vol.230
, pp. 1054-1057
-
-
Tsui, L.C.1
Buchwald, M.2
Barker, D.3
-
3
-
-
0024453308
-
Identification of the cystic fibrosis gene: Chromosome walking and jumping
-
Rommens JM, Iannuzzi MC, Kerem B, et al. Identification of the cystic fibrosis gene: chromosome walking and jumping. Science 1989;245:1059-65.
-
(1989)
Science
, vol.245
, pp. 1059-1065
-
-
Rommens, J.M.1
Iannuzzi, M.C.2
Kerem, B.3
-
4
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan JR, Rommens JM, Kerem B, et al. Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 1989;245:1066-73.
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.3
-
5
-
-
0024423668
-
Identification of the cystic fibrosis gene: Genetic analysis
-
Kerem B, Rommens JM, Buchanan JA, et al. Identification of the cystic fibrosis gene: genetic analysis. Science 1989;245: 1073-80.
-
(1989)
Science
, vol.245
, pp. 1073-1080
-
-
Kerem, B.1
Rommens, J.M.2
Buchanan, J.A.3
-
6
-
-
0020700816
-
Chloride impermeability in cystic fibrosis
-
Quinton PM. Chloride impermeability in cystic fibrosis. Nature 1983;301:421-2.
-
(1983)
Nature
, vol.301
, pp. 421-422
-
-
Quinton, P.M.1
-
7
-
-
0022970788
-
Missing Cl conductance in cystic fibrosis
-
Quinten PM. Missing Cl conductance in cystic fibrosis. Am J Physiol 1986;251:C649-C652.
-
(1986)
Am J Physiol
, vol.251
-
-
Quinten, P.M.1
-
8
-
-
0019809960
-
Increased bioelectric potential differences across respiratory epithelial in cystic fibrosis
-
Knowles MR, Gatzy J, Boucher RC. Increased bioelectric potential differences across respiratory epithelial in cystic fibrosis. N Engl J Med 1981;305:1489-98.
-
(1981)
N Engl J Med
, vol.305
, pp. 1489-1498
-
-
Knowles, M.R.1
Gatzy, J.2
Boucher, R.C.3
-
9
-
-
0020610435
-
Abnormal ion permeation through cystic fibrosis respiratory epithelium
-
Knowles MR, Stutts MJ, Spock A, et al. Abnormal ion permeation through cystic fibrosis respiratory epithelium. Science 1983;221:1067-70.
-
(1983)
Science
, vol.221
, pp. 1067-1070
-
-
Knowles, M.R.1
Stutts, M.J.2
Spock, A.3
-
10
-
-
0000026508
-
Cystic fibrosis
-
Scriver CR, Beaudet AL, Sly WS, Valle D, eds. New York: McGraw-Hill
-
Welsh MJ, Tsui-L-C, Boat TF, et al. Cystic fibrosis, In: Scriver CR, Beaudet AL, Sly WS, Valle D, eds. The metabolic and molecular bases of inherited disease. 7th ed. vol. 3, New York: McGraw-Hill, 1995:799-1876.
-
(1995)
The Metabolic and Molecular Bases of Inherited Disease. 7th Ed.
, vol.3
, pp. 799-1876
-
-
Welsh, M.J.1
Tsui, L.C.2
Boat, T.F.3
-
11
-
-
0029019461
-
Cystic fibrosis transmembrane conductance regulator and obstructive azoospermia
-
Jarvi K, Zielenski J, Wilschanski M, et al. Cystic fibrosis transmembrane conductance regulator and obstructive azoospermia. Lancet 1995;345:1578.
-
(1995)
Lancet
, vol.345
, pp. 1578
-
-
Jarvi, K.1
Zielenski, J.2
Wilschanski, M.3
-
12
-
-
85030306340
-
The diagnosis of cystic fibrosis: Consensus statement
-
Section I. CF Foundation, Bethesda, MD
-
Boat TF, et al. The diagnosis of cystic fibrosis: consensus statement. Clinical practice guidelines for CF, consensus conferences. Vol. VII, Section I. CF Foundation, Bethesda, MD, 1996.
-
(1996)
Clinical Practice Guidelines for CF, Consensus Conferences
, vol.7
-
-
Boat, T.F.1
-
13
-
-
0028910076
-
The cystic fibrosis transmembrane conductance regulator gene
-
Tsui LC. The cystic fibrosis transmembrane conductance regulator gene. Am J Respir Crit Care Med 1995;151:S47-S53.
-
(1995)
Am J Respir Crit Care Med
, vol.151
-
-
Tsui, L.C.1
-
14
-
-
0028940005
-
Functions of the cystic fibrosis transmembrane conductance protein
-
Frizzell RA. Functions of the cystic fibrosis transmembrane conductance protein. Am J Respir Crit Care Med 1995;151:S54-S58.
-
(1995)
Am J Respir Crit Care Med
, vol.151
-
-
Frizzell, R.A.1
-
15
-
-
0026732670
-
Cystic fibrosis transmembrane conductance regulator and the etiology and pathogenesis of cystic fibrosis
-
McIntosh I, Cutting GR. Cystic fibrosis transmembrane conductance regulator and the etiology and pathogenesis of cystic fibrosis. FASEB J 1992;6:2775-82.
-
(1992)
FASEB J
, vol.6
, pp. 2775-2782
-
-
McIntosh, I.1
Cutting, G.R.2
-
16
-
-
0026763138
-
Cystic fibrosis transmembrane conductance regulator: A chloride channel with novel regulation
-
Welsh MJ, Anderson MP, Rich DP, et al. Cystic fibrosis transmembrane conductance regulator: a chloride channel with novel regulation. Neuron 1982;8:821-9.
-
(1982)
Neuron
, vol.8
, pp. 821-829
-
-
Welsh, M.J.1
Anderson, M.P.2
Rich, D.P.3
-
17
-
-
0026523829
-
Cystic fibrosis: Molecular biology and therapeutic implications
-
Collins FS. Cystic fibrosis: molecular biology and therapeutic implications. Science 1992;256:774-9.
-
(1992)
Science
, vol.256
, pp. 774-779
-
-
Collins, F.S.1
-
18
-
-
0027191065
-
CFTR and outward rec- Tifying chloride channels are distinct proteins with a regulatory relationship
-
Gabriel SE, Clarke LL, Boucher RC, et al. CFTR and outward rec- tifying chloride channels are distinct proteins with a regulatory relationship. Nature 1993;393:263-6.
-
(1993)
Nature
, vol.393
, pp. 263-266
-
-
Gabriel, S.E.1
Clarke, L.L.2
Boucher, R.C.3
-
19
-
-
0029871744
-
Phosphorylation-dependent block of CFTR chloride channel by exogenous R domain protein
-
Ma J, Tasch JE, Tao T, et al. Phosphorylation-dependent block of CFTR chloride channel by exogenous R domain protein. J Biol Chem 1995;271:7351-6.
-
(1995)
J Biol Chem
, vol.271
, pp. 7351-7356
-
-
Ma, J.1
Tasch, J.E.2
Tao, T.3
-
20
-
-
0025987020
-
Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channels
-
Cheng SH, Rich DP, Marshall J, et al. Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channels. Cell 1991;66:1027-6.
-
(1991)
Cell
, vol.66
, pp. 1027-1036
-
-
Cheng, S.H.1
Rich, D.P.2
Marshall, J.3
-
22
-
-
0025776409
-
The cystic fibrosis gene has a "housekeeping"-type promoter and is expressed at low levels in cells of epithelial origin
-
Yoshimura K, Nakamura H, Trapnell BC, et al. The cystic fibrosis gene has a "housekeeping"-type promoter and is expressed at low levels in cells of epithelial origin. J Biol Chem 1991;266:9140-4.
-
(1991)
J Biol Chem
, vol.266
, pp. 9140-9144
-
-
Yoshimura, K.1
Nakamura, H.2
Trapnell, B.C.3
-
23
-
-
84920211040
-
Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas
-
diSant'Agnese PA, Darling RC, Perera GA, et al. Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas. Pediatrics 1953;12:549-63.
-
(1953)
Pediatrics
, vol.12
, pp. 549-563
-
-
DiSanT'Agnese, P.A.1
Darling, R.C.2
Perera, G.A.3
-
24
-
-
9244225677
-
A test for concentration of electrolytes in sweat in cystic fibrosis of the pancreas utilizing pilocarpine iontophoresis
-
Gibson LE, Cooke RE. A test for concentration of electrolytes in sweat in cystic fibrosis of the pancreas utilizing pilocarpine iontophoresis. Pediatrics 1959;23:545-9.
-
(1959)
Pediatrics
, vol.23
, pp. 545-549
-
-
Gibson, L.E.1
Cooke, R.E.2
-
25
-
-
0018520720
-
Cystic fibrosis with acute hypoelectrolytemia and metabolic alkalosis in infancy
-
Nussbaum E, Boat TF, Wood RE, et al. Cystic fibrosis with acute hypoelectrolytemia and metabolic alkalosis in infancy. Am J Dis Child 1979;133:965-6.
-
(1979)
Am J Dis Child
, vol.133
, pp. 965-966
-
-
Nussbaum, E.1
Boat, T.F.2
Wood, R.E.3
-
26
-
-
0018341373
-
Hypoelectrolytemia and metabolic alkalosis in infants with cystic fibrosis
-
Beckerman RC, Taussig LM. Hypoelectrolytemia and metabolic alkalosis in infants with cystic fibrosis. Pediatrics 1979;63:580-3.
-
(1979)
Pediatrics
, vol.63
, pp. 580-583
-
-
Beckerman, R.C.1
Taussig, L.M.2
-
27
-
-
0021917723
-
Pancreatic fluid secretion and protein hyperconcentration in cystic fibrosis
-
Kopelman H, Dune P, Gaskin K, et al. Pancreatic fluid secretion and protein hyperconcentration in cystic fibrosis. N Engl J Med 1985;312:329-34.
-
(1985)
N Engl J Med
, vol.312
, pp. 329-334
-
-
Kopelman, H.1
Dune, P.2
Gaskin, K.3
-
28
-
-
0023719216
-
Impaired chloride secretion, as well as bicarbonate secretion, underlies the fluid secretory defect in the cystic fibrosis pancreas
-
Kopelman H, Corey M, Gaskin K, et al. Impaired chloride secretion, as well as bicarbonate secretion, underlies the fluid secretory defect in the cystic fibrosis pancreas. Gastroenterology 1988;95:349-55.
-
(1988)
Gastroenterology
, vol.95
, pp. 349-355
-
-
Kopelman, H.1
Corey, M.2
Gaskin, K.3
-
29
-
-
0041857366
-
The pancreas in cystic fibrosis
-
Davis PB, ed. New York: Marcel Dekker
-
Cotton CU, Davis PB. The pancreas in cystic fibrosis. In: Davis PB, ed. Cystic fibrosis. New York: Marcel Dekker, 1993:161-92.
-
(1993)
Cystic Fibrosis
, pp. 161-192
-
-
Cotton, C.U.1
Davis, P.B.2
-
30
-
-
0026505294
-
Pancreatitis in young children with cystic fibrosis
-
Atlas AB, Orenstein SR, Orenstein DM. Pancreatitis in young children with cystic fibrosis. J Pediatr 1992;120:756-9.
-
(1992)
J Pediatr
, vol.120
, pp. 756-759
-
-
Atlas, A.B.1
Orenstein, S.R.2
Orenstein, D.M.3
-
31
-
-
0042150584
-
CF and the gastrointestinal tract
-
Davis PB, ed: New York: Marcel Dekker
-
Stern RC. CF and the gastrointestinal tract. In: Davis PB, ed: Cystic fibrosis. New York: Marcel Dekker, 1993:401-34.
-
(1993)
Cystic Fibrosis
, pp. 401-434
-
-
Stern, R.C.1
-
32
-
-
0002121738
-
The pathology of cystic fibrosis
-
Davis PB, ed. New York: Marcel Dekker
-
Tomashefski JF, Abramowsky CR, Dahms BB. The pathology of cystic fibrosis. In: Davis PB, ed. Cystic fibrosis. New York: Marcel Dekker, 1993:435-590.
-
(1993)
Cystic Fibrosis
, pp. 435-590
-
-
Tomashefski, J.F.1
Abramowsky, C.R.2
Dahms, B.B.3
-
34
-
-
0022973473
-
+ transport in cystic fibrosis respiratory epithelia: Abnormal basal rate and response to adenylate cyclase activation
-
+ transport in cystic fibrosis respiratory epithelia: abnormal basal rate and response to adenylate cyclase activation. J Clin Invest 1986;78:1245-52.
-
(1986)
J Clin Invest
, vol.78
, pp. 1245-1252
-
-
Boucher, R.C.1
Stutts, M.J.2
Knowles, M.R.3
-
35
-
-
0028982894
-
CFTR as a cAMP-dependent regulator of sodium channels
-
Stutts MJ, Canessa CM, Olsen JC, et al. CFTR as a cAMP-dependent regulator of sodium channels. Science 1995;269:847-50.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
-
37
-
-
0030949875
-
Human β-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis
-
Goldman MJ, Anderson GM, Stolzenberg ED, et al. Human β-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis. Cell 1997;88:553-60.
-
(1997)
Cell
, vol.88
, pp. 553-560
-
-
Goldman, M.J.1
Anderson, G.M.2
Stolzenberg, E.D.3
-
38
-
-
85030304763
-
-
May 23
-
Cystic Fibrosis Genetic Analysis Consortium. (Consortium Newsletter, May 23, 1996); Website: http://www.genet.sickkids.on.ca/daniel-cgi-bin/news?news=68.
-
(1996)
Consortium Newsletter
-
-
-
39
-
-
0007696559
-
Genetic aspects of cystic fibrosis
-
Human BC, ed. Philadelphia: W B Saunders
-
Klinger K. Genetic aspects of cystic fibrosis. In: Human BC, ed. Pediatric respiratory disease. Philadelphia: W B Saunders, 1993:652-60.
-
(1993)
Pediatric Respiratory Disease
, pp. 652-660
-
-
Klinger, K.1
-
40
-
-
85030304002
-
70 Mutation cystic fibrosis test
-
Framingham, MA
-
Genzyme Corporation. 70 Mutation cystic fibrosis test. Genzyme Genetics, Framingham, MA, 1997.
-
(1997)
Genzyme Genetics
-
-
-
41
-
-
0026503640
-
Association of a nonsense mutation (W1282X), the most common mutation in the Ashkenazi Jewish cystic fibrosis patients in Israel, with presentation of severe disease
-
Shoshani T, Augarten A, Gazit E, et al. Association of a nonsense mutation (W1282X), the most common mutation in the Ashkenazi Jewish cystic fibrosis patients in Israel, with presentation of severe disease. Am J Hum Genet 1992;50:222-8.
-
(1992)
Am J Hum Genet
, vol.50
, pp. 222-228
-
-
Shoshani, T.1
Augarten, A.2
Gazit, E.3
-
42
-
-
0029866870
-
The molecular basis for disease variability in cystic fibrosis
-
Kerem B, Kerem E. The molecular basis for disease variability in cystic fibrosis. Eur J Hum Genet 1996;4:65-73.
-
(1996)
Eur J Hum Genet
, vol.4
, pp. 65-73
-
-
Kerem, B.1
Kerem, E.2
-
43
-
-
0026937999
-
CFTR nonsense mutations G542X and W1282X associated with severe reduction of CFTR mRNA in nasal epithelial cells
-
Hamosh A, Rosenstein BJ, Cutting GR. CFTR nonsense mutations G542X and W1282X associated with severe reduction of CFTR mRNA in nasal epithelial cells. Hum Mol Genet 1992;1:542-4.
-
(1992)
Hum Mol Genet
, vol.1
, pp. 542-544
-
-
Hamosh, A.1
Rosenstein, B.J.2
Cutting, G.R.3
-
44
-
-
0025906695
-
Variable deletion of exon 9 coding sequences in cystic fibrosis transmembrane conductance regulator gene mRNA transcripts in normal bronchial epithelium
-
Chu CS, Trapnell BC, Murtagh JJ, et al. Variable deletion of exon 9 coding sequences in cystic fibrosis transmembrane conductance regulator gene mRNA transcripts in normal bronchial epithelium. E. M. B. O. J. 1991;10:1355-63.
-
(1991)
E. M. B. O. J.
, vol.10
, pp. 1355-1363
-
-
Chu, C.S.1
Trapnell, B.C.2
Murtagh, J.J.3
-
45
-
-
0029616734
-
Cystic fibrosis: Genotypic and phenotypic variations
-
Zielenski J, Tsui LC. Cystic fibrosis: genotypic and phenotypic variations. Ann Rev Genetics 1995;29:777-807.
-
(1995)
Ann Rev Genetics
, vol.29
, pp. 777-807
-
-
Zielenski, J.1
Tsui, L.C.2
-
47
-
-
0028929909
-
Mechanism of dysfunction of two nucleotide binding domain mutations in cystic fibrosis transmembrane conductance regulator that are associated with pancreatic sufficiency
-
Sheppard DN, Ostedgaard LS, Winter MC, et al. Mechanism of dysfunction of two nucleotide binding domain mutations in cystic fibrosis transmembrane conductance regulator that are associated with pancreatic sufficiency. E. M. B. O. J. 1995;14:876-83.
-
(1995)
E. M. B. O. J.
, vol.14
, pp. 876-883
-
-
Sheppard, D.N.1
Ostedgaard, L.S.2
Winter, M.C.3
-
48
-
-
0020070795
-
Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption
-
Gaskin K, Gurwitz D, Durie M, et al. Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption. J Pediatr 1982;100:857-62.
-
(1982)
J Pediatr
, vol.100
, pp. 857-862
-
-
Gaskin, K.1
Gurwitz, D.2
Durie, M.3
-
49
-
-
0028086056
-
A novel mutation in the cystic fibrosis gene in patients with pulmonary disease but normal sweat chloride concentrations
-
Highsmith WE, Burch LH, Zhou Z, et al. A novel mutation in the cystic fibrosis gene in patients with pulmonary disease but normal sweat chloride concentrations. N Engl J Med 1994;331:974-80.
-
(1994)
N Engl J Med
, vol.331
, pp. 974-980
-
-
Highsmith, W.E.1
Burch, L.H.2
Zhou, Z.3
-
50
-
-
0027278161
-
Mild cystic fibrosis and normal or borderline sweat test in patients with the 3849+10kb C→T mutation
-
Augarten A, Kerem B-S, Yahav Y, et al. Mild cystic fibrosis and normal or borderline sweat test in patients with the 3849+10kb C→T mutation. Lancet 1993;342:25-6.
-
(1993)
Lancet
, vol.342
, pp. 25-26
-
-
Augarten, A.1
Kerem, B.-S.2
Yahav, Y.3
-
51
-
-
0030071693
-
Cystic fibrosis 3849+10kb C→T mutation associated with severe pulmonary disease and male fertility
-
Dreyfus DH, Bethel R, Gelfand EW. Cystic fibrosis 3849+10kb C→T mutation associated with severe pulmonary disease and male fertility. Am J Respir Crit Care Med 1996;153:858-60.
-
(1996)
Am J Respir Crit Care Med
, vol.153
, pp. 858-860
-
-
Dreyfus, D.H.1
Bethel, R.2
Gelfand, E.W.3
-
52
-
-
0026562867
-
Congenital bilateral absence of the vas deferens. A primarily genital form of cystic fibrosis
-
Anguiano A, Oates RD, Amos JA, et al. Congenital bilateral absence of the vas deferens. A primarily genital form of cystic fibrosis. JAMA 1992;267:1794-7.
-
(1992)
JAMA
, vol.267
, pp. 1794-1797
-
-
Anguiano, A.1
Oates, R.D.2
Amos, J.A.3
-
53
-
-
0029025333
-
Mutations in the cystic fibrosis gene in patients with congenital absence of the vas deferens
-
Chillon MT, Casals T, Mercier B, et al. Mutations in the cystic fibrosis gene in patients with congenital absence of the vas deferens. N Engl J Med 1995;332:1475-80.
-
(1995)
N Engl J Med
, vol.332
, pp. 1475-1480
-
-
Chillon, M.T.1
Casals, T.2
Mercier, B.3
-
54
-
-
0027521663
-
A mutation in CFTR produces different phenotypes depending on chromosomal background
-
Kiesewetter S, Macek MJ, Davis C, et al. A mutation in CFTR produces different phenotypes depending on chromosomal background. Nat Genet 1993;5:274-7.
-
(1993)
Nat Genet
, vol.5
, pp. 274-277
-
-
Kiesewetter, S.1
Macek, M.J.2
Davis, C.3
-
55
-
-
0027502580
-
Genetic basis of variable exon 9 skipping in cystic fibrosis transmembrane conductance regulator mRNA
-
Chu CS, Trapnell BC, Curriston S, et al. Genetic basis of variable exon 9 skipping in cystic fibrosis transmembrane conductance regulator mRNA. Nat Genet 1993;3:151-6.
-
(1993)
Nat Genet
, vol.3
, pp. 151-156
-
-
Chu, C.S.1
Trapnell, B.C.2
Curriston, S.3
-
56
-
-
0027310434
-
Expression of an abundant alternatively spliced form of cystic fibrosis transmembrane conductance regulator (CFTR) gene is not associated with a cAMP-activated chloride conductance
-
Strong TV, Wilkinson DJ, Mansoura MK, et al. Expression of an abundant alternatively spliced form of cystic fibrosis transmembrane conductance regulator (CFTR) gene is not associated with a cAMP-activated chloride conductance. Hum Mol Genet 1993;2:225-30.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 225-230
-
-
Strong, T.V.1
Wilkinson, D.J.2
Mansoura, M.K.3
-
57
-
-
0347794426
-
Correlation of the level of full-length CFTR transcript with pulmonary phenotype in patients carrying R117H and 1342-1, -2 delAG mutation
-
Hamosh A, Oates R, Amos J, et al. Correlation of the level of full-length CFTR transcript with pulmonary phenotype in patients carrying R117H and 1342-1, -2 delAG mutation. Pediatr Pulmonol(Suppl)1994;10:124A.
-
(1994)
Pediatr Pulmonol(Suppl)
, vol.10
-
-
Hamosh, A.1
Oates, R.2
Amos, J.3
-
59
-
-
0029882475
-
The sweat test for quantitation of electrolytes: A challenge in precision
-
Constantinescu M, Hilman BC. The sweat test for quantitation of electrolytes: a challenge in precision. Lab Med 1996;27:472-7.
-
(1996)
Lab Med
, vol.27
, pp. 472-477
-
-
Constantinescu, M.1
Hilman, B.C.2
-
60
-
-
0030365197
-
Sweat testing for the diagnosis of cystic fibrosis: Practical considerations
-
LeGrys VA. Sweat testing for the diagnosis of cystic fibrosis: practical considerations. J Pediatr 1996;129:892-7.
-
(1996)
J Pediatr
, vol.129
, pp. 892-897
-
-
LeGrys, V.A.1
-
62
-
-
0028309683
-
Human airway ion transport
-
Boucher RC. Human airway ion transport. Am J Respir Crit Care Med 1994;150:271-81, 581-93.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 271-281
-
-
Boucher, R.C.1
-
63
-
-
0020596438
-
Relative ion permeability of normal and cystic fibrosis epithelium
-
Knowles MR, Gatzy J, Boucher RC. Relative ion permeability of normal and cystic fibrosis epithelium. J Clin Invest 1983;71:1410-8.
-
(1983)
J Clin Invest
, vol.71
, pp. 1410-1418
-
-
Knowles, M.R.1
Gatzy, J.2
Boucher, R.C.3
-
64
-
-
0025609981
-
Nasal potential difference: A clinical diagnostic test for cystic fibrosis
-
Alton EW, Currie D, Logan-Sinclair R, et al. Nasal potential difference: a clinical diagnostic test for cystic fibrosis. Eur Respir J 1990;3:922-6.
-
(1990)
Eur Respir J
, vol.3
, pp. 922-926
-
-
Alton, E.W.1
Currie, D.2
Logan-Sinclair, R.3
-
65
-
-
0026698816
-
Localization of cystic fibrosis transmembrane conductance regulator mRNA in human fetal lung tissue by in situ hybridization
-
McCray PB Jr, Wohlford-Lenane CL, Snyder JM. Localization of cystic fibrosis transmembrane conductance regulator mRNA in human fetal lung tissue by in situ hybridization. J Clin Invest 1992;90:619-25.
-
(1992)
J Clin Invest
, vol.90
, pp. 619-625
-
-
McCray Jr., P.B.1
Wohlford-Lenane, C.L.2
Snyder, J.M.3
-
66
-
-
0027546872
-
Cystic fibrosis gene and protein expression during fetal lung development
-
McGrath SA, Basu A, Zeitlin PL. Cystic fibrosis gene and protein expression during fetal lung development. Am J Respir Cell Mol Biol 1993;8:201-8.
-
(1993)
Am J Respir Cell Mol Biol
, vol.8
, pp. 201-208
-
-
McGrath, S.A.1
Basu, A.2
Zeitlin, P.L.3
-
67
-
-
0020082418
-
Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants
-
Sturgess J, Imrie J. Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants. Am J Pathol 1982;106:303-11.
-
(1982)
Am J Pathol
, vol.106
, pp. 303-311
-
-
Sturgess, J.1
Imrie, J.2
-
68
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
Khan TZ, Wagener JS, Bost T, et al. Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med 1995;151:1075-82.
-
(1995)
Am J Respir Crit Care Med
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
-
69
-
-
0029010510
-
Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis
-
Armstrong DS, Grimwood K, Carzino R, et al. Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis. Brit Med J 1995;310:1571-2.
-
(1995)
Brit Med J
, vol.310
, pp. 1571-1572
-
-
Armstrong, D.S.1
Grimwood, K.2
Carzino, R.3
-
70
-
-
0029346937
-
The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis
-
Balough K, McCubbin M, Weinberger M, et al. The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis. Pediatr Pulmonol 1995;20:63-70.
-
(1995)
Pediatr Pulmonol
, vol.20
, pp. 63-70
-
-
Balough, K.1
McCubbin, M.2
Weinberger, M.3
-
71
-
-
0002005094
-
BALF PCR and ELISA identification of non-culturable Pseudomonas aeruginosa in infants and toddlers with cystic fibrosis
-
Copenhaver S, Sage A, Vasil A, et al. BALF PCR and ELISA identification of non-culturable Pseudomonas aeruginosa in infants and toddlers with cystic fibrosis. Pediatr Pulmonol (Suppl)1996;13:291A.
-
(1996)
Pediatr Pulmonol (Suppl)
, vol.13
-
-
Copenhaver, S.1
Sage, A.2
Vasil, A.3
-
72
-
-
0028015883
-
Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
-
Konstan MW, Milliard HA, Norvell TM, et al. Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation. Am J Respir Crit Care Med 1994;150:448-54.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 448-454
-
-
Konstan, M.W.1
Milliard, H.A.2
Norvell, T.M.3
-
74
-
-
0029372481
-
Normal bronchial epithelial cells consistently produce the anti-inflammatory cytokine/interleukin-10, which is downregulated in cystic fibrosis
-
Bonfield TL, Konstan MW, Burfeind P, et al. Normal bronchial epithelial cells consistently produce the anti-inflammatory cytokine/interleukin-10, which is downregulated in cystic fibrosis. Am J Respir Cell Mol Biol 1995;13:257-61.
-
(1995)
Am J Respir Cell Mol Biol
, vol.13
, pp. 257-261
-
-
Bonfield, T.L.1
Konstan, M.W.2
Burfeind, P.3
-
75
-
-
0026687233
-
Defective regulation of outwardly rectifying Cl channels by protein kinase A corrected by insertion of CFTR
-
Egan M, Flotte T, Afione S, et al. Defective regulation of outwardly rectifying Cl channels by protein kinase A corrected by insertion of CFTR. Nature 1992;358:581-4.
-
(1992)
Nature
, vol.358
, pp. 581-584
-
-
Egan, M.1
Flotte, T.2
Afione, S.3
-
76
-
-
0026681802
-
Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line
-
Nakamura H, Yoshimura K, McElvaney NG, et al. Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line. J Clin Invest 1992;89:1478-84.
-
(1992)
J Clin Invest
, vol.89
, pp. 1478-1484
-
-
Nakamura, H.1
Yoshimura, K.2
McElvaney, N.G.3
-
77
-
-
0021783739
-
Biochemical and pathologic evidence for proteolytic destruction of lung connective tissue in cystic fibrosis
-
Bruce MC, Poncz L, Klinger JD, et al. Biochemical and pathologic evidence for proteolytic destruction of lung connective tissue in cystic fibrosis. Am Rev Respir Dis 1985;132:529-35.
-
(1985)
Am Rev Respir Dis
, vol.132
, pp. 529-535
-
-
Bruce, M.C.1
Poncz, L.2
Klinger, J.D.3
-
78
-
-
0021239746
-
Proteins of the cystic fibrosis respiratory tract. Fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis
-
Pick RB Jr, Nagel GP, Squier SU, et al. Proteins of the cystic fibrosis respiratory tract. Fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis. J Clin Invest 1984;74:236-48.
-
(1984)
J Clin Invest
, vol.74
, pp. 236-248
-
-
Pick Jr., R.B.1
Nagel, G.P.2
Squier, S.U.3
-
79
-
-
0024459145
-
Complement receptor expression on neutrophils at an inflammatory site, the Pseudomonas-infected lung in cystic fibrosis
-
Berger M, Sorensen RU, Tosi MF, et al. Complement receptor expression on neutrophils at an inflammatory site, the Pseudomonas-infected lung in cystic fibrosis. J Clin Invest 1989;84:1302-13.
-
(1989)
J Clin Invest
, vol.84
, pp. 1302-1313
-
-
Berger, M.1
Sorensen, R.U.2
Tosi, M.F.3
-
80
-
-
0025374923
-
Neutrophil elastase cleaves C3bi on opsonized Pseudomonas as well as CR1 in neutrophils to create a functionally important opsonin receptor mismatch
-
Tosi MF, Zakem H, Berger M. Neutrophil elastase cleaves C3bi on opsonized Pseudomonas as well as CR1 in neutrophils to create a functionally important opsonin receptor mismatch. J Clin Invest 1990;86:300-8.
-
(1990)
J Clin Invest
, vol.86
, pp. 300-308
-
-
Tosi, M.F.1
Zakem, H.2
Berger, M.3
-
81
-
-
0029870085
-
Cystic fibrosis airway epithelia fail to kill bacteria be- Cause of abnormal airway surface fluid
-
Smith JJ, Travis SM, Greenberg EP, et al. Cystic fibrosis airway epithelia fail to kill bacteria be- cause of abnormal airway surface fluid. Cell 1996;85:229-36.
-
(1996)
Cell
, vol.85
, pp. 229-236
-
-
Smith, J.J.1
Travis, S.M.2
Greenberg, E.P.3
-
82
-
-
0000125109
-
Transient pulmonary infiltrations in cystic fibrosis due to aspergillosis
-
Mearns M, Young W, Batten J. Transient pulmonary infiltrations in cystic fibrosis due to aspergillosis. Thorax 1995;20:385-92.
-
(1995)
Thorax
, vol.20
, pp. 385-392
-
-
Mearns, M.1
Young, W.2
Batten, J.3
-
83
-
-
0026040220
-
Variability in parameters of allergic bronchopulmonary aspergillosis in patients with cystic fibrosis
-
Hutchespn PS, Rejent AJ, Slavin RG. Variability in parameters of allergic bronchopulmonary aspergillosis in patients with cystic fibrosis. J Allergy Clin Immunol 1991;88:390-4.
-
(1991)
J Allergy Clin Immunol
, vol.88
, pp. 390-394
-
-
Hutchespn, P.S.1
Rejent, A.J.2
Slavin, R.G.3
-
84
-
-
1542433158
-
Allergic aspergillosis: Cystic fibrosis
-
Batten JC. Allergic aspergillosis: cystic fibrosis. Mod Probl Pediatr 1967;10:227-32.
-
(1967)
Mod Probl Pediatr
, vol.10
, pp. 227-232
-
-
Batten, J.C.1
-
86
-
-
0018934438
-
Allergic bronchopulmonary aspergillosis complicating cystic fibrosis in childhood
-
Brueton MJ, Ormerod LP, Shah KJ, et al. Allergic bronchopulmonary aspergillosis complicating cystic fibrosis in childhood. Arch Dis Child 1980;55:348-53.
-
(1980)
Arch Dis Child
, vol.55
, pp. 348-353
-
-
Brueton, M.J.1
Ormerod, L.P.2
Shah, K.J.3
-
87
-
-
84980207961
-
Allergic bronchopulmonary aspergillosis in cystic fibrosis
-
Henry R, Mellis C, Simpson S, et al. Allergic bronchopulmonary aspergillosis in cystic fibrosis. Aust Paediatr J 1982;18:110-3.
-
(1982)
Aust Paediatr J
, vol.18
, pp. 110-113
-
-
Henry, R.1
Mellis, C.2
Simpson, S.3
-
88
-
-
0021327925
-
Allergic bronchopulmonary aspergillosis in cystic fibrosis
-
Laufer P, Fink J, Bruns W, et al. Allergic bronchopulmonary aspergillosis in cystic fibrosis. J Allergy Clin Immunol 1984;73:44-8.
-
(1984)
J Allergy Clin Immunol
, vol.73
, pp. 44-48
-
-
Laufer, P.1
Fink, J.2
Bruns, W.3
-
89
-
-
0030009088
-
Prevalence of allergic bronchopulmonary aspergillosis and atopy in adult patients with cystic fibrosis
-
Becker JW, Burke W, McDonald G, et al. Prevalence of allergic bronchopulmonary aspergillosis and atopy in adult patients with cystic fibrosis. Chest 1996;109:1536-40.
-
(1996)
Chest
, vol.109
, pp. 1536-1540
-
-
Becker, J.W.1
Burke, W.2
McDonald, G.3
-
90
-
-
0022518392
-
Diagnosis and management of allergic bronchopulmonary aspergillosis
-
Greenberger P, Patterson R. Diagnosis and management of allergic bronchopulmonary aspergillosis. Ann Allergy 1986;56:444-8.
-
(1986)
Ann Allergy
, vol.56
, pp. 444-448
-
-
Greenberger, P.1
Patterson, R.2
-
91
-
-
0025153035
-
Computer tomography in the evaluation of allergic bronchopulmonary aspergillosis
-
Neeld O, Goodman L, Gurney J, et al. Computer tomography in the evaluation of allergic bronchopulmonary aspergillosis. Am Rev Respir Dis 1990;142:1200-5.
-
(1990)
Am Rev Respir Dis
, vol.142
, pp. 1200-1205
-
-
Neeld, O.1
Goodman, L.2
Gurney, J.3
-
92
-
-
0029154030
-
Identification of allergic bronchopulmonary aspergillosis in cystic fibrosis patients by recombinant Aspergillus fumigatus I/a-Specific Serology
-
Nikolaizik WH, Moser M, Crameri R, et al. Identification of allergic bronchopulmonary aspergillosis in cystic fibrosis patients by recombinant Aspergillus fumigatus I/a-Specific Serology. Am J Respir Crit Care Med 1995;152:634-9.
-
(1995)
Am J Respir Crit Care Med
, vol.152
, pp. 634-639
-
-
Nikolaizik, W.H.1
Moser, M.2
Crameri, R.3
-
93
-
-
0029818295
-
Skin test reactivity to recombinant Aspergillus fumigatus allergen I/a in patients with cystic fibrosis
-
Nikolaizik WH, Crameri R, Blaser K, et al. Skin test reactivity to recombinant Aspergillus fumigatus allergen I/a in patients with cystic fibrosis. Int Arch Allergy Immunol 1996;111:403-8.
-
(1996)
Int Arch Allergy Immunol
, vol.111
, pp. 403-408
-
-
Nikolaizik, W.H.1
Crameri, R.2
Blaser, K.3
-
94
-
-
1842367349
-
-
CF Foundation, Bethesda, MD
-
Cystic Fibrosis Foundation. 1997. 1996 Annual Patient Data Registry, CF Foundation, Bethesda, MD.
-
(1997)
1996 Annual Patient Data Registry
-
-
-
95
-
-
0015620179
-
The variable effect of a bronchodilating agent on pulmonary function in cystic fibrosis
-
Landau LI, Phelan PD. The variable effect of a bronchodilating agent on pulmonary function in cystic fibrosis. J Pediatr 1973;82:863-8.
-
(1973)
J Pediatr
, vol.82
, pp. 863-868
-
-
Landau, L.I.1
Phelan, P.D.2
-
96
-
-
0018758250
-
A comparative study of inhaled atropine sulfate and iso-proterenol hydrochloride in cystic fibrosis
-
Larsen GL, Barron RJ, Cotton EK, et al. A comparative study of inhaled atropine sulfate and iso-proterenol hydrochloride in cystic fibrosis. Am Rev Respir Dis 1979;119:399-407.
-
(1979)
Am Rev Respir Dis
, vol.119
, pp. 399-407
-
-
Larsen, G.L.1
Barron, R.J.2
Cotton, E.K.3
-
97
-
-
0018927212
-
Response to aerosol salbutamol, SCH 1000, and placebo in cystic fibrosis
-
Kattan M, Mansell A, Levison H, et al. Response to aerosol salbutamol, SCH 1000, and placebo in cystic fibrosis. Thorax 1980;35:531-5.
-
(1980)
Thorax
, vol.35
, pp. 531-535
-
-
Kattan, M.1
Mansell, A.2
Levison, H.3
-
98
-
-
0019129438
-
Reversible airway obstruction in cystic fibrosis
-
Ormerol LP, Thomson RA, Anderson CM, et al. Reversible airway obstruction in cystic fibrosis. Thorax 1980;35:768-72.
-
(1980)
Thorax
, vol.35
, pp. 768-772
-
-
Ormerol, L.P.1
Thomson, R.A.2
Anderson, C.M.3
-
100
-
-
0021845941
-
A longitudinal study of bronchodilator responsiveness in cystic fibrosis
-
Hordvik NL, Konig P, Morris D, et al. A longitudinal study of bronchodilator responsiveness in cystic fibrosis. Am Rev Respir Dis 1985;131:889-93.
-
(1985)
Am Rev Respir Dis
, vol.131
, pp. 889-893
-
-
Hordvik, N.L.1
Konig, P.2
Morris, D.3
-
101
-
-
0021848184
-
Bronchodilators increase airway instability in cystic fibrosis
-
Zach MS, Oberwaldner B, Forche G, et al. Bronchodilators increase airway instability in cystic fibrosis. Am Rev Respir Dis 1985;131:537-43.
-
(1985)
Am Rev Respir Dis
, vol.131
, pp. 537-543
-
-
Zach, M.S.1
Oberwaldner, B.2
Forche, G.3
-
102
-
-
0023819109
-
Bronchodilator responsiveness in infants and young children with cystic fibrosis
-
Hiatt P, Eigen H, Yu P, et al. Bronchodilator responsiveness in infants and young children with cystic fibrosis. Am Rev Respir Dis 1988;137:119-22.
-
(1988)
Am Rev Respir Dis
, vol.137
, pp. 119-122
-
-
Hiatt, P.1
Eigen, H.2
Yu, P.3
-
103
-
-
0024985472
-
Longitudinal response of pulmonary function to bronchodilators in cystic fibrosis
-
Pattishall EN. Longitudinal response of pulmonary function to bronchodilators in cystic fibrosis. Pediatr Pulmonol 1990;9:80-5.
-
(1990)
Pediatr Pulmonol
, vol.9
, pp. 80-85
-
-
Pattishall, E.N.1
-
104
-
-
0029383649
-
Short-term and long-term effects of albuterol aerosol therapy in cysticfibrosis: A preliminary report
-
König P, Gayer D, Barbero GJ, et al. Short-term and long-term effects of albuterol aerosol therapy in cysticfibrosis: a preliminary report. Pediatr Pulmonol 1995;20:205-14.
-
(1995)
Pediatr Pulmonol
, vol.20
, pp. 205-214
-
-
König, P.1
Gayer, D.2
Barbero, G.J.3
-
105
-
-
0025223381
-
Regular inhaled beta agonist treatment in bronchial asthma
-
Sears MR, Taylor OR, Print CG, et al. Regular inhaled beta agonist treatment in bronchial asthma. Lancet 1990;336:1391-6.
-
(1990)
Lancet
, vol.336
, pp. 1391-1396
-
-
Sears, M.R.1
Taylor, O.R.2
Print, C.G.3
-
106
-
-
0028129568
-
Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
-
Fuchs HJ, Borowitz DS, Chris- tiansen DH, et al. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med 1994;331:637-42.
-
(1994)
N Engl J Med
, vol.331
, pp. 637-642
-
-
Fuchs, H.J.1
Borowitz, D.S.2
Chris-tiansen, D.H.3
-
107
-
-
1842328654
-
Aerosol delivery and safety of rhDNase in young children with cystic fibrosis. A bronchoscopic study
-
Rock M, Kirchner K, McCubbin M, et al. Aerosol delivery and safety of rhDNase in young children with cystic fibrosis. A bronchoscopic study. Pediatr Pulmonol 1996;(Suppl)13:284A.
-
(1996)
Pediatr Pulmonol
, vol.13
, Issue.SUPPL.
-
-
Rock, M.1
Kirchner, K.2
McCubbin, M.3
-
108
-
-
0025874599
-
Activation by extra-cellular nucleotides of chloride secretion in the airway epithelial of patients with cystic fibrosis
-
Knowles MR, Clarke LL, Boucher RC. Activation by extra-cellular nucleotides of chloride secretion in the airway epithelial of patients with cystic fibrosis. N Engl J Med 1991;325:533-8.
-
(1991)
N Engl J Med
, vol.325
, pp. 533-538
-
-
Knowles, M.R.1
Clarke, L.L.2
Boucher, R.C.3
-
109
-
-
0025236867
-
A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis
-
Knowles MR, Church NL, Waltner WE, et al. A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis. N Engl J Med 1990;332:1189-94.
-
(1990)
N Engl J Med
, vol.332
, pp. 1189-1194
-
-
Knowles, M.R.1
Church, N.L.2
Waltner, W.E.3
-
110
-
-
0027486593
-
No added benefit from nebulized amiloride in patients with cystic fibrosis
-
Graham AA, Hasani A, Alton EW, et al. No added benefit from nebulized amiloride in patients with cystic fibrosis. Eur Respir J 1993;6:1243-8.
-
(1993)
Eur Respir J
, vol.6
, pp. 1243-1248
-
-
Graham, A.A.1
Hasani, A.2
Alton, E.W.3
-
111
-
-
1842416044
-
Safety of delivery of adeno-associated virus mediated gene transfer of CFTR in the maxillary sinus of CF patients with antrostomies
-
Wagner JA, Moran ML, Messner AH, et al. Safety of delivery of adeno-associated virus mediated gene transfer of CFTR in the maxillary sinus of CF patients with antrostomies. Pediatr Pulmonol 1996(Suppl)13:276A.
-
(1996)
Pediatr Pulmonol
, vol.13
, Issue.SUPPL.
-
-
Wagner, J.A.1
Moran, M.L.2
Messner, A.H.3
-
112
-
-
85030306241
-
Chemical chaperones correct the folding defect associated with the ΔF508 CFTR protein and restore cAMP dependent chloride transport
-
Welch WJ, Brown CR, Brown LQ, et al. Chemical chaperones correct the folding defect associated with the ΔF508 CFTR protein and restore cAMP dependent chloride transport. Pediatr Pulmonol 1996;(Suppl)13:90.
-
(1996)
Pediatr Pulmonol
, vol.13
, Issue.SUPPL.
, pp. 90
-
-
Welch, W.J.1
Brown, C.R.2
Brown, L.Q.3
-
113
-
-
85030302881
-
Pharmacological modulation of wild-type and ΔF508 CFTR by genistein and CPX
-
Yang I, Zeltwanger S, Wang F, et al. Pharmacological modulation of wild-type and ΔF508 CFTR by genistein and CPX. Pediatr Pulmonol 1996;(Suppl)13:258A.
-
(1996)
Pediatr Pulmonol
, vol.13
, Issue.SUPPL.
-
-
Yang, I.1
Zeltwanger, S.2
Wang, F.3
-
114
-
-
0026611093
-
A1 adenosine receptor antagonists activate chloride efflux from cystic fibrosis cells
-
Eidelman O, Guay-Broder C, vanGalen PJ, et al. A1 adenosine receptor antagonists activate chloride efflux from cystic fibrosis cells. Proc Natl Acad Sci USA, 1992;89:5562-6.
-
(1992)
Proc Natl Acad Sci USA
, vol.89
, pp. 5562-5566
-
-
Eidelman, O.1
Guay-Broder, C.2
VanGalen, P.J.3
-
115
-
-
0029556721
-
- mediated chloride permeability mediated chloride permeability is regulated by Type III phosphodiesterases in airway epithelial cells
-
- mediated chloride permeability mediated chloride permeability is regulated by Type III phosphodiesterases in airway epithelial cells. Am J Respir Care Mol Biol 1995;13:657-64.
-
(1995)
Am J Respir Care Mol Biol
, vol.13
, pp. 657-664
-
-
Kelley, T.J.1
Al-Nakkash, L.2
Drumm, M.L.3
-
116
-
-
85030301699
-
Effect of genistein on chloride secretions in CF tissues in vivo and in vitro
-
Browning J, Farley R, Smith S, et al. Effect of genistein on chloride secretions in CF tissues in vivo and in vitro. Pediatr Pulmonol 1996;(Suppl)13:281A.
-
(1996)
Pediatr Pulmonol
, vol.13
, Issue.SUPPL.
-
-
Browning, J.1
Farley, R.2
Smith, S.3
-
117
-
-
85030301564
-
Milrinone induces chloride secretion in normal but not CF airways in vivo
-
Middleton PG, Chadwick SL, Pollard KA, et al. Milrinone induces chloride secretion in normal but not CF airways in vivo. Pediatric Pulmonol 1996;(Suppl)13:282A.
-
(1996)
Pediatric Pulmonol
, vol.13
, Issue.SUPPL.
-
-
Middleton, P.G.1
Chadwick, S.L.2
Pollard, K.A.3
-
118
-
-
1842408435
-
Lung transplantation for cystic fibrosis: State of the art
-
Mallory GB Jr. Lung transplantation for cystic fibrosis: state of the art. Pediatr Pulmonol 1996;(Suppl)13:121.
-
(1996)
Pediatr Pulmonol
, vol.13
, Issue.SUPPL.
, pp. 121
-
-
Mallory Jr., G.B.1
-
119
-
-
0028305715
-
Living-related donor lobectomy for bilateral lobar transplantation in patients with cystic fibrosis
-
Cohen RG, Barr ML, Schenkel FA, et al. Living-related donor lobectomy for bilateral lobar transplantation in patients with cystic fibrosis. Ann Thorac Surg 1994;57:1473-8.
-
(1994)
Ann Thorac Surg
, vol.57
, pp. 1473-1478
-
-
Cohen, R.G.1
Barr, M.L.2
Schenkel, F.A.3
|