A review of cochlear implantation in mitochondrial sensorineural hearing loss

Otology and Neurotology

Volumn 24, Issue 3, 2003, Pages 418-426

  Sinnathuray, A R ^a,b   Raut, V ^a   Awa, A ^a   Magee, A ^b   Toner, J G ^a  

^a BELFAST CITY HOSPITAL   (United Kingdom)

^b QUEEN'S UNIVERSITY BELFAST   (United Kingdom)

Author keywords

Aminoglycoside; Antibiotics; Cochlear implantation; DNA; Kearns Sayre syndrome; MELAS syndrome; MIDD syndrome; Mitochondrial; Sensorineural deafness

Indexed keywords

AUDIOGRAPHY; CHRONIC PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA; COCHLEA PROSTHESIS; COMPUTER ASSISTED TOMOGRAPHY; DIABETES MELLITUS; DIFFERENTIAL DIAGNOSIS; DISEASE ASSOCIATION; GENE; GENE MTTL1; GENETIC ANALYSIS; HIGH RISK POPULATION; HUMAN; KEARNS SAYRE SYNDROME; MELAS SYNDROME; MIDD SYNDROME; MITOCHONDRIAL SENSORINEURAL HEARING LOSS; OPHTHALMOPLEGIA; PATHOPHYSIOLOGY; PERCEPTION DEAFNESS; POINT MUTATION; PREVALENCE; PRIORITY JOURNAL; REVIEW; SYNDROME;

ADULT; AGED; AUDIOMETRY, PURE-TONE; BRAIN; COCHLEAR IMPLANTATION; DNA, MITOCHONDRIAL; FEMALE; GENE EXPRESSION; HEARING LOSS, SENSORINEURAL; HUMANS; KEARNS-SAYER SYNDROME; MALE; MELAS SYNDROME; MIDDLE AGED; PEDIGREE; POINT MUTATION; POLYMERASE CHAIN REACTION; RNA; RNA, TRANSFER; SEVERITY OF ILLNESS INDEX; TOMOGRAPHY, X-RAY COMPUTED; VESTIBULAR DISEASES;

EID: 0038813819     PISSN: 15317129     EISSN: None     Source Type: Journal    
DOI: 10.1097/00129492-200305000-00012     Document Type: Review

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