Dysferlin expression in tubular aggregates: Their possible relationship to endoplasmic reticulum stress

Acta Neuropathologica

Volumn 105, Issue 6, 2003, Pages 603-609

  Ikezoe, Koji ^a   Furuya, Hirokazu ^a   Ohyagi, Yasumasa ^a   Osoegawa, Manabu ^a   Nishino, Ichizo ^b   Nonaka, Ikuya ^c   Kira, Jun Ichi ^a  

^a KYUSHU UNIVERSITY   (Japan)

^b NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

^c NATIONAL INSTITUTE OF MENTAL HEALTH   (Japan)

Author keywords

Dysferlin; Endoplasmic reticulum stress; Periodic paralysis; Sarcoplasmic reticulum; Tubular aggregates

Indexed keywords

CALCIUM ION; DYSFERLIN; GLUCOSE REGULATED PROTEIN; ADENOSINE TRIPHOSPHATASE (CALCIUM); CYTOSKELETON PROTEIN; DAG1 PROTEIN, HUMAN; DYSF PROTEIN, HUMAN; DYSTROGLYCAN; DYSTROPHIN; GLUCOSE REGULATED PROTEINS; GLUCOSE-REGULATED PROTEINS; GRP8 PROTEIN, HUMAN; HEAT SHOCK PROTEIN 70; LAMININ; MEMBRANE PROTEIN; MUSCLE PROTEIN; NEUROPEPTIDE RECEPTOR; SARCOPLASMIC RETICULUM CALCIUM TRANSPORTING ADENOSINE TRIPHOSPHATASE;

ADOLESCENT; ADULT; AMINO ACID SEQUENCE; ARTICLE; CALCIUM CELL LEVEL; CALCIUM HOMEOSTASIS; CELL ORGANELLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; FEMALE; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; MALE; MUSCLE BIOPSY; MUSCLE CRAMP; MYALGIA; PATHOLOGY; PERIODIC PARALYSIS; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; SARCOLEMMA; SARCOPLASMIC RETICULUM; STRESS; TRANSVERSE TUBULAR SYSTEM; UPREGULATION; COMPARATIVE STUDY; IMMUNOLOGY; METABOLISM; MUSCLE CELL; MYOPATHY; PRESCHOOL CHILD;

ADOLESCENT; ADULT; CALCIUM-TRANSPORTING ATPASES; CHILD; CHILD, PRESCHOOL; CYTOSKELETAL PROTEINS; DYSTROGLYCANS; DYSTROPHIN; ENDOPLASMIC RETICULUM; FEMALE; HSP70 HEAT-SHOCK PROTEINS; HUMANS; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; LAMININ; MALE; MEMBRANE GLYCOPROTEINS; MEMBRANE PROTEINS; MUSCLE FIBERS; MUSCLE PROTEINS; MYOPATHIES, STRUCTURAL, CONGENITAL; RECEPTORS, NEUROPEPTIDE; SARCOLEMMA; SARCOPLASMIC RETICULUM CALCIUM-TRANSPORTING ATPASES;

EID: 0038481506     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-003-0686-1     Document Type: Article

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