Embryonal hyperplasia of Bowman's capsular epithelium in patients with WT1 mutations

Pediatric Nephrology

Volumn 18, Issue 1, 2003, Pages 9-13

  Fukuzawa, Ryuji ^a,b   Eccles, Michael R ^b   Ikeda, Masahiro ^c   Hata, Jun Ichi ^d  

^a KEIO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b UNIVERSITY OF OTAGO   (New Zealand)

^c TOKYO METROPOLITAN CHILDREN'S MEDICAL CENTER   (Japan)

^d NATIONAL RESEARCH INSTITUTE FOR CHILD HEALTH AND DEVELOPMENT   (Japan)

Author keywords

Continuous ambulatory peritoneal dialysis; Denys Drash syndrome; Diffuse mesangial sclerosis; End stage renal disease; PAX2; Wilms tumor; WT1

Indexed keywords

CYTOKERATIN; EPITHELIAL MEMBRANE ANTIGEN; TRANSCRIPTION FACTOR; TRANSCRIPTION FACTOR PAX2; UNCLASSIFIED DRUG; VIMENTIN; WT1 PROTEIN;

ARTICLE; AUTOPSY; CASE REPORT; CELL DIFFERENTIATION; CHILD; CONTINUOUS AMBULATORY PERITONEAL DIALYSIS; DENYS DRASH SYNDROME; DISEASE ASSOCIATION; DISEASE COURSE; EXON; FEMALE; GLOMERULOSCLEROSIS; HUMAN; HUMAN TISSUE; HYPERPLASIA; IMMUNOHISTOCHEMISTRY; KIDNEY EPITHELIUM; KIDNEY FAILURE; KIDNEY SURGERY; MALE; MESANGIUM CELL; MISSENSE MUTATION; NEPHROBLASTOMA; PODOCYTE; PRIORITY JOURNAL; PROTEIN EXPRESSION; STEM CELL; UROGENITAL TRACT DISEASE;

CELL DIFFERENTIATION; CHILD; CHILD, PRESCHOOL; DENYS-DRASH SYNDROME; DNA-BINDING PROTEINS; EPITHELIUM; FEMALE; HUMANS; HYPERPLASIA; IMMUNOHISTOCHEMISTRY; INFANT; KIDNEY; KIDNEY FAILURE, CHRONIC; MALE; MUTATION; PAX2 TRANSCRIPTION FACTOR; PERITONEAL DIALYSIS; TRANSCRIPTION FACTORS; WT1 PROTEINS;

EID: 0037743763     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-002-1019-7     Document Type: Article

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