Mice with targeted disruption of the fatty acid transport protein 4 (Fatp 4, Slc27a4) gene show features of lethal restrictive dermopathy

Journal of Cell Biology

Volumn 161, Issue 6, 2003, Pages 1105-1115

  Herrmann, Thomas ^a   Van der Hoeven, Frank ^b   Gröne, Hermann Josef ^b   Stewart, Adrian Francis ^c   Langbein, Lutz ^b   Kaiser, Iris ^a   Liebisch, Gerhard ^d   Gosch, Isabella ^a   Buchkremer, Florian ^a   Drobnik, Wolfgang ^d   Schmitz, Gerd ^d   Stremmel, Wolfgang ^a  

^a UNIVERSITY OF HEIDELBERG   (Germany)

^b GERMAN CANCER RESEARCH CENTER DKFZ   (Germany)

^c DRESDEN UNIVERSITY OF TECHNOLOGY   (Germany)

^d UNIVERSITY OF REGENSBURG   (Germany)

Author keywords

Ceramides; Epidermis; Fatp4; Fatty acid metabolism; Fatty acid transport

Indexed keywords

CARRIER PROTEIN; PROTEIN FATP 4; PROTEIN SLC17A4; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; BODY BUILD; BREATHING; CELL METABOLISM; CELL PROLIFERATION; CELL TRANSPORT; CONTROLLED STUDY; DERMOEPIDERMAL JUNCTION; EPIDERMIS; FACE DYSMORPHIA; FATTY ACID TRANSPORT; GENE DISRUPTION; GENE FUNCTION; HYPERKERATOSIS; JOINT CONTRACTURE; LETHAL RESTRICTIVE DERMOPATHY; LIPID ANALYSIS; LIPID COMPOSITION; MOUSE; NEWBORN; NONHUMAN; PRIORITY JOURNAL; PROTEIN FAMILY; SEBACEOUS GLAND; SKIN DISEASE; SUCKLING;

ANIMALS; BODY WEIGHT; CARRIER PROTEINS; CERAMIDES; DISEASE MODELS, ANIMAL; EPIDERMIS; FATTY ACID TRANSPORT PROTEINS; FATTY ACIDS; FEMALE; GENE TARGETING; GENES, LETHAL; HEAD; JOINTS; LIPID METABOLISM; LUNG; MALE; MEMBRANE PROTEINS; MEMBRANE TRANSPORT PROTEINS; MICE; MICE, KNOCKOUT; MICROSCOPY, ELECTRON; MUTATION; PHENOTYPE; SKIN ABNORMALITIES; SKIN DISEASES, GENETIC;

ANIMALIA; HEDYOTIS MANNII;

EID: 0037477788     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.200207080     Document Type: Article

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