-
1
-
-
0015423263
-
The activities of pyruvate carboxylase, phosphoenolpyruvate carboxylase and fructose diphosphatase in muscles from vertebrates and invertebrates
-
Crabtree, B., Higgins, S. J. and Newsholme, E. A. (1972) The activities of pyruvate carboxylase, phosphoenolpyruvate carboxylase and fructose diphosphatase in muscles from vertebrates and invertebrates. Biochem. J. 130, 391-396
-
(1972)
Biochem. J.
, vol.130
, pp. 391-396
-
-
Crabtree, B.1
Higgins, S.J.2
Newsholme, E.A.3
-
2
-
-
0018800259
-
Carboxylation and decarboxylation reactions: Anaplerotic flux and removal of citrate cycle intermediates in skeletal muscle
-
Lee, S. H. and Davis, E. J. (1979) Carboxylation and decarboxylation reactions: anaplerotic flux and removal of citrate cycle intermediates in skeletal muscle. J. Biol. Chem. 254, 420-430
-
(1979)
J. Biol. Chem.
, vol.254
, pp. 420-430
-
-
Lee, S.H.1
Davis, E.J.2
-
4
-
-
0034036980
-
Anaplerosis of the citric acid cycle: Role in energy metabolism of heart and skeletal muscle
-
Gibala, M. J., Young, M. E. and Taegtmeyer, H. (2000) Anaplerosis of the citric acid cycle: role in energy metabolism of heart and skeletal muscle. Acta Physiol. Scand. 168, 657-665
-
(2000)
Acta Physiol. Scand.
, vol.168
, pp. 657-665
-
-
Gibala, M.J.1
Young, M.E.2
Taegtmeyer, H.3
-
5
-
-
0024576611
-
Pyruvate carboxylation in the rat heart. Role of biotin-dependent enzymes
-
Sundqvist, K. E., Hiltunen, J. K. and Hassinen, I. E. (1989) Pyruvate carboxylation in the rat heart. Role of biotin-dependent enzymes. Biochem. J. 257, 913-916
-
(1989)
Biochem. J.
, vol.257
, pp. 913-916
-
-
Sundqvist, K.E.1
Hiltunen, J.K.2
Hassinen, I.E.3
-
6
-
-
0028121599
-
Substrate cycling between pyruvate and oxaloacetate in awake normal and 3,3′-5-triiodo-L-thyronine-treated rats
-
Petersen, K. F., Cline, G. W., Blair, J. B. and Shulman, G. I. (1994) Substrate cycling between pyruvate and oxaloacetate in awake normal and 3,3′-5-triiodo-L-thyronine-treated rats. Am. J. Physiol 267, E273-E277
-
(1994)
Am. J. Physiol.
, vol.267
-
-
Petersen, K.F.1
Cline, G.W.2
Blair, J.B.3
Shulman, G.I.4
-
8
-
-
0029556146
-
Triiodothyronine treatment increases substrate cycling between pyruvate carboxylase and malic enzyme in perfused rat liver
-
Petersen, K. F., Blair, J. B. and Shulman, G. I. (1995) Triiodothyronine treatment increases substrate cycling between pyruvate carboxylase and malic enzyme in perfused rat liver. Metabolism 44, 1380-1383
-
(1995)
Metabolism
, vol.44
, pp. 1380-1383
-
-
Petersen, K.F.1
Blair, J.B.2
Shulman, G.I.3
-
9
-
-
0021988603
-
Pyruvate carboxylase: An astrocyte-specific enzyme implicated in the replenishment of amino acid neurotransmitter pools
-
Shank, R. P., Bennett, G. S., Freytag, S. O. and Campbell, G. L. (1985) Pyruvate carboxylase: an astrocyte-specific enzyme implicated in the replenishment of amino acid neurotransmitter pools. Brain Res. 329, 364-367
-
(1985)
Brain Res.
, vol.329
, pp. 364-367
-
-
Shank, R.P.1
Bennett, G.S.2
Freytag, S.O.3
Campbell, G.L.4
-
10
-
-
0033566731
-
Astrocytes: Glutamate producers for neurons
-
Hertz, L., Dringen, R., Schousboe, A. and Robinson, S. R. (1999) Astrocytes: glutamate producers for neurons. J. Neurosci. Res. 57, 417-428
-
(1999)
J. Neurosci. Res.
, vol.57
, pp. 417-428
-
-
Hertz, L.1
Dringen, R.2
Schousboe, A.3
Robinson, S.R.4
-
11
-
-
78651118312
-
Pyruvate carboxylase I: Nature of the reaction
-
Utter, M. F. and Keech, D. B. (1963) Pyruvate carboxylase I: nature of the reaction. J. Biol. Chem. 283, 2603-2608
-
(1963)
J. Biol. Chem.
, vol.283
, pp. 2603-2608
-
-
Utter, M.F.1
Keech, D.B.2
-
13
-
-
0029971641
-
Effects of acetyl CoA on the pre-steady-state kinetics of the biotin carboxylation reaction of pyruvate carboxylase
-
Legge, G. B., Branson, J. P. and Attwood, P. V. (1996) Effects of acetyl CoA on the pre-steady-state kinetics of the biotin carboxylation reaction of pyruvate carboxylase. Biochemistry 35, 3849-3856
-
(1996)
Biochemistry
, vol.35
, pp. 3849-3856
-
-
Legge, G.B.1
Branson, J.P.2
Attwood, P.V.3
-
14
-
-
0025778755
-
Pyruvate carboxylase deficiency: A benign variant with normal development
-
Van Coster, R. N., Fernhoff, P. M. and De Vivo, D. C. (1991) Pyruvate carboxylase deficiency: a benign variant with normal development. Pediatr. Res. 30, 1-4
-
(1991)
Pediatr. Res.
, vol.30
, pp. 1-4
-
-
Van Coster, R.N.1
Fernhoff, P.M.2
De Vivo, D.C.3
-
15
-
-
0030758201
-
A case of benign pyruvate carboxylase deficiency with normal development
-
Hamilton, J., Rae, M. D., Logan, R. W. and Robinson, P. H. (1997) A case of benign pyruvate carboxylase deficiency with normal development. J. Inher. Metab. Dis. 20, 401-403
-
(1997)
J. Inher. Metab. Dis.
, vol.20
, pp. 401-403
-
-
Hamilton, J.1
Rae, M.D.2
Logan, R.W.3
Robinson, P.H.4
-
16
-
-
0034827627
-
Pyruvate carboxylase deficiency. Report of a case and additional evidence for the 'mild' Phenotype
-
Arnold, G. L., Griebel, M. L., Porterfield, M. and Brewster, M. (2001) Pyruvate carboxylase deficiency. Report of a case and additional evidence for the 'mild' Phenotype. Clin. Ped. 40, 519-521
-
(2001)
Clin. Ped.
, vol.40
, pp. 519-521
-
-
Arnold, G.L.1
Griebel, M.L.2
Porterfield, M.3
Brewster, M.4
-
17
-
-
0020646513
-
3H]biotin-labeled proteins in cultured human skin fibroblasts from patients with pyruvate carboxylase deficiency
-
3H]biotin-labeled proteins in cultured human skin fibroblasts from patients with pyruvate carboxylase deficiency. J. Biol. Chem. 258, 6660-6664
-
(1983)
J. Biol. Chem.
, vol.258
, pp. 6660-6664
-
-
Robinson, B.H.1
Oei, J.2
Saunders, M.3
Gravel, R.4
-
18
-
-
0021346589
-
The molecular basis for the two different clinical presentations of classical pyruvate carboxylase deficiency
-
Robinson, B. H., Oei, J., Sherwood, W. G., Applegarth, D., Wong, L., Haworth, J., Goodyer, P., Casey, R. and Zaleski, L. A. (1984) The molecular basis for the two different clinical presentations of classical pyruvate carboxylase deficiency. Am. J. Hum. Genet. 36, 283-294
-
(1984)
Am. J. Hum. Genet.
, vol.36
, pp. 283-294
-
-
Robinson, B.H.1
Oei, J.2
Sherwood, W.G.3
Applegarth, D.4
Wong, L.5
Haworth, J.6
Goodyer, P.7
Casey, R.8
Zaleski, L.A.9
-
19
-
-
0023146521
-
35S-streptavidin labeling, and Northern blotting with a cloned cDNA probe
-
35S-streptavidin labeling, and Northern blotting with a cloned cDNA probe. Am. J. Hum. Genet. 40, 50-59
-
(1987)
Am. J. Hum. Genet.
, vol.40
, pp. 50-59
-
-
Robinson, B.H.1
Oei, J.2
Saudubray, J.M.3
Marsac, C.4
Bartlett, K.5
Quan, F.6
Gravel, R.7
-
20
-
-
0029766887
-
Disorders of pyruvate carboxylase and the pyruvate dehydrogenase complex
-
Robinson, B. H., MacKay, N., Chun, K. and Ling, M. (1996) Disorders of pyruvate carboxylase and the pyruvate dehydrogenase complex. J. Inher. Metab. Dis. 19, 452-462
-
(1996)
J. Inher. Metab. Dis.
, vol.19
, pp. 452-462
-
-
Robinson, B.H.1
MacKay, N.2
Chun, K.3
Ling, M.4
-
21
-
-
17344363493
-
Amerindian pyruvate carboxylase deficiency is associated with two distinct missense mutations
-
Carbone, M. A., MacKay, N., Ling, M., Cole, D. E., Douglas, C., Rigat, B., Feigenbaum, A., Clarke, J. T., Haworth, J. C, Greenberg, C. R. et al. (1998) Amerindian pyruvate carboxylase deficiency is associated with two distinct missense mutations. Am. J. Hum. Genet. 62, 1312-1319
-
(1998)
Am. J. Hum. Genet.
, vol.62
, pp. 1312-1319
-
-
Carbone, M.A.1
MacKay, N.2
Ling, M.3
Cole, D.E.4
Douglas, C.5
Rigat, B.6
Feigenbaum, A.7
Clarke, J.T.8
Haworth, J.C.9
Greenberg, C.R.10
-
22
-
-
0031956954
-
Molecular characterization of pyruvate carboxylase deficiency in two consanguineous families
-
Wexler, I. D., Kerr, D. S., Du, Y., Kaung, M. M., Stephenson, W., Lusk, M. M., Wappner, R. S. and Higgins, J. J. (1998) Molecular characterization of pyruvate carboxylase deficiency in two consanguineous families. Pediatr Res. 43, 579-584
-
(1998)
Pediatr. Res.
, vol.43
, pp. 579-584
-
-
Wexler, I.D.1
Kerr, D.S.2
Du, Y.3
Kaung, M.M.4
Stephenson, W.5
Lusk, M.M.6
Wappner, R.S.7
Higgins, J.J.8
-
23
-
-
0036307823
-
Intron retention and frameshift mutations result in severe pyruvate carboxylase deficiency in two male siblings
-
Carbone, M. A., Applegarth, D. A. and Robinson, B. H. (2002) Intron retention and frameshift mutations result in severe pyruvate carboxylase deficiency in two male siblings. Hum. Mut. 20, 48-56
-
(2002)
Hum. Mut.
, vol.20
, pp. 48-56
-
-
Carbone, M.A.1
Applegarth, D.A.2
Robinson, B.H.3
-
24
-
-
0033590217
-
Functional expression, purification, and characterization of recombinant human pyruvate carboxylase
-
Jitrapakdee, S., Walker, M. E. and Wallace, J. C. (1999) Functional expression, purification, and characterization of recombinant human pyruvate carboxylase. Biochem. Biophys. Res. Commun. 266, 512-517
-
(1999)
Biochem. Biophys. Res. Commun.
, vol.266
, pp. 512-517
-
-
Jitrapakdee, S.1
Walker, M.E.2
Wallace, J.C.3
-
25
-
-
0027532691
-
Properties of skeletal muscle mitochondria isolated from subsarcolemmal and intermyofibrillar regions
-
Cogswell, A. M., Stevens, R. J. and Hood, D. A. (1993) Properties of skeletal muscle mitochondria isolated from subsarcolemmal and intermyofibrillar regions. Am. J. Physiol. 264, C383-C389
-
(1993)
Am. J. Physiol.
, vol.264
-
-
Cogswell, A.M.1
Stevens, R.J.2
Hood, D.A.3
-
26
-
-
0030447468
-
Diagnosis of complex 1 deficiency in patients with lactic acidemia using skin fbroblast cultures
-
Pitkanen, S., Raha, S. and Robinson, B. H. (1996) Diagnosis of complex 1 deficiency in patients with lactic acidemia using skin fbroblast cultures. Biochem. Mol. Med. 59, 134-137
-
(1996)
Biochem. Mol. Med.
, vol.59
, pp. 134-137
-
-
Pitkanen, S.1
Raha, S.2
Robinson, B.H.3
-
27
-
-
71849104860
-
Protein Measurement with the Folin-Phenol reagents
-
Lowry, O. H., Rosebrough, N. J., Farr, A. L. and Randall, R. J. (1951) Protein Measurement with the Folin-Phenol reagents. J. Biol. Chem. 193, 265-275
-
(1951)
J. Biol. Chem.
, vol.193
, pp. 265-275
-
-
Lowry, O.H.1
Rosebrough, N.J.2
Farr, A.L.3
Randall, R.J.4
-
28
-
-
0021987577
-
Prenatal diagnosis of pyruvate carboxylase deficiency
-
Robinson, B. H., Toone, J. R., Benedict, R. P., Dimmick, J. E., Oei, J. and Applegarth, D. A. (1985) Prenatal diagnosis of pyruvate carboxylase deficiency. Prenat. Diagn. 5, 67-71
-
(1985)
Prenat. Diagn.
, vol.5
, pp. 67-71
-
-
Robinson, B.H.1
Toone, J.R.2
Benedict, R.P.3
Dimmick, J.E.4
Oei, J.5
Applegarth, D.A.6
-
29
-
-
0034514655
-
Ubiquitination and deubiquitination: Targeting of proteins for degradation by the proteasome
-
Wirkinson, K. D. (2000) Ubiquitination and deubiquitination: targeting of proteins for degradation by the proteasome. Cell Dev. Bol. 11, 141-148
-
(2000)
Cell Dev. Bol.
, vol.11
, pp. 141-148
-
-
Wirkinson, K.D.1
-
30
-
-
0034874791
-
AAA proteases of mitochondria: Quality control of membrane proteins and regulatory functions during mitochondrial biogenesis
-
Langer, T., Kaser, M., Klanner, C. and Leohard, K. (2001) AAA proteases of mitochondria: quality control of membrane proteins and regulatory functions during mitochondrial biogenesis. Biochem. Soc. Trans. 29, 431-436
-
(2001)
Biochem. Soc. Trans.
, vol.29
, pp. 431-436
-
-
Langer, T.1
Kaser, M.2
Klanner, C.3
Leohard, K.4
-
31
-
-
0036578543
-
Changes in catalytic activity and association state of pyruvate carboxylase which are dependent on enzyme concentration
-
Attwood, P. V. and Geeves, M. A. (2002) Changes in catalytic activity and association state of pyruvate carboxylase which are dependent on enzyme concentration. Arch. Biochem. Biophys. 401, 63-72
-
(2002)
Arch. Biochem. Biophys.
, vol.401
, pp. 63-72
-
-
Attwood, P.V.1
Geeves, M.A.2
-
32
-
-
0025976691
-
Studies on dilution inactivation of sleep liver pyruvate carboxylase
-
Khew-Goodall, Y. S., Johannssen, W., Attwood, P. V., Wallace, J. C. and Keech, D. B. (1991) Studies on dilution inactivation of sleep liver pyruvate carboxylase. Arch. Biochem. Biophys. 284, 98-105
-
(1991)
Arch. Biochem. Biophys.
, vol.284
, pp. 98-105
-
-
Khew-Goodall, Y.S.1
Johannssen, W.2
Attwood, P.V.3
Wallace, J.C.4
Keech, D.B.5
-
33
-
-
0027405927
-
The existence of multiple tetrameric conformers of chicken liver pyruvate carboxylase and their roles in dilution inactivation
-
Attwood, P. V., Johannssen, W., Chapman-Smith, A. and Wallace, J. C. (1993) The existence of multiple tetrameric conformers of chicken liver pyruvate carboxylase and their roles in dilution inactivation. Biochem J. 290, 583-590
-
(1993)
Biochem. J.
, vol.290
, pp. 583-590
-
-
Attwood, P.V.1
Johannssen, W.2
Chapman-Smith, A.3
Wallace, J.C.4
-
34
-
-
78651126425
-
Pyruvate carboxylase II: Properties
-
Keech, D. B. and Utter, M. F. (1963) Pyruvate carboxylase II: properties. J. Biol. Chem. 238, 2609-2613
-
(1963)
J. Biol. Chem.
, vol.238
, pp. 2609-2613
-
-
Keech, D.B.1
Utter, M.F.2
-
35
-
-
0029889988
-
PHD: Predicting 1D protein structure by profile based neural networks
-
Rost, B. (1996) PHD: predicting 1D protein structure by profile based neural networks. Methods Enzymol. 266, 525-539
-
(1996)
Methods Enzymol.
, vol.266
, pp. 525-539
-
-
Rost, B.1
|