-
1
-
-
0025868103
-
Demonstration that CFTR is a chloride channel by alteration of its anion selectivity
-
Anderson MP, Gregory RJ, Thompson S, Souza DW, Paul S, Mulligan RC, Smith AE & Welsh MJ (1991). Demonstration that CFTR is a chloride channel by alteration of its anion selectivity. Science 253, 202-205.
-
(1991)
Science
, vol.253
, pp. 202-205
-
-
Anderson, M.P.1
Gregory, R.J.2
Thompson, S.3
Souza, D.W.4
Paul, S.5
Mulligan, R.C.6
Smith, A.E.7
Welsh, M.J.8
-
2
-
-
0022559226
-
Intracellular pH regulation in epithelial cells
-
Boron WF (1986). Intracellular pH regulation in epithelial cells. Annu Rev Physiol 48, 377-388.
-
(1986)
Annu. Rev. Physiol.
, vol.48
, pp. 377-388
-
-
Boron, W.F.1
-
3
-
-
0026670029
-
Chloride secretory response to extracellular ATP in normal and cystic fibrosis nasal epithelia
-
Clarke LL & Boucher RC (1992). Chloride secretory response to extracellular ATP in normal and cystic fibrosis nasal epithelia. Am J Physiol 263, C348-356.
-
(1992)
Am. J. Physiol.
, vol.263
-
-
Clarke, L.L.1
Boucher, R.C.2
-
6
-
-
0032908449
-
Bicarbonate and chloride secretion in Calu-3 human airway epithelial cells
-
Devor DC, Singh AK, Lambert LC, Deluca A, Frizzell RA & Bridges RJ (1999). Bicarbonate and chloride secretion in Calu-3 human airway epithelial cells. J Gen Physiol 113, 743-760.
-
(1999)
J. Gen. Physiol.
, vol.113
, pp. 743-760
-
-
Devor, D.C.1
Singh, A.K.2
Lambert, L.C.3
Deluca, A.4
Frizzell, R.A.5
Bridges, R.J.6
-
7
-
-
0034326719
-
Basal nucleotide levels, release, and metabolism in normal and cystic fibrosis airways
-
Donaldson SH, Lazarowski ER, Picher M, Knowles MR, Stutts MJ & Boucher RC (2000). Basal nucleotide levels, release, and metabolism in normal and cystic fibrosis airways. Mol Med 6, 969-982.
-
(2000)
Mol. Med.
, vol.6
, pp. 969-982
-
-
Donaldson, S.H.1
Lazarowski, E.R.2
Picher, M.3
Knowles, M.R.4
Stutts, M.J.5
Boucher, R.C.6
-
8
-
-
0032991755
-
- exchanger isoforms in proximal and distal human airways
-
- exchanger isoforms in proximal and distal human airways. Am J Physiol 276, L971-978.
-
(1999)
Am. J. Physiol.
, vol.276
-
-
Dudeja, P.K.1
Hafez, N.2
Tyagi, S.3
Gailey, C.A.4
Toofanfard, M.5
Alrefai, W.A.6
Nazir, T.M.7
Ramaswamy, K.8
Al-Bazzaz, F.J.9
-
9
-
-
0024824522
-
The pathophysiology of the pancreatic defect in cystic fibrosis
-
Durie PR (1989). The pathophysiology of the pancreatic defect in cystic fibrosis. Acta Paediatr Scand Suppl 363, 41-44.
-
(1989)
Acta Paediatr. Scand. Suppl.
, vol.363
, pp. 41-44
-
-
Durie, P.R.1
-
11
-
-
0030882184
-
Intestinal physiology and pathology in gene-targeted mouse models of cystic fibrosis
-
Grubb BR & Gabriel SE (1997). Intestinal physiology and pathology in gene-targeted mouse models of cystic fibrosis. Am J Physiol 273, G258-266.
-
(1997)
Am. J. Physiol.
, vol.273
-
-
Grubb, B.R.1
Gabriel, S.E.2
-
13
-
-
0035923676
-
Compartmentalized autocrine signaling to cystic fibrosis transmembrane conductance regulator at the apical membrane of airway epithelial cells
-
Huang P, Lazarowski ER, Tarran R, Milgram SL, Boucher RC & Stutts MJ (2001). Compartmentalized autocrine signaling to cystic fibrosis transmembrane conductance regulator at the apical membrane of airway epithelial cells. Proc Natl Acad Sci U S A 98, 14120-14125.
-
(2001)
Proc. Natl. Acad. Sci. U S A
, vol.98
, pp. 14120-14125
-
-
Huang, P.1
Lazarowski, E.R.2
Tarran, R.3
Milgram, S.L.4
Boucher, R.C.5
Stutts, M.J.6
-
15
-
-
0016162176
-
Diminished excretion of bicarbonate from the single sweat gland of patients with cystic fibrosis of the pancreas
-
Kaiser D & Drack E (1974). Diminished excretion of bicarbonate from the single sweat gland of patients with cystic fibrosis of the pancreas. Eur J Clin Invest 4, 261-265.
-
(1974)
Eur. J. Clin. Invest.
, vol.4
, pp. 261-265
-
-
Kaiser, D.1
Drack, E.2
-
16
-
-
0014411090
-
Reproductive failure in males with cystic fibrosis
-
Kaplan E, Shwachman H, Perlmutter AD, Rule A, Khaw KT & Holsclaw DS (1968). Reproductive failure in males with cystic fibrosis. N Engl J Med 279, 65-69.
-
(1968)
N. Engl. J. Med.
, vol.279
, pp. 65-69
-
-
Kaplan, E.1
Shwachman, H.2
Perlmutter, A.D.3
Rule, A.4
Khaw, K.T.5
Holsclaw, D.S.6
-
17
-
-
0028991826
-
In vivo nasal potential difference: Techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis
-
Knowles MR, Paradiso AM & Boucher RC (1995). In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis. Hum Gene Ther 6, 447-457.
-
(1995)
Hum. Gene Ther.
, vol.6
, pp. 447-457
-
-
Knowles, M.R.1
Paradiso, A.M.2
Boucher, R.C.3
-
19
-
-
0033524506
-
- exchange by cystic fibrosis transmembrane conductance regulator expressed in NIH 3T3 and HEK 293 cells
-
- exchange by cystic fibrosis transmembrane conductance regulator expressed in NIH 3T3 and HEK 293 cells. J Biol Chem 274, 3414-3421.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 3414-3421
-
-
Lee, M.G.1
Wigley, W.C.2
Zeng, W.3
Noel, L.E.4
Marino, C.R.5
Thomas, P.J.6
Muallem, S.7
-
20
-
-
0030885564
-
Permeability of wild-type and mutant cystic fibrosis transmembrane conductance regulator chloride channels to polyatomic anions
-
Linsdell P, Tabcharani JA, Rommens JM, Hou YX, Chang XB, Tsui LC, Riordan JR & Hanrahan JW (1999). Permeability of wild-type and mutant cystic fibrosis transmembrane conductance regulator chloride channels to polyatomic anions. J Gen Physiol 110, 355-364.
-
(1999)
J. Gen. Physiol.
, vol.110
, pp. 355-364
-
-
Linsdell, P.1
Tabcharani, J.A.2
Rommens, J.M.3
Hou, Y.X.4
Chang, X.B.5
Tsui, L.C.6
Riordan, J.R.7
Hanrahan, J.W.8
-
22
-
-
0032435523
-
Role of CFTR and anion exchanger in bicarbonate fluxes in C127 cell lines
-
Mastrocola T, Porcelli AM & Rugolo M (1998). Role of CFTR and anion exchanger in bicarbonate fluxes in C127 cell lines. FEBS Lett 440, 268-272.
-
(1998)
FEBS Lett.
, vol.440
, pp. 268-272
-
-
Mastrocola, T.1
Porcelli, A.M.2
Rugolo, M.3
-
23
-
-
0023818517
-
- exchange modulates intracellular pH in rat type II alveolar epithelial cells
-
- exchange modulates intracellular pH in rat type II alveolar epithelial cells. J Biol Chem 263, 5599-5606.
-
(1988)
J. Biol. Chem.
, vol.263
, pp. 5599-5606
-
-
Nord, E.P.1
Brown, S.E.S.2
Crandall, E.D.3
-
24
-
-
0026773480
-
+ exchange in human normal and cystic fibrosis ciliated airway epithelium
-
+ exchange in human normal and cystic fibrosis ciliated airway epithelium. Am J Physiol 262, L757-764.
-
(1992)
Am. J. Physiol.
, vol.262
-
-
Paradiso, A.M.1
-
25
-
-
0031182749
-
+ exchange in human normal and cystic fibrosis airway epithelium
-
+ exchange in human normal and cystic fibrosis airway epithelium. Am J Physiol 273, L148-158.
-
(1997)
Am. J. Physiol.
, vol.273
-
-
Paradiso, A.M.1
-
26
-
-
0012783434
-
+-ATPase in proximal human airway
-
+-ATPase in proximal human airway. Pediatr Pulmonol Suppl 20, 206.
-
(2000)
Pediatr. Pulmonol. Suppl.
, vol.20
, pp. 206
-
-
Paradiso, A.M.1
Coakley, R.D.2
Winders, A.3
Ribeiro, C.M.4
Kreda, S.M.5
Rochelle, L.G.6
Burch, L.H.7
Boucher, R.C.8
-
27
-
-
0035165915
-
Polarized signaling via purinoceptors in normal and cystic fibrosis airway epithelia
-
Paradiso AM, Ribeiro CMP & Boucher RC (2001). Polarized signaling via purinoceptors in normal and cystic fibrosis airway epithelia. J Gen Physiol 117, 53-68.
-
(2001)
J. Gen. Physiol.
, vol.117
, pp. 53-68
-
-
Paradiso, A.M.1
Ribeiro, C.M.P.2
Boucher, R.C.3
-
28
-
-
0028232830
-
Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator
-
Poulsen JH, Fischer H, Illek B & Machen TE (1994). Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator. Proc Natl Acad Sci U S A 91, 5340-5344.
-
(1994)
Proc. Natl. Acad. Sci. U S A
, vol.91
, pp. 5340-5344
-
-
Poulsen, J.H.1
Fischer, H.2
Illek, B.3
Machen, T.E.4
-
29
-
-
0020700816
-
Chloride impermeability in cystic fibrosis
-
Quinton PM (1983). Chloride impermeability in cystic fibrosis. Nature 301, 421-422.
-
(1983)
Nature
, vol.301
, pp. 421-422
-
-
Quinton, P.M.1
-
30
-
-
0025349031
-
Cystic fibrosis: A disease in electrolyte transport
-
Quinton PM (1990). Cystic fibrosis: a disease in electrolyte transport. FASEB J 4, 2709-2717.
-
(1990)
FASEB J.
, vol.4
, pp. 2709-2717
-
-
Quinton, P.M.1
-
32
-
-
0026645366
-
cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia
-
Smith JJ & Welsh MJ (1992). cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia. J Clin Invest 89, 1148-1153.
-
(1992)
J. Clin. Invest.
, vol.89
, pp. 1148-1153
-
-
Smith, J.J.1
Welsh, M.J.2
-
37
-
-
0026662657
-
Intracellular pH and its relationship to regulation of ion transport in normal and cystic fibrosis human nasal epithelia
-
Willumsen NJ & Boucher RC (1992). Intracellular pH and its relationship to regulation of ion transport in normal and cystic fibrosis human nasal epithelia. J Physiol 455, 247-269.
-
(1992)
J. Physiol.
, vol.455
, pp. 247-269
-
-
Willumsen, N.J.1
Boucher, R.C.2
-
39
-
-
0021921161
-
Growth and differentiation of human nasal epithelial cells in culture. Serum-free, hormone-supplemented medium and proteoglycan synthesis
-
Wu R, Yankaskas J, Cheng E, Knowles MR & Boucher R (1985). Growth and differentiation of human nasal epithelial cells in culture. Serum-free, hormone-supplemented medium and proteoglycan synthesis. Am Rev Respir Dis 132, 311-320.
-
(1985)
Am. Rev. Respir. Dis.
, vol.132
, pp. 311-320
-
-
Wu, R.1
Yankaskas, J.2
Cheng, E.3
Knowles, M.R.4
Boucher, R.5
-
40
-
-
0034192747
-
Direct comparison of NPPB and DPC as probes of CFTR expressed in Xenopus oocytes
-
Zhang ZR, Zeltwanger S & McCarty NA (2000). Direct comparison of NPPB and DPC as probes of CFTR expressed in Xenopus oocytes. J Membr Biol 175, 35-52.
-
(2000)
J. Membr. Biol.
, vol.175
, pp. 35-52
-
-
Zhang, Z.R.1
Zeltwanger, S.2
McCarty, N.A.3
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